Epidemiology

Estimates from population studies of the prevalence of early-onset dystonia vary widely, ranging from as low as 7 per 100,000 to as high as 500 per 100,000.[3][4][5][6][7] Meta-analyses have calculated the prevalence of idiopathic ("primary") dystonia as 16-30 per 100,000, although this is likely to be an underestimate.[8][9][10]

The prevalence is higher in specific subgroups, such as Ashkenazi Jews where it is estimated at 1110 per 100,000. When late-onset cases are included, estimates of the prevalence of dystonia range from 300 per 100,000 to as high as 732 per 100,000.[4][5][11]

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