For patients with mild or moderate stenosis, the aortic valve area decreases on average by 0.1 cm²/year and the mean gradient increases by 7 mmHg annually.[78]Faggiano P, Ghizzoni G, Sorgato A, et al. Rate of progression of valvular aortic stenosis in adults. Am J Cardiol. 1992 Jul 15;70(2):229-33.
http://www.ncbi.nlm.nih.gov/pubmed/1626512?tool=bestpractice.com
It is recommended that patients with moderate AS have an echocardiogram every 1 to 2 years, and those with mild AS have one every 3 to 5 years.[26]Otto CM, Nishimura RA, Bonow RO, et al. 2020 ACC/AHA guideline for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Joint Committee on clinical practice guidelines. Circulation. 2021 Feb 2;143(5):e72-227.
https://www.ahajournals.org/doi/full/10.1161/CIR.0000000000000923
It is important to note that the rate of progression is extremely variable and so the recommended follow-up periods may vary between individuals.
The onset of symptoms is a significant milestone and portends a poor prognosis, with an average survival of only 2 to 3 years without surgery. Between 8% and 34% of symptomatic patients die suddenly.[79]Sorgato A, Faggiano P, Aurigemma GP, et al. Ventricular arrhythmias in adult aortic stenosis: prevalence, mechanisms, and clinical relevance. Chest. 1998 Feb;113(2):482-91.
http://www.ncbi.nlm.nih.gov/pubmed/9498969?tool=bestpractice.com
It is thus essential that symptomatic patients be referred for surgical aortic valve replacement.
Surgical replacement of the aortic valve is extremely effective therapy. Advances in prosthetic-valve design, cardiopulmonary bypass, surgical technique, and anaesthesia have steadily improved outcomes for aortic valve surgery. An analysis of the 2006 American Society of Thoracic Surgery STS database shows that during the previous decade, the mortality risk of isolated aortic valve replacement decreased from 3.4% to 2.6%. For those <70 years at surgery, the mortality risk is 1.3%.[46]Brown JM, O'Brien SM, Wu C, et al. Isolated aortic valve replacement in North America comprising 108,687 patients in 10 years: changes in risks, valve types, and outcomes in the Society of Thoracic Surgeons National Database. J Thorac Cardiovasc Surg. 2009 Jan;137(1):82-90.
http://www.ncbi.nlm.nih.gov/pubmed/19154908?tool=bestpractice.com
Patients who survive surgery have near-normal life expectancy, with relative survival at 5, 10, and 15 years of 99%, 85%, and 82%, respectively.[80]Kvidal P, Bergstrom R, Horte LG, et al. Observed and relative survival after aortic valve replacement. J Am Coll Cardiol. 2000 Mar 1;35(3):747-56.
http://www.ncbi.nlm.nih.gov/pubmed/10716479?tool=bestpractice.com
[81]Ståhle E, Kvidal P, Nyström SO, et al. Long-term relative survival after primary heart valve replacement. Eur J Cardiothorac Surg. 1997 Jan;11(1):81-91.
http://www.ncbi.nlm.nih.gov/pubmed/9030794?tool=bestpractice.com
Nearly all patients have improvement in ejection fraction and heart failure symptoms, with the most significant benefit seen in those with more advanced preoperative symptoms.[82]Vaquette B, Corbineau H, Laurent M, et al. Valve replacement in patients with critical aortic stenosis and depressed left ventricular function: predictors of operative risk, left ventricular function recovery, and long term outcome. Heart. 2005 Oct;91(10):1324-9.
http://heart.bmj.com/content/91/10/1324.long
http://www.ncbi.nlm.nih.gov/pubmed/16162627?tool=bestpractice.com
[83]Sharma UC, Barenbrug P, Pokharel S, et al. Systematic review of the outcome of aortic valve replacement in patients with aortic stenosis. Ann Thorac Surg. 2004 Jul;78(1):90-5.
http://www.ncbi.nlm.nih.gov/pubmed/15223410?tool=bestpractice.com
For those who do not improve, factors to consider are valve dysfunction, less-than-expected improvement in preoperative left ventricle function, valve-prosthesis mismatch, and other comorbid conditions.
Appropriately selected patients at all levels of surgical risk may be offered surgery or transcatheter aortic valve replacement (TAVR), while patients with prohibitive risk (i.e., surgical non-candidates) should be referred for TAVR if predicted post-TAVR survival is greater than 12 months.[59]Holmes DR Jr, Mack MJ, Kaul S, et al. 2012 ACCF/AATS/SCAI/STS expert consensus document on transcatheter aortic valve replacement. J Am Coll Cardiol. 2012 Mar 27;59(13):1200-54.
http://content.onlinejacc.org/article.aspx
http://www.ncbi.nlm.nih.gov/pubmed/22300974?tool=bestpractice.com
[26]Otto CM, Nishimura RA, Bonow RO, et al. 2020 ACC/AHA guideline for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Joint Committee on clinical practice guidelines. Circulation. 2021 Feb 2;143(5):e72-227.
https://www.ahajournals.org/doi/full/10.1161/CIR.0000000000000923
In the PARTNER study comparing surgery and TAVR in high-risk patients, mortality and symptom reduction were similar at 2 and 5 years for each modality.[52]Kodali SK, Williams MR, Smith CR, et al. Two-year outcomes after transcatheter or surgical aortic-valve replacement. N Engl J Med. 2012 May 3;366(18):1686-95.
http://www.ncbi.nlm.nih.gov/pubmed/22443479?tool=bestpractice.com
[53]Mack MJ, Leon MB, Smith CR, et al. 5-year outcomes of transcatheter aortic valve replacement or surgical aortic valve replacement for high surgical risk patients with aortic stenosis (PARTNER 1): a randomised controlled trial. Lancet. 2015 Jun 20;385(9986):2477-84.
http://www.ncbi.nlm.nih.gov/pubmed/25788234?tool=bestpractice.com
Peri-procedural risks varied at 30 days; vascular complications and neurological events such as stroke occurred more frequently after TAVR, while major bleeding and new-onset atrial fibrillation more commonly followed surgery.[54]Smith CR, Leon MB, Mack MJ, et al; PARTNER Trial Investigators. Transcatheter versus surgical aortic-valve replacement in high-risk patients. N Engl J Med. 2011 Jun 9;364(23):2187-98.
http://www.ncbi.nlm.nih.gov/pubmed/21639811?tool=bestpractice.com
[55]Généreux P, Cohen DJ, Williams MR, et al. Bleeding complications after surgical aortic valve replacement compared with transcatheter aortic valve replacement: insights from the PARTNER I Trial (Placement of Aortic Transcatheter Valve). J Am Coll Cardiol. 2014 Mar 25;63(11):1100-9.
http://www.ncbi.nlm.nih.gov/pubmed/24291283?tool=bestpractice.com
Acute kidney injury and new pacemaker implantation were complications of both interventions at similar rates.[54]Smith CR, Leon MB, Mack MJ, et al; PARTNER Trial Investigators. Transcatheter versus surgical aortic-valve replacement in high-risk patients. N Engl J Med. 2011 Jun 9;364(23):2187-98.
http://www.ncbi.nlm.nih.gov/pubmed/21639811?tool=bestpractice.com
At 2 and 5 years, echocardiographic improvements in valve area and mean gradients were similar in both groups, but total and paravalvular aortic regurgitation was encountered more frequently after TAVR.[52]Kodali SK, Williams MR, Smith CR, et al. Two-year outcomes after transcatheter or surgical aortic-valve replacement. N Engl J Med. 2012 May 3;366(18):1686-95.
http://www.ncbi.nlm.nih.gov/pubmed/22443479?tool=bestpractice.com
[53]Mack MJ, Leon MB, Smith CR, et al. 5-year outcomes of transcatheter aortic valve replacement or surgical aortic valve replacement for high surgical risk patients with aortic stenosis (PARTNER 1): a randomised controlled trial. Lancet. 2015 Jun 20;385(9986):2477-84.
http://www.ncbi.nlm.nih.gov/pubmed/25788234?tool=bestpractice.com
[57]Hahn RT, Pibarot P, Stewart WJ, et al. Comparison of transcatheter and surgical aortic valve replacement in severe aortic stenosis: a longitudinal study of echocardiography parameters in cohort A of the PARTNER trial (placement of aortic transcatheter valves). J Am Coll Cardiol. 2013 Jun 25;61(25):2514-21.
http://www.ncbi.nlm.nih.gov/pubmed/23623915?tool=bestpractice.com
In patients with prohibitive surgical risk (i.e., surgical non-candidates), the PARTNER trial compared standard therapy, including balloon aortic valvuloplasty, with TAVR and found a 20% absolute reduction in mortality at 1 year in favour of TAVR.[60]Leon MB, Smith CR, Mack M, et al. Transcatheter aortic-valve implantation for aortic stenosis in patients who cannot undergo surgery. N Engl J Med. 2010 Oct 21;363(17):1597-607.
http://www.nejm.org/doi/full/10.1056/NEJMoa1008232#t=article
http://www.ncbi.nlm.nih.gov/pubmed/20961243?tool=bestpractice.com
At 3 years, mortality with TAVR was 54.1% compared with 80.9% with standard therapy, while at 5 years, mortality was 71.8% and 93.6%, respectively.[61]Kapadia SR, Tuzcu EM, Makkar RR, et al. Long-term outcomes of inoperable patients with aortic stenosis randomly assigned to transcatheter aortic valve replacement or standard therapy. Circulation. 2014 Oct 21;130(17):1483-92.
http://circ.ahajournals.org/content/130/17/1483.long
http://www.ncbi.nlm.nih.gov/pubmed/25205802?tool=bestpractice.com
[62]Kapadia SR, Leon MB, Makkar RR, et al. 5-year outcomes of transcatheter aortic valve replacement compared with standard treatment for patients with inoperable aortic stenosis (PARTNER 1): a randomised controlled trial. Lancet. 2015 Jun 20;385(9986):2485-91.
http://www.ncbi.nlm.nih.gov/pubmed/25788231?tool=bestpractice.com
Heart failure symptoms improved between 30 days and 6 months, while at 3 years 29.7% of patients in the TAVR group were alive with New York Heart Association Class I/II symptoms, compared with 4.8% of patients in the standard therapy group.[60]Leon MB, Smith CR, Mack M, et al. Transcatheter aortic-valve implantation for aortic stenosis in patients who cannot undergo surgery. N Engl J Med. 2010 Oct 21;363(17):1597-607.
http://www.nejm.org/doi/full/10.1056/NEJMoa1008232#t=article
http://www.ncbi.nlm.nih.gov/pubmed/20961243?tool=bestpractice.com
[61]Kapadia SR, Tuzcu EM, Makkar RR, et al. Long-term outcomes of inoperable patients with aortic stenosis randomly assigned to transcatheter aortic valve replacement or standard therapy. Circulation. 2014 Oct 21;130(17):1483-92.
http://circ.ahajournals.org/content/130/17/1483.long
http://www.ncbi.nlm.nih.gov/pubmed/25205802?tool=bestpractice.com
[63]Makkar RR, Fontana GP, Jilaihawi H, et al. Transcatheter aortic-valve replacement for inoperable severe aortic stenosis. N Engl J Med. 2012 May 3;366(18):1696-704.
http://www.ncbi.nlm.nih.gov/pubmed/22443478?tool=bestpractice.com
Patients treated with TAVR also showed significant improvements on assessments of health-related quality of life when compared with those receiving standard therapy.[64]Reynolds MR, Magnuson EA, Lei Y, et al. Valvular heart disease: Health-related quality of life after transcatheter aortic valve replacement in inoperable patients with severe aortic stenosis. Circulation. 2011 Nov 1;124(18):1964-72.
http://circ.ahajournals.org/content/124/18/1964.full
http://www.ncbi.nlm.nih.gov/pubmed/21969017?tool=bestpractice.com
Many patients with bicuspid aortic valves will require valve replacement at some point in their lives. After valve replacement, patients with bicuspid valves have a significant mortality benefit and improvement in symptoms. However, they remain at risk for aortic dissection and require serial follow-up for this potential complication.