The overall mortality from OP is about 5%.[3]Epler GR. Bronchiolitis obliterans organizing pneumonia, 25 years: a variety of causes, but what are the treatment options? Expert Rev Respir Med. 2011 Jun;5(3):353-61.
http://www.ncbi.nlm.nih.gov/pubmed/21702658?tool=bestpractice.com
[6]Chang J, Han J, Kim DW, et al. Bronchiolitis obliterans organizing pneumonia: clinicopathologic review of a series of 45 Korean patients including rapidly progressive form. J Korean Med Sci. 2002 Apr;17(2):179-86.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3054867
http://www.ncbi.nlm.nih.gov/pubmed/11961300?tool=bestpractice.com
[8]Oymak FS, Demirbas HM, Mavili E, et al. Bronchiolitis obliterans organizing pneumonia: clinical and roentgenological features in 26 cases. Respiration. 2005 May-Jun;72(3):254-62.
http://www.ncbi.nlm.nih.gov/pubmed/15942294?tool=bestpractice.com
However, patients with rapidly progressive OP have a mortality of about 25%. Rapid diagnosis and initiation of corticosteroids are particularly critical in patients with rapidly progressive OP, to avoid death from a potentially treatable lesion.