Categoria 2 do AREDS (Age-Related Eye Disease Study Group) (degeneração macular relacionada à idade [DMRI] precoce)
Geralmente, a acuidade visual permanece não afetada, a menos que ocorra progressão.
Os pacientes têm um risco de 1.3% ao longo de 5 anos de progredirem para DMRI avançada.[34]Age-Related Eye Disease Study Research Group. A randomized, placebo-controlled, clinical trial of high-dose supplementation with vitamins C and E, beta carotene, and zinc for age-related macular degeneration and vision loss: AREDS report no. 8. Arch Ophthalmol. 2001 Oct;119(10):1417-36.
https://jamanetwork.com/journals/jamaophthalmology/fullarticle/268224
http://www.ncbi.nlm.nih.gov/pubmed/11594942?tool=bestpractice.com
Nenhum tratamento demonstrou ser eficaz para essa categoria da doença.
Categoria 3 do AREDS (DMRI intermediária)
Geralmente, a acuidade visual permanece não afetada, a menos que ocorra progressão.
Os pacientes têm um risco de 18% ao longo de 5 anos de que a doença evolua para DMRI avançada.[34]Age-Related Eye Disease Study Research Group. A randomized, placebo-controlled, clinical trial of high-dose supplementation with vitamins C and E, beta carotene, and zinc for age-related macular degeneration and vision loss: AREDS report no. 8. Arch Ophthalmol. 2001 Oct;119(10):1417-36.
https://jamanetwork.com/journals/jamaophthalmology/fullarticle/268224
http://www.ncbi.nlm.nih.gov/pubmed/11594942?tool=bestpractice.com
Os pacientes que receberam suplementos antioxidantes no estudo AREDS tiveram uma redução de 25% na progressão para doença avançada e uma redução de 19% na perda da visão de ≥3 linhas ao longo de 5 anos.[34]Age-Related Eye Disease Study Research Group. A randomized, placebo-controlled, clinical trial of high-dose supplementation with vitamins C and E, beta carotene, and zinc for age-related macular degeneration and vision loss: AREDS report no. 8. Arch Ophthalmol. 2001 Oct;119(10):1417-36.
https://jamanetwork.com/journals/jamaophthalmology/fullarticle/268224
http://www.ncbi.nlm.nih.gov/pubmed/11594942?tool=bestpractice.com
Categoria 4 do AREDS (DMRI avançada)
Os pacientes com doença unilateral têm uma chance de 43% ao longo de 5 anos de desenvolver DMRI avançada no outro olho.[34]Age-Related Eye Disease Study Research Group. A randomized, placebo-controlled, clinical trial of high-dose supplementation with vitamins C and E, beta carotene, and zinc for age-related macular degeneration and vision loss: AREDS report no. 8. Arch Ophthalmol. 2001 Oct;119(10):1417-36.
https://jamanetwork.com/journals/jamaophthalmology/fullarticle/268224
http://www.ncbi.nlm.nih.gov/pubmed/11594942?tool=bestpractice.com
A DMRI (seca) com atrofia geográfica tende a resultar em menor comprometimento visual que a DMRI exsudativa (úmida). Em contraste, a DMRI úmida, se não tratada, resultará em perda da visão significativa (duplicação do ângulo visual ou pior) em mais da metade dos pacientes ao longo dos próximos anos.[83]Macular Photocoagulation Study Group. Argon laser photocoagulation for neovascular maculopathy. Five-year results from randomized clinical trials. Arch Ophthalmol. 1991 Aug;109(8):1109-14.
http://www.ncbi.nlm.nih.gov/pubmed/1714270?tool=bestpractice.com
[84]Macular Photocoagulation Study Group. Laser photocoagulation for juxtafoveal choroidal neovascularization. Five-year results from randomized clinical trials. Arch Ophthalmol. 1994 Apr;112(4):500-9.
http://www.ncbi.nlm.nih.gov/pubmed/7512336?tool=bestpractice.com
[85]Macular Photocoagulation Study Group. Laser photocoagulation of subfoveal neovascular lesions in age-related macular degeneration. Results of a randomized clinical trial. Arch Ophthalmol. 1991 Sep;109(9):1220-31.
http://www.ncbi.nlm.nih.gov/pubmed/1718250?tool=bestpractice.com
[105]Sunness JS, Rubin GS, Applegate CA, et al. Visual function abnormalities and prognosis in eyes with age-related geographic atrophy of the macula and good visual acuity. Ophthalmology. 1997 Oct;104(10):1677-91.
http://www.ncbi.nlm.nih.gov/pubmed/9331210?tool=bestpractice.com
O tratamento da neovascularização da coroide (NVC) extrafoveal por fotocoagulação a laser resulta em uma redução significativa da perda da visão grave, mas a recorrência é comum.[83]Macular Photocoagulation Study Group. Argon laser photocoagulation for neovascular maculopathy. Five-year results from randomized clinical trials. Arch Ophthalmol. 1991 Aug;109(8):1109-14.
http://www.ncbi.nlm.nih.gov/pubmed/1714270?tool=bestpractice.com
[84]Macular Photocoagulation Study Group. Laser photocoagulation for juxtafoveal choroidal neovascularization. Five-year results from randomized clinical trials. Arch Ophthalmol. 1994 Apr;112(4):500-9.
http://www.ncbi.nlm.nih.gov/pubmed/7512336?tool=bestpractice.com
[85]Macular Photocoagulation Study Group. Laser photocoagulation of subfoveal neovascular lesions in age-related macular degeneration. Results of a randomized clinical trial. Arch Ophthalmol. 1991 Sep;109(9):1220-31.
http://www.ncbi.nlm.nih.gov/pubmed/1718250?tool=bestpractice.com
O tratamento da NVC subfoveal por terapia fotodinâmica reduz as taxas de perda da visão, mas a maioria dos pacientes ainda apresenta perda da visão, e os resultados são inferiores aos obtidos usando inibidores do fator de crescimento endotelial vascular intravítreo. Portanto, não é mais recomendado como tratamento de primeira linha.[23]American Academy of Ophthalmology. Preferred practice pattern: age-related macular degeneration. Oct 2019 [internet publication].
https://www.aao.org/preferred-practice-pattern/age-related-macular-degeneration-ppp
[106]Bressler NM; Treatment of Age-Related Macular Degeneration with Photodynamic Therapy (TAP) Study Group. Photodynamic therapy of subfoveal choroidal neovascularization in age-related macular degeneration with verteporfin: two-year results of 2 randomized clinical trials-TAP report 2. Arch Ophthalmol. 2001 Feb;119(2):198-207.
http://www.ncbi.nlm.nih.gov/pubmed/11176980?tool=bestpractice.com
[107]Verteporfin In Photodynamic Therapy Study Group. Verteporfin therapy of subfoveal choroidal neovascularization in age-related macular degeneration: two-year results of a randomized clinical trial including lesions with occult with no classic choroidal neovascularization - verteporfin in photodynamic therapy report 2. Am J Ophthalmol. 2001 May;131(5):541-60.
http://www.ncbi.nlm.nih.gov/pubmed/11336929?tool=bestpractice.com
[108]Barbazetto I, Burdan A, Bressler NM, et al. Photodynamic therapy of subfoveal choroidal neovascularization with verteporfin: fluorescein angiographic guidelines for evaluation and treatment - TAP and VIP report No. 2. Arch Ophthalmol. 2003 Sep;121(9):1253-68.
http://www.ncbi.nlm.nih.gov/pubmed/12963608?tool=bestpractice.com
[109]Blinder KJ, Bradley S, Bressler NM, et al. Effect of lesion size, visual acuity, and lesion composition on visual acuity change with and without verteporfin therapy for choroidal neovascularization secondary to age-related macular degeneration: TAP and VIP report no. 1. Am J Ophthalmol. 2003 Sep;136(3):407-18.
http://www.ncbi.nlm.nih.gov/pubmed/12967792?tool=bestpractice.com
Por comparação, o tratamento da NVC subfoveal por injeção intravítrea de ranibizumabe resulta na estabilização da visão em até 95% dos pacientes e em melhora da visão em até um terço dos pacientes.[76]Brown DM, Kaiser PK, Michels M, et al; ANCHOR Study Group. Ranibizumab versus verteporfin for neovascular age-related macular degeneration. N Engl J Med. 2006 Oct 5;355(14):1432-44.
https://www.nejm.org/doi/full/10.1056/NEJMoa062655
http://www.ncbi.nlm.nih.gov/pubmed/17021319?tool=bestpractice.com
[77]Rosenfeld PJ, Brown DM, Heier JS, et al. Ranibizumab for neovascular age-related macular degeneration. N Engl J Med. 2006 Oct 5;355(14):1419-31.
https://www.nejm.org/doi/10.1056/NEJMoa054481
http://www.ncbi.nlm.nih.gov/pubmed/17021318?tool=bestpractice.com
Foi demonstrado que o bevacizumabe apresenta eficácia similar à do ranibizumabe.[54]Martin DF, Maguire MG, Fine SL, et al. Ranibizumab and bevacizumab for treatment of neovascular age-related macular degeneration: two-year results. Ophthalmology. 2012 Jul;119(7):1388-98.
https://www.aaojournal.org/article/S0161-6420(12)00321-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/22555112?tool=bestpractice.com
[55]Chakravarthy U, Harding SP, Rogers CA, et al. Ranibizumab versus bevacizumab to treat neovascular age-related macular degeneration: one-year findings from the IVAN randomized trial. Ophthalmology. 2012 Jul;119(7):1399-411. O aflibercepte de maneira geral tem eficácia similar e requer tratamentos menos frequentes.[51]Heier JS, Boyer D, Nguyen QD, et al. The 1-year results of CLEAR-IT 2, a phase 2 study of vascular endothelial growth factor trap-eye dosed as-needed after 12-week fixed dosing. Ophthalmology. 2011 Jun;118(6):1098-106.
http://www.ncbi.nlm.nih.gov/pubmed/21640258?tool=bestpractice.com
Brolucizumabe demonstra eficácia similar com cronograma de dosagem estendido em uma proporção de pacientes após a terceira injeção mensal.[67]Dugel PU, Koh A, Ogura Y, et al. HAWK and HARRIER: Phase 3, multicenter, randomized, double-masked trials of brolucizumab for neovascular age-related macular degeneration. Ophthalmology. 2020 Jan;127(1):72-84.
https://www.aaojournal.org/article/S0161-6420(18)33018-5/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/30986442?tool=bestpractice.com
Eventos adversos de inflamação intraocular, vasculite e vasculite oclusiva da retina foram relatados em relação ao brolucizumabe em taxas ligeiramente superiores do que com outros inibidores de VEGF.[67]Dugel PU, Koh A, Ogura Y, et al. HAWK and HARRIER: Phase 3, multicenter, randomized, double-masked trials of brolucizumab for neovascular age-related macular degeneration. Ophthalmology. 2020 Jan;127(1):72-84.
https://www.aaojournal.org/article/S0161-6420(18)33018-5/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/30986442?tool=bestpractice.com
[68]Dugel PU, Singh RP, Koh A, et al. HAWK and HARRIER: Ninety-six-week outcomes from the phase 3 trials of brolucizumab for neovascular age-related macular degeneration. Ophthalmology. 2021 Jan;128(1):89-99.
https://www.aaojournal.org/article/S0161-6420(20)30570-4/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/32574761?tool=bestpractice.com
[69]Monés J, Srivastava SK, Jaffe GJ, et al. Risk of Inflammation, Retinal Vasculitis, and Retinal Occlusion-Related Events with Brolucizumab: Post Hoc Review of HAWK and HARRIER. Ophthalmology. 2021 Jul;128(7):1050-9.
https://www.doi.org/10.1016/j.ophtha.2020.11.011
http://www.ncbi.nlm.nih.gov/pubmed/33207259?tool=bestpractice.com
Esses eventos adversos estão sendo investigados por um comitê de revisão de segurança externo, e a empresa farmacêutica está comunicando as atualizações por meio de um site.[110]Novartis. Global Safety Information for Healthcare Professionals. Beovu® Brolucizumab. 2021 [internet publication].
https://www.brolucizumab.info
Em janeiro de 2022, a Medicines and Healthcare Products Regulatory Agency (MHRA) do Reino Unido recomendou que, após as três injeções de ataque, as doses de brolucizumabe devem ser administradas com pelo menos 8 semanas de intervalo para reduzir os eventos adversos.[71]Medicines and Healthcare products Regulatory Agency: Brolucizumab (Beovu▼): risk of intraocular inflammation and retinal vascular occlusion increased with short dosing intervals. Jan 2022 [internet publication].
https://www.gov.uk/drug-safety-update/brolucizumab-beovuv-risk-of-intraocular-inflammation-and-retinal-vascular-occlusion-increased-with-short-dosing-intervals