The incidence of mucormycosis is significantly lower than those of invasive Candida or Aspergillus infections, by about 10- to 50-fold.[3]Spellberg B, Edwards J Jr, Ibrahim A. Novel perspectives on mucormycosis: pathophysiology, presentation, and management. Clin Microbiol Rev. 2005 Jul;18(3):556-69.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1195964
http://www.ncbi.nlm.nih.gov/pubmed/16020690?tool=bestpractice.com
Estimating exact case numbers and trends for mucormycosis is challenging, as most epidemiological data rely on case reports and case series rather than comprehensive surveillance.[8]Gouzien L, Che D, Cassaing S, et al. Epidemiology and prognostic factors of mucormycosis in France (2012-2022): a cross-sectional study nested in a prospective surveillance programme. Lancet Reg Health Eur. 2024 Oct;45:101010.
https://pmc.ncbi.nlm.nih.gov/articles/PMC11363841
http://www.ncbi.nlm.nih.gov/pubmed/39220434?tool=bestpractice.com
However, there has been an increase in the incidence of mucormycosis in regions such as Europe and India, which may reflect a growing population of at-risk individuals, improved awareness, and advancements in diagnostic tools.[8]Gouzien L, Che D, Cassaing S, et al. Epidemiology and prognostic factors of mucormycosis in France (2012-2022): a cross-sectional study nested in a prospective surveillance programme. Lancet Reg Health Eur. 2024 Oct;45:101010.
https://pmc.ncbi.nlm.nih.gov/articles/PMC11363841
http://www.ncbi.nlm.nih.gov/pubmed/39220434?tool=bestpractice.com
[9]Skiada A, Pavleas I, Drogari-Apiranthitou M. Epidemiology and diagnosis of mucormycosis: an update. J Fungi (Basel). 2020 Nov 2;6(4):265.
https://pmc.ncbi.nlm.nih.gov/articles/PMC7711598
http://www.ncbi.nlm.nih.gov/pubmed/33147877?tool=bestpractice.com
The estimated incidence in the US is about 1.7 cases per million per year, or 500 cases annually.[3]Spellberg B, Edwards J Jr, Ibrahim A. Novel perspectives on mucormycosis: pathophysiology, presentation, and management. Clin Microbiol Rev. 2005 Jul;18(3):556-69.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1195964
http://www.ncbi.nlm.nih.gov/pubmed/16020690?tool=bestpractice.com
[10]Roilides E, Zaoutis TE, Walsh TJ. Invasive zygomycosis in neonates and children. Clin Microbiol Infect. 2009 Oct;15(suppl 5):50-4.
http://www.ncbi.nlm.nih.gov/pubmed/19754758?tool=bestpractice.com
This disease is more commonly encountered in the immunosuppressed population, but cases in immunocompetent hosts have been described with organisms in the order Entomophthorales.[11]Shaikh N, Hussain KA, Petraitiene R, et al. Entomophthoramycosis: a neglected tropical mycosis. Clin Microbiol Infect. 2016 Aug;22(8):688-94.
https://www.clinicalmicrobiologyandinfection.com/article/S1198-743X(16)30062-3/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/27109491?tool=bestpractice.com
The most vulnerable hosts are those with diabetes mellitus (with or without ketoacidosis), haematological malignancies, solid organ or bone marrow transplants, history of corticosteroid use, and graft-versus-host disease.[4]Centers for Disease Control and Prevention. Mucormycosis: clinical overview of mucormycosis. Apr 2024 [internet publication].
https://www.cdc.gov/mucormycosis/hcp/clinical-overview/index.html
[12]Cornely OA, Alastruey-Izquierdo A, Arenz D, et al. Global guideline for the diagnosis and management of mucormycosis: an initiative of the European Confederation of Medical Mycology in cooperation with the Mycoses Study Group Education and Research Consortium. Lancet Infect Dis. 2019 Dec;19(12):e405-21.
https://pmc.ncbi.nlm.nih.gov/articles/PMC8559573
http://www.ncbi.nlm.nih.gov/pubmed/31699664?tool=bestpractice.com
[13]Lamoth F. Novel approaches in the management of mucormycosis. Curr Fungal Infect Rep. 2023 May 8:1-10.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10165581
http://www.ncbi.nlm.nih.gov/pubmed/37360854?tool=bestpractice.com
Prematurity is a major underlying factor for acquiring the disease in neonates.[14]Francis JR, Villanueva P, Bryant P, et al. Mucormycosis in children: review and recommendations for management. J Pediatric Infect Dis Soc. 2018 May 15;7(2):159-64.
https://academic.oup.com/jpids/article-abstract/7/2/159/4780392
http://www.ncbi.nlm.nih.gov/pubmed/29294067?tool=bestpractice.com
Gastrointestinal and cutaneous disease is more common in neonates than in older children and adults. Neonates are also at increased risk for disseminated disease. Overall mortality is 64% in neonates compared with 56% in children more than a month old and less than 18 years of age. Disseminated infection and age less than 12 months are independent risk factors for increased mortality.[10]Roilides E, Zaoutis TE, Walsh TJ. Invasive zygomycosis in neonates and children. Clin Microbiol Infect. 2009 Oct;15(suppl 5):50-4.
http://www.ncbi.nlm.nih.gov/pubmed/19754758?tool=bestpractice.com
In adults, rhino-orbito-cerebral disease is the most common presentation (44% to 49%), followed by cutaneous (10% to 16%), pulmonary (10% to 11%), disseminated (6% to 11.6%), and gastrointestinal (2% to 11%).[15]Prabhu RM, Patel R. Mucormycosis and entomophthoramycosis: a review of the clinical manifestations, diagnosis and treatment. Clin Microbiol Infect. 2004 Mar;10(suppl 1):31-47.
http://onlinelibrary.wiley.com/doi/10.1111/j.1470-9465.2004.00843.x/full
http://www.ncbi.nlm.nih.gov/pubmed/14748801?tool=bestpractice.com
Rhino-orbito-cerebral is more common in patients with diabetes, whereas pulmonary manifestation is more typical of patients with haematological malignancies or transplants. The incidence in a study over a 10-year period among transplant recipients, per 1000 patients, was 0.4 to 0.5 in renal transplant recipients, 8 in heart transplant recipients, 4 to 6 in liver transplant recipients, and 13.7 to 14 in lung transplant recipients.[3]Spellberg B, Edwards J Jr, Ibrahim A. Novel perspectives on mucormycosis: pathophysiology, presentation, and management. Clin Microbiol Rev. 2005 Jul;18(3):556-69.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1195964
http://www.ncbi.nlm.nih.gov/pubmed/16020690?tool=bestpractice.com
Most cases of mucormycosis are sporadic, though rare outbreaks have occurred in healthcare settings, often linked to non-sterile products such as contaminated bandages, linens, drugs, and food.[4]Centers for Disease Control and Prevention. Mucormycosis: clinical overview of mucormycosis. Apr 2024 [internet publication].
https://www.cdc.gov/mucormycosis/hcp/clinical-overview/index.html
[9]Skiada A, Pavleas I, Drogari-Apiranthitou M. Epidemiology and diagnosis of mucormycosis: an update. J Fungi (Basel). 2020 Nov 2;6(4):265.
https://pmc.ncbi.nlm.nih.gov/articles/PMC7711598
http://www.ncbi.nlm.nih.gov/pubmed/33147877?tool=bestpractice.com
[16]Centers for Disease Control and Prevention. Mucormycosis risk factors. Apr 2024 [internet publication].
https://www.cdc.gov/mucormycosis/risk-factors/index.html
[17]Jordan A, James AE, Gold JAW, et al. Investigation of a prolonged and large outbreak of healthcare-associated mucormycosis cases in an Acute Care Hospital-Arkansas, June 2019-May 2021. Open Forum Infect Dis. 2022 Oct;9(10):ofac510.
https://pmc.ncbi.nlm.nih.gov/articles/PMC9605704
http://www.ncbi.nlm.nih.gov/pubmed/36320193?tool=bestpractice.com
Invasive procedures such as surgery, dental extractions, and tube insertions, as well as medical devices like insulin pumps, finger sticks, and ostomy bags, have also been implicated in transmission.[9]Skiada A, Pavleas I, Drogari-Apiranthitou M. Epidemiology and diagnosis of mucormycosis: an update. J Fungi (Basel). 2020 Nov 2;6(4):265.
https://pmc.ncbi.nlm.nih.gov/articles/PMC7711598
http://www.ncbi.nlm.nih.gov/pubmed/33147877?tool=bestpractice.com
Outbreaks have also been reported following natural disasters, likely due to increased environmental exposure to fungal spores.[4]Centers for Disease Control and Prevention. Mucormycosis: clinical overview of mucormycosis. Apr 2024 [internet publication].
https://www.cdc.gov/mucormycosis/hcp/clinical-overview/index.html
[18]Benedict K, Park BJ. Invasive fungal infections after natural disasters. Emerg Infect Dis. 2014 Mar;20(3):349-55.
https://pmc.ncbi.nlm.nih.gov/articles/PMC3944874
http://www.ncbi.nlm.nih.gov/pubmed/24565446?tool=bestpractice.com
Mucormycosis has been increasingly reported in patients with coronavirus disease 2019 (COVID-19), particularly in patients who have diabetes mellitus and have also received corticosteroids.[19]Moorthy A, Gaikwad R, Krishna S, et al. SARS-CoV-2, uncontrolled diabetes and corticosteroids-an unholy trinity in invasive fungal infections of the maxillofacial region? A retrospective, multi-centric analysis. J Maxillofac Oral Surg. 2021 Mar 6;1-8.
https://link.springer.com/article/10.1007/s12663-021-01532-1
http://www.ncbi.nlm.nih.gov/pubmed/33716414?tool=bestpractice.com
[20]John TM, Jacob CN, Kontoyiannis DP. When uncontrolled diabetes mellitus and severe COVID-19 converge: the perfect storm for mucormycosis. J Fungi (Basel). 2021 Apr 15;7(4):2021 Apr 15;7(4):298.
https://www.mdpi.com/2309-608X/7/4/298/htm
http://www.ncbi.nlm.nih.gov/pubmed/33920755?tool=bestpractice.com
[21]Özbek L, Topçu U, Manay M, et al. COVID-19-associated mucormycosis: a systematic review and meta-analysis of 958 cases. Clin Microbiol Infect. 2023 Jun;29(6):722-31.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10008766
http://www.ncbi.nlm.nih.gov/pubmed/36921716?tool=bestpractice.com
[22]Kuehn BM. Cluster of mucormycosis cases linked with delta surge. JAMA. 2022 Feb 8;327(6):518.[23]Mejía-Santos H, Montoya S, Chacón-Fuentes R, et al. Notes from the field: mucormycosis cases during the COVID-19 pandemic - Honduras, May-September 2021. MMWR Morb Mortal Wkly Rep. 2021 Dec 17;70(50):1747-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC8675660
http://www.ncbi.nlm.nih.gov/pubmed/34914675?tool=bestpractice.com
[24]Dulski TM, DeLong M, Garner K, et al. Notes from the field: COVID-19-associated mucormycosis - Arkansas, July-September 2021. MMWR Morb Mortal Wkly Rep. 2021 Dec 17;70(50):1750-1.
https://pmc.ncbi.nlm.nih.gov/articles/PMC8675658
[25]Joshi S, Telang R, Tambe M, et al. Outbreak of mucormycosis in coronavirus disease patients, Pune, India. Emerg Infect Dis. 2022 Jan;28(1):1-8.
https://pmc.ncbi.nlm.nih.gov/articles/PMC8714213
http://www.ncbi.nlm.nih.gov/pubmed/34586055?tool=bestpractice.com