A incidência de todas as formas de síndrome do desfiladeiro torácico (SDT) é difícil de determinar e mal capturada nos bancos de dados e registros grandes, em grande parte devido às grandes variações na suspeita clínica e na aplicação de critérios diagnósticos sólidos.[32]Povlsen B, Hansson T, Povlsen SD. Treatment for thoracic outlet syndrome. Cochrane Database Syst Rev. 2014 Nov 26;2014(11):CD007218.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD007218.pub3/full
http://www.ncbi.nlm.nih.gov/pubmed/25427003?tool=bestpractice.com
A incidência é estimada entre 3 e 80/1000. A SDT neurogênica é a forma mais comum, respondendo por mais de 90% dos casos, seguida pela SDT venosa (aproximadamente 5% a 10%) e, por fim, pela SDT arterial (aproximadamente 1% a 2%).[33]Jones MR, Prabhakar A, Viswanath O, et al. Thoracic outlet syndrome: a comprehensive review of pathophysiology, diagnosis, and treatment. Pain Ther. 2019 Jun;8(1):5-18.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6514035
http://www.ncbi.nlm.nih.gov/pubmed/31037504?tool=bestpractice.com
Sintomas subclínicos e achados de SDT neurogênica podem ser observados em um número substancial de funcionários de escritórios.[34]Pascarelli EF, Hsu YP. Understanding work-related upper extremity disorders: clinical findings in 485 computer users, musicians, and others. J Occup Rehabil. 2001 Mar;11(1):1-21.
http://www.ncbi.nlm.nih.gov/pubmed/11706773?tool=bestpractice.com
A incidência da SDT venosa também é provavelmente pouco relatada, pois as investigações relativas a essa condição são frequentemente negligenciadas na avaliação das tromboses venosas profundas dos membros superiores.[35]Rosa V, Chaar CIO, Espitia O, et al. A RIETE registry analysis of patients with upper extremity deep vein thrombosis and thoracic outlet syndrome. Thromb Res. 2022 May;213:65-70.
http://www.ncbi.nlm.nih.gov/pubmed/35303616?tool=bestpractice.com
[36]Illig KA, Rodriguez-Zoppi E, Bland T, et al. The incidence of thoracic outlet syndrome. Ann Vasc Surg. 2021 Jan;70:263-72.
http://www.ncbi.nlm.nih.gov/pubmed/32771464?tool=bestpractice.com
[37]Illig KA, Rodriguez-Zoppi E. How common is thoracic outlet syndrome? Thorac Surg Clin. 2021 Feb;31(1):11-7.
http://www.ncbi.nlm.nih.gov/pubmed/33220767?tool=bestpractice.com
Com base em padrões de encaminhamentos clínicos, a incidência de SDT neurogênica foi estimada em cerca de 2 a 3 casos por 100,000 habitantes por ano.[36]Illig KA, Rodriguez-Zoppi E, Bland T, et al. The incidence of thoracic outlet syndrome. Ann Vasc Surg. 2021 Jan;70:263-72.
http://www.ncbi.nlm.nih.gov/pubmed/32771464?tool=bestpractice.com
[37]Illig KA, Rodriguez-Zoppi E. How common is thoracic outlet syndrome? Thorac Surg Clin. 2021 Feb;31(1):11-7.
http://www.ncbi.nlm.nih.gov/pubmed/33220767?tool=bestpractice.com
As mulheres predominam na maioria das séries clínicas.[38]Brewin J, Hill M, Ellis H. The prevalence of cervical ribs in a London population. Clin Anat. 2009 Apr;22(3):331-6.
http://www.ncbi.nlm.nih.gov/pubmed/19280652?tool=bestpractice.com
[39]Sanders RJ, Hammond SL. Management of cervical ribs and anomalous first ribs causing neurogenic thoracic outlet syndrome. J Vasc Surg. 2002 Jul;36(1):51-6.
https://www.jvascsurg.org/article/S0741-5214(02)00008-3/pdf
http://www.ncbi.nlm.nih.gov/pubmed/12096257?tool=bestpractice.com
A faixa etária varia de crianças e adolescentes a idosos, com a maioria dos casos ocorrendo em pessoas de 20 a 50 anos.[39]Sanders RJ, Hammond SL. Management of cervical ribs and anomalous first ribs causing neurogenic thoracic outlet syndrome. J Vasc Surg. 2002 Jul;36(1):51-6.
https://www.jvascsurg.org/article/S0741-5214(02)00008-3/pdf
http://www.ncbi.nlm.nih.gov/pubmed/12096257?tool=bestpractice.com
Associada a costelas cervicais (parciais ou completas) em aproximadamente 10% a 20% dos pacientes. A maioria dos pacientes com costelas cervicais são assintomáticos durante toda a vida, com apenas 10% necessitando de tratamento cirúrgico para sintomas relacionados à SDT.[38]Brewin J, Hill M, Ellis H. The prevalence of cervical ribs in a London population. Clin Anat. 2009 Apr;22(3):331-6.
http://www.ncbi.nlm.nih.gov/pubmed/19280652?tool=bestpractice.com
[39]Sanders RJ, Hammond SL. Management of cervical ribs and anomalous first ribs causing neurogenic thoracic outlet syndrome. J Vasc Surg. 2002 Jul;36(1):51-6.
https://www.jvascsurg.org/article/S0741-5214(02)00008-3/pdf
http://www.ncbi.nlm.nih.gov/pubmed/12096257?tool=bestpractice.com
[40]Chang KZ, Likes K, Davis K, et al. The significance of cervical ribs in thoracic outlet syndrome. J Vasc Surg. 2013 Mar;57(3):771-5.
https://www.jvascsurg.org/article/S0741-5214(12)01928-3/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/23446121?tool=bestpractice.com
[41]Weber AE, Criado E. Relevance of bone anomalies in patients with thoracic outlet syndrome. Ann Vasc Surg. 2014 May;28(4):924-32.
http://www.ncbi.nlm.nih.gov/pubmed/24316293?tool=bestpractice.com
[42]Gelabert HA, Rigberg DA, O'Connell JB, et al. Transaxillary decompression of thoracic outlet syndrome patients presenting with cervical ribs. J Vasc Surg. 2018 Oct;68(4):1143-9.
https://www.jvascsurg.org/article/S0741-5214(18)30415-4/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/29705086?tool=bestpractice.com
A etiologia mudou com as mudanças na força de trabalho e os avanços das tecnologias. Os trabalhadores da indústria e de trabalhos manuais foram superados por causas acidentais e lesões por movimentos repetitivos relacionadas ao uso de computadores e a má postura. Subpopulações como funcionários de escritório, vítimas de acidente com veículos automotores, pessoas feridas no local de trabalho e atletas foram identificadas como potencialmente mais propensas a desenvolverem SDT neurogênica.[5]Wilbourn AJ. Thoracic outlet syndromes. Neurol Clin. 1999;17:477-497.
http://www.ncbi.nlm.nih.gov/pubmed/10393750?tool=bestpractice.com
[6]Ferrante MA. The thoracic outlet syndromes. Muscle Nerve. 2012;45:780-95.
http://www.ncbi.nlm.nih.gov/pubmed/22581530?tool=bestpractice.com
[7]Nichols AW. Diagnosis and management of thoracic outlet syndrome. Curr Sports Med Rep. 2009;8:240-249.
http://www.ncbi.nlm.nih.gov/pubmed/19741351?tool=bestpractice.com
[8]Chang K, Graf E, Davis K, et al. Spectrum of thoracic outlet syndrome presentation in adolescents. Arch Surg. 2011;146:1383-1387.
http://archsurg.jamanetwork.com/article.aspx?articleid=1107261
http://www.ncbi.nlm.nih.gov/pubmed/22184299?tool=bestpractice.com
[9]Caputo FJ, Wittenberg AM, Vemuri C, et al. Supraclavicular decompression for neurogenic thoracic outlet syndrome in adolescent and adult populations. J Vasc Surg. 2013;57:149-157.
http://www.ncbi.nlm.nih.gov/pubmed/23127984?tool=bestpractice.com
[10]Maru S, Dosluoglu H, Dryjski M, et al. Thoracic outlet syndrome in children and young adults. Eur J Vasc Endovasc Surg. 2009;38:560-564.
http://www.ejves.com/article/S1078-5884(09)00339-6/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/19703780?tool=bestpractice.com
[11]Stewman C, Vitanzo PC Jr, Harwood MI. Neurologic thoracic outlet syndrome: summarizing a complex history and evolution. Curr Sports Med Rep. 2014;13:100-106.
http://www.ncbi.nlm.nih.gov/pubmed/24614423?tool=bestpractice.com
[12]Vanti C, Natalini L, Romeo A, et al. Conservative treatment of thoracic outlet syndrome: a review of the literature. Eura Medicophys. 2007;43:55-70.
http://www.ncbi.nlm.nih.gov/pubmed/16955064?tool=bestpractice.com
[34]Pascarelli EF, Hsu YP. Understanding work-related upper extremity disorders: clinical findings in 485 computer users, musicians, and others. J Occup Rehabil. 2001 Mar;11(1):1-21.
http://www.ncbi.nlm.nih.gov/pubmed/11706773?tool=bestpractice.com
[43]Demondion X, Herbinet P, Van Sint Jan S, et al. Imaging assessment of thoracic outlet syndrome. Radiographics. 2006;26:1735-50.
http://www.ncbi.nlm.nih.gov/pubmed/17102047?tool=bestpractice.com
[44]Barton NJ, Hooper G, Noble J, et al. Occupational causes of disorders in the upper limb. BMJ. 1992;304:309-311.
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1881046/pdf/bmj00058-0049.pdf
http://www.ncbi.nlm.nih.gov/pubmed/1739835?tool=bestpractice.com
[45]Hagberg M, Wegman DH. Prevalence rates and odds ratios of shoulder-neck diseases in different occupational groups. Br J Ind Med. 1987 Sep;44(9):602-10.
http://www.ncbi.nlm.nih.gov/pubmed/3311128?tool=bestpractice.com
[46]Laulan J, Fouquet B, Rodaix C, et al. Thoracic outlet syndrome: definition, aetiological factors, diagnosis, management and occupational impact. J Occup Rehabil. 2011 Sep;21(3):366-73.
http://www.ncbi.nlm.nih.gov/pubmed/21193950?tool=bestpractice.com
[47]Demaree CJ, Wang K, Lin PH. Thoracic outlet syndrome affecting high-performance musicians playing bowed string instruments. Vascular. 2017 Jun;25(3):329-2.
http://www.ncbi.nlm.nih.gov/pubmed/27694556?tool=bestpractice.com
[48]Abraham P, Lecoq S, Mechenin M, et al. Role of lifestyle in thoracic outlet syndrome: a narrative review. J Clin Med. 2024 Jan 11;13(2):417.
https://www.mdpi.com/2077-0383/13/2/417
http://www.ncbi.nlm.nih.gov/pubmed/38256551?tool=bestpractice.com
[49]Logiou C, Demondion X, Tiffreau V, et al. Evaluation of the socioprofessional consequences of thoracic outlet syndrome. BMC Res Notes. 2023 Sep 11;16(1):207.
https://bmcresnotes.biomedcentral.com/articles/10.1186/s13104-023-06448-2
http://www.ncbi.nlm.nih.gov/pubmed/37697402?tool=bestpractice.com
A compressão concomitante do plexo braquial nos espaços do triângulo escaleno e do peitoral menor pode estar presente em aproximadamente 80% a 90% dos pacientes com SDT neurogênica. A compressão nervosa isolada no espaço do peitoral menor ocorre em cerca de 5% a 10% dos pacientes.[50]Sanders RJ, Rao NM. The forgotten pectoralis minor syndrome: 100 operations for pectoralis minor syndrome alone or accompanied by neurogenic thoracic outlet syndrome. Ann Vasc Surg. 2010;24:701-708.
http://www.ncbi.nlm.nih.gov/pubmed/20471786?tool=bestpractice.com
[51]Vemuri C, Wittenberg AM, Caputo FJ, et al. Early effectiveness of isolated pectoralis minor tenotomy in selected patients with neurogenic thoracic outlet syndrome. J Vasc Surg. 2013;57:1345-1352.
http://www.ncbi.nlm.nih.gov/pubmed/23375605?tool=bestpractice.com
Com base em padrões de encaminhamentos clínicos, a incidência de SDT venosa foi estimada em cerca de 0.5 a 1 por 100,000 habitantes/ano.[36]Illig KA, Rodriguez-Zoppi E, Bland T, et al. The incidence of thoracic outlet syndrome. Ann Vasc Surg. 2021 Jan;70:263-72.
http://www.ncbi.nlm.nih.gov/pubmed/32771464?tool=bestpractice.com
[37]Illig KA, Rodriguez-Zoppi E. How common is thoracic outlet syndrome? Thorac Surg Clin. 2021 Feb;31(1):11-7.
http://www.ncbi.nlm.nih.gov/pubmed/33220767?tool=bestpractice.com
[52]Illig KA, Gober L. Optimal management of upper extremity deep vein thrombosis: Is venous thoracic outlet syndrome underrecognized? J Vasc Surg Venous Lymphat Disord. 2022 Mar;10(2):514-26.
http://www.ncbi.nlm.nih.gov/pubmed/34352421?tool=bestpractice.com
Na maioria das vezes há uma predominância do sexo masculino com uma proporção de 2:1, com uma equivalência entre os sexos observada em outras séries.
Tende a afetar pacientes desde a adolescência até os 50 anos.
Não está associada a costelas cervicais.
Está frequentemente relacionada a exercícios repetitivos, levantamento de peso e movimentos acima da cabeça. Estes, por sua vez, estão mais frequentemente associados a atividades atléticas e também podem estar associados a trabalhos braçais. Ocasionalmente ela está associada a causas congênitas e do desenvolvimento.[13]Illig KA, Doyle AJ. A comprehensive review of Paget-Schroetter syndrome. J Vasc Surg. 2010;51:1538-47.
http://www.jvascsurg.org/article/S0741-5214(09)02518-X/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/20304578?tool=bestpractice.com
[14]Farrar TA, Rankin G, Chatfield M. Venous thoracic outlet syndrome: approach to diagnosis and treatment with focus on affected athletes. Curr Sports Med Rep. 2014;13:81-5.
http://www.ncbi.nlm.nih.gov/pubmed/24614420?tool=bestpractice.com
[53]Laker S, Sullivan WJ, Whitehill TA. Thoracic outlet syndrome. In: Akuthota V, Herring S, eds. Nerve and vascular injuries in sports medicine. New York, NY: Springer; 2009:113-126.
Com base em padrões de encaminhamentos clínicos, a incidência da SDT arterial foi caracterizada como rara. Em clínicas grandes ela foi observada com uma frequência de 2% a 5% dos casos cirúrgicos.[18]Vemuri C, McLaughlin LN, Abuirqeba AA, et al. Clinical presentation and management of arterial thoracic outlet syndrome. J Vasc Surg. 2017 May;65(5):1429-39.
https://www.jvascsurg.org/article/S0741-5214(16)31853-5/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/28189360?tool=bestpractice.com
[54]Archie MM, Gelabert HA. Endovascular reconstruction of subclavian artery aneurysms in patients with arterial thoracic outlet syndrome. Ann Vasc Surg. 2019 May;57:10-5.
http://www.ncbi.nlm.nih.gov/pubmed/30476600?tool=bestpractice.com
[55]Pantoja JL, Rigberg DA, Gelabert HA. The evolving role of endovascular therapy in the management of arterial thoracic outlet syndrome. J Vasc Surg. 2022 Mar;75(3):968-75.e1.
https://www.jvascsurg.org/article/S0741-5214(21)02341-7/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/34695555?tool=bestpractice.com
[56]de Kleijn RJCMF, Schropp L, Westerink J, et al. Functional outcome of arterial thoracic outlet syndrome treatment. Front Surg. 2022;9:1072536.
https://www.frontiersin.org/journals/surgery/articles/10.3389/fsurg.2022.1072536/full
http://www.ncbi.nlm.nih.gov/pubmed/36726955?tool=bestpractice.com
As mulheres predominam em uma proporção de aproximadamente 60:40 a 70:30.
Foi relatada em uma ampla faixa etária, desde adolescentes até o final dos 60 anos.
Está associada à presença de anomalias ósseas congênitas (costelas cervicais, primeiras costelas aberrantes) e lesões ortopédicas (fraturas da clavícula e da primeira costela), bem como atividades acima da cabeça (atletas).[19]Daniels B, Michaud L, Sease F Jr, et al. Arterial thoracic outlet syndrome. Curr Sports Med Rep. 2014;13:75-80.
http://www.ncbi.nlm.nih.gov/pubmed/24614419?tool=bestpractice.com
[20]Durham JR, Yao JS, Pearce WH, et al. Arterial injuries in the thoracic outlet syndrome. J Vasc Surg. 1995;21:57-70.
http://www.jvascsurg.org/article/S0741-5214(95)70244-X/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/7823362?tool=bestpractice.com
[21]Abdollahi K, Wood VE. Thoracic outlet syndrome. In: DeLee J, Drez D, Miller MD, eds. DeLee and Drez’s orthopaedic sports medicine: principles and practice. 3rd ed. Philadelphia, PA: WB Saunders; 2010:1128-1137.[22]Roos DB. Congenital anomalies associated with thoracic outlet syndrome: anatomy, symptoms, diagnosis, and treatment. Am J Surg. 1976;132:771-778.
http://www.ncbi.nlm.nih.gov/pubmed/998867?tool=bestpractice.com