Monitoring

The European Reference Network guideline recommends that children with Hirschsprung disease receive regular interdisciplinary follow-up to adulthood.[27]​ Follow-up should be frequent in the first year of life and every 1-2 years afterward, and should include assessment of growth, nutrition, development, and social functioning.[27]​ Guidelines have been proposed for the evaluation of postoperative complications in children with Hirschsprung disease.​​[88][89][90]​​​​​​[102][103]

Importantly, parents and caregivers should seek urgent medical care for any signs and symptoms of Hirschsprung-associated enterocolitis (HAEC).[11]​ Recurrent episodes of enterocolitis should prompt evaluation of an anatomic cause.[11]​ ​The pathogenesis of HAEC is thought to be due in part to dysbiosis, but there is no good evidence for or against probiotics to prevent HAEC.[12][104]

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