Other presentations
This skin condition most commonly presents as the papular type, although other subtypes occur.[1]Holzle E, Plewig G, von Kries R, et al. Polymorphous light eruption. J Invest Dermatol. 1987;88(3 Suppl):32s-8.
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[2]Kontos AP, Cusack CA, Chaffins M, et al. Polymorphous light eruption in African Americans: pinpoint papular variant. Photodermatol Photoimmunol Photomed. 2002 Dec;18(6):303-6.
http://www.ncbi.nlm.nih.gov/pubmed/12535026?tool=bestpractice.com
[3]Bansal I, Kerr H, Janiga JJ, et al. Pinpoint papular variant of polymorphous light eruption: clinical and pathological. Eur Acad Dermatol Venereol. 2006 Apr;20(4):406-10.
http://www.ncbi.nlm.nih.gov/pubmed/16643137?tool=bestpractice.com
The papular variant has pinpoint size lesions (1-3 mm in diameter) is also quite common, hemorrhagic manifestations occur less frequently.[1]Holzle E, Plewig G, von Kries R, et al. Polymorphous light eruption. J Invest Dermatol. 1987;88(3 Suppl):32s-8.
http://www.ncbi.nlm.nih.gov/pubmed/3819473?tool=bestpractice.com
[2]Kontos AP, Cusack CA, Chaffins M, et al. Polymorphous light eruption in African Americans: pinpoint papular variant. Photodermatol Photoimmunol Photomed. 2002 Dec;18(6):303-6.
http://www.ncbi.nlm.nih.gov/pubmed/12535026?tool=bestpractice.com
[3]Bansal I, Kerr H, Janiga JJ, et al. Pinpoint papular variant of polymorphous light eruption: clinical and pathological. Eur Acad Dermatol Venereol. 2006 Apr;20(4):406-10.
http://www.ncbi.nlm.nih.gov/pubmed/16643137?tool=bestpractice.com
The subtype of the second most common, plaque type, of PLE is erythema exudativum multiforme, which forms figurate, cockaded lesions.[4]Calzavara Pinton PG, Venturini M, Capezzera R, et al. Photosensitive erythema multiforme and erythema multiforme-like polymorphous light eruption. Photodermatol Photoimmunol Photomed. 2003 Jun;19(3):157-9.
http://www.ncbi.nlm.nih.gov/pubmed/12914602?tool=bestpractice.com
The ictus or insect bite-like variant belongs to the papular-vesicular group of PLE.[5]Elpern DJ, Morison WL, Hood AF. Papulovesicular light eruption. A defined subset of polymorphous light eruption. Arch Dermatol. 1985 Oct;121(10):1286-8.
http://www.ncbi.nlm.nih.gov/pubmed/4037822?tool=bestpractice.com
[6]Diepgen TL, Haberle M, Fartasch M, et al. Characteristics of polymorphous light dermatosis - results of a prospective survey and study of 302 affected patients. Z Hautkr. 1989 Apr 15;64(4):279-80, 283-5.
http://www.ncbi.nlm.nih.gov/pubmed/2735085?tool=bestpractice.com
It is characterized by a central vesicle surrounded by multiple urticarial papules. The vesiculobullous type is a rare variant that appears as a mix of papules and bullae.[7]Neumann NJ, Holzle E, Lehmann P. Polymorphous light dermatoses. J Dtsch Dermatol Ges. 2004 Mar;2(3):220-4, 226.
http://www.ncbi.nlm.nih.gov/pubmed/16281641?tool=bestpractice.com
Although PLE appears in distinct (polymorphous) variants and differs between people, in each patient the clinical picture is monomorphous: that is, restricted to one of the variants.[1]Holzle E, Plewig G, von Kries R, et al. Polymorphous light eruption. J Invest Dermatol. 1987;88(3 Suppl):32s-8.
http://www.ncbi.nlm.nih.gov/pubmed/3819473?tool=bestpractice.com
[6]Diepgen TL, Haberle M, Fartasch M, et al. Characteristics of polymorphous light dermatosis - results of a prospective survey and study of 302 affected patients. Z Hautkr. 1989 Apr 15;64(4):279-80, 283-5.
http://www.ncbi.nlm.nih.gov/pubmed/2735085?tool=bestpractice.com
PLE only affects sun-exposed areas; dissemination occurs very rarely.[8]Guarrera M, Micalizzi C, Rebora A. Heterogeneity of polymorphous light eruption: a study of 105 patients. Arch Dermatol. 1993 Aug;129(8):1060-1.
http://www.ncbi.nlm.nih.gov/pubmed/8352615?tool=bestpractice.com
Predilection sites (in decreasing frequency) are the throat, V-shaped neck area, extensor surfaces of the arms, hands, legs, and face.[9]Berg M. Epidemiological studies of the influence of sunlight on the skin. Photodermatology. 1989 Apr;6(2):80-4.
http://www.ncbi.nlm.nih.gov/pubmed/2748434?tool=bestpractice.com
[10]Dummer R, Ivanova K, Scheidegger EP, et al. Clinical and therapeutic aspects of polymorphous light eruption. Dermatology. 2003;207(1):93-5.
http://www.ncbi.nlm.nih.gov/pubmed/12835565?tool=bestpractice.com
[11]Jansen CT. The natural history of polymorphous light eruptions. Arch Dermatol. 1979 Feb;115(2):165-9.
http://www.ncbi.nlm.nih.gov/pubmed/426521?tool=bestpractice.com
In children, the face is more frequently affected.[1]Holzle E, Plewig G, von Kries R, et al. Polymorphous light eruption. J Invest Dermatol. 1987;88(3 Suppl):32s-8.
http://www.ncbi.nlm.nih.gov/pubmed/3819473?tool=bestpractice.com
Juvenile spring eruption (JSE) is characterized by a papulovesicular rash affecting young males and is suggested to be a subtype of PLE.[12]Stratigos AJ, Antoniou C, Papadakis P, et al. Juvenile spring eruption: clinicopathologic features and phototesting results in 4 cases. J Am Acad Dermatol. 2004 Feb;50(2 Suppl):S57-60.
http://www.ncbi.nlm.nih.gov/pubmed/14726868?tool=bestpractice.com
[13]Lava SA, Simonetti GD, Ragazzi M,et al. Juvenile spring eruption: an outbreak report and systematic review of the literature. Br J Dermatol. 2013 May;168(5):1066-72.
http://www.ncbi.nlm.nih.gov/pubmed/23374016?tool=bestpractice.com