Metabolic dysfunction-associated steatotic liver (MASL) has a benign course and does not warrant treatment beyond lifestyle modification. Because metabolic dysfunction-associated steatohepatitis (MASH) has the potential to progress to cirrhosis in a significant number of patients, pharmacological treatment may be considered in those with more advanced disease on biopsy. Several treatments improve liver enzyme abnormalities, radiographic findings, and histological disease progression. However, there are no data that demonstrate improvement in morbidity or mortality. Effective treatment options are needed to prevent future disease-related morbidity and mortality.
Management of steatosis should be individualised and should target relevant modifiable risk factors.
Weight loss through lifestyle modification
Dietary modifications, physical activity, and weight loss are first-line therapy in patients with metabolic dysfunction-associated steatotic liver disease (MASLD).[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
A diet rich in fresh fruit and vegetables, fibre, and omega-3 polyunsaturated fatty acids is recommended. A calorie-deficit diet is recommended for patients with MASLD who are overweight or obese.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
Patients should reduce intake of sugar-sweetened beverages and highly processed foods.[69]Chitturi S, Wong VW, Chan WK, et al. The Asia-Pacific Working Party on Non-alcoholic Fatty Liver Disease guidelines 2017 - part 2: management and special groups. J Gastroenterol Hepatol. 2018 Jan;33(1):86-98.
https://www.doi.org/10.1111/jgh.13856
http://www.ncbi.nlm.nih.gov/pubmed/28692197?tool=bestpractice.com
Weight loss causes a loss of adipose tissue that leads to reduced insulin resistance and improved muscular insulin sensitivity. Studies have shown variable improvement in liver enzymes with weight loss, with some also showing an improvement in histology.[70]Thoma C, Day CP, Trenell MI. Lifestyle interventions for the treatment of non-alcoholic fatty liver disease in adults: a systematic review. J Hepatol. 2012 Jan;56(1):255-66.
https://www.journal-of-hepatology.eu/article/S0168-8278(11)00509-5/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/21723839?tool=bestpractice.com
[71]Keating SE, Hackett DA, George J, et al. Exercise and non-alcoholic fatty liver disease: a systematic review and meta-analysis. J Hepatol. 2012 Jul;57(1):157-66.
http://www.ncbi.nlm.nih.gov/pubmed/22414768?tool=bestpractice.com
[72]Younossi ZM, Reyes MJ, Mishra A, et al. Systematic review with meta-analysis: non-alcoholic steatohepatitis - a case for personalised treatment based on pathogenic targets. Aliment Pharmacol Ther. 2014 Jan;39(1):3-14.
https://onlinelibrary.wiley.com/doi/full/10.1111/apt.12543
http://www.ncbi.nlm.nih.gov/pubmed/24206433?tool=bestpractice.com
Weight loss should be gradual, approximately 0.5 to 1.0 kg per week through dietary alterations (restriction of carbohydrates and saturated fats with a 500 to 1000 kcal/day caloric deficit) and regular aerobic exercise (30 minutes 3-5 times per week).[73]Zelber-Sagi S, Kessler A, Brazowsky E, et al. A double-blind randomized placebo-controlled trial of orlistat for the treatment of nonalcoholic fatty liver disease. Clin Gastroenterol Hepatol. 2006 May;4(5):639-44.
http://www.ncbi.nlm.nih.gov/pubmed/16630771?tool=bestpractice.com
Patients should be cautioned not to lose too much weight quickly, as the development of portal inflammation and fibrosis may occur in patients who lose >1.5 kg per week.[74]Zeng MD, Fan JG, Lu LG, et al. Guidelines for the diagnosis and treatment of nonalcoholic fatty liver diseases. J Dig Dis. 2008 May;9(2):108-12.
http://www.ncbi.nlm.nih.gov/pubmed/18419645?tool=bestpractice.com
Improvement in SLD has been demonstrated in patients able to lose 3% to 5% of total body weight.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
Moreover, ≥10% weight loss has been associated with improvement in all histological features of MASH including portal inflammation and fibrosis.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
[21]Cusi K, Isaacs S, Barb D, et al. American Association of Clinical Endocrinology clinical practice guideline for the diagnosis and management of nonalcoholic fatty liver disease in primary care and endocrinology clinical settings: co-sponsored by the American Association for the Study of Liver Diseases (AASLD). Endocr Pract. 2022 May;28(5):528-62.
https://www.endocrinepractice.org/article/S1530-891X(22)00090-8/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/35569886?tool=bestpractice.com
[75]Vilar-Gomez E, Martinez-Perez Y, Calzadilla-Bertot L, et al. Weight loss through lifestyle modification significantly reduces features of nonalcoholic steatohepatitis. Gastroenterology. 2015 Aug;149(2):367-78.e5; quiz e14-5.
https://www.doi.org/10.1053/j.gastro.2015.04.005
http://www.ncbi.nlm.nih.gov/pubmed/25865049?tool=bestpractice.com
Weight loss is also associated with improvement in glucose metabolism and plasma lipid profile in patients with MASLD.[76]Musso G, Cassader M, Rosina F, et al. Impact of current treatments on liver disease, glucose metabolism and cardiovascular risk in non-alcoholic fatty liver disease (NAFLD): a systematic review and meta-analysis of randomised trials. Diabetologia. 2012 Apr;55(4):885-904.
https://www.doi.org/10.1007/s00125-011-2446-4
http://www.ncbi.nlm.nih.gov/pubmed/22278337?tool=bestpractice.com
Physical activity recommendations should be individualised to the patient.[41]European Association for the Study of the Liver (EASL), European Association for the Study of Diabetes (EASD), European Association for the Study of Obesity (EASO). EASL-EASD-EASO clinical practice guidelines for the management of non-alcoholic fatty liver disease. J Hepatol. 2016 Jun;64(6):1388-402.
https://www.doi.org/10.1016/j.jhep.2015.11.004
http://www.ncbi.nlm.nih.gov/pubmed/27062661?tool=bestpractice.com
Both aerobic activity and progressive resistance training are associated with a reduction of liver fat, even without weight loss.[71]Keating SE, Hackett DA, George J, et al. Exercise and non-alcoholic fatty liver disease: a systematic review and meta-analysis. J Hepatol. 2012 Jul;57(1):157-66.
http://www.ncbi.nlm.nih.gov/pubmed/22414768?tool=bestpractice.com
[77]Bacchi E, Negri C, Targher G, et al. Both resistance training and aerobic training reduce hepatic fat content in type 2 diabetic subjects with nonalcoholic fatty liver disease (the RAED2 Randomized Trial). Hepatology. 2013 Oct;58(4):1287-95.
https://www.doi.org/10.1002/hep.26393
http://www.ncbi.nlm.nih.gov/pubmed/23504926?tool=bestpractice.com
Increasing physical activity to ≥150 minutes per week is associated with greater improvements in liver enzymes.[78]St George A, Bauman A, Johnston A, et al. Independent effects of physical activity in patients with nonalcoholic fatty liver disease. Hepatology. 2009 Jul;50(1):68-76.
https://www.doi.org/10.1002/hep.22940
http://www.ncbi.nlm.nih.gov/pubmed/19444870?tool=bestpractice.com
One meta-analysis examined randomised controlled trials (RCTs) of lifestyle interventions, compared with usual care, for patients with MASLD. Most RCTs identified were at high risk of bias. The follow-up periods ranged from 2 to 24 months, so data on clinical events related to MASLD were sparse, and there was significant uncertainty about the effects of the intervention. High-quality RCTs with adequate follow-up (at least 8 years) are recommended.[79]Buzzetti E, Linden A, Best LM, et al. Lifestyle modifications for nonalcohol-related fatty liver disease: a network meta-analysis. Cochrane Database Syst Rev. 2021 Jun 11;6:CD013156.
https://www.doi.org/10.1002/14651858.CD013156.pub2
http://www.ncbi.nlm.nih.gov/pubmed/34114650?tool=bestpractice.com
Any level of alcohol use may be harmful to liver health in patients with MASLD.[80]Jarvis H, O'Keefe H, Craig D, et al. Does moderate alcohol consumption accelerate the progression of liver disease in NAFLD? A systematic review and narrative synthesis. BMJ Open. 2022 Jan 4;12(1):e049767.
https://www.doi.org/10.1136/bmjopen-2021-049767
http://www.ncbi.nlm.nih.gov/pubmed/34983755?tool=bestpractice.com
Patients should be counselled to abstain or keep alcohol intake below the risk threshold.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
[41]European Association for the Study of the Liver (EASL), European Association for the Study of Diabetes (EASD), European Association for the Study of Obesity (EASO). EASL-EASD-EASO clinical practice guidelines for the management of non-alcoholic fatty liver disease. J Hepatol. 2016 Jun;64(6):1388-402.
https://www.doi.org/10.1016/j.jhep.2015.11.004
http://www.ncbi.nlm.nih.gov/pubmed/27062661?tool=bestpractice.com
[80]Jarvis H, O'Keefe H, Craig D, et al. Does moderate alcohol consumption accelerate the progression of liver disease in NAFLD? A systematic review and narrative synthesis. BMJ Open. 2022 Jan 4;12(1):e049767.
https://www.doi.org/10.1136/bmjopen-2021-049767
http://www.ncbi.nlm.nih.gov/pubmed/34983755?tool=bestpractice.com
Weight loss through pharmacological agents or surgery
Orlistat is an enteric lipase inhibitor that prevents the absorption of fats from the gastrointestinal tract. Systematic reviews suggest that orlistat may improve biochemical indicators of liver damage, but its effect on liver histology remains unclear.[72]Younossi ZM, Reyes MJ, Mishra A, et al. Systematic review with meta-analysis: non-alcoholic steatohepatitis - a case for personalised treatment based on pathogenic targets. Aliment Pharmacol Ther. 2014 Jan;39(1):3-14.
https://onlinelibrary.wiley.com/doi/full/10.1111/apt.12543
http://www.ncbi.nlm.nih.gov/pubmed/24206433?tool=bestpractice.com
[81]Wang H, Wang L, Cheng Y, et al. Efficacy of orlistat in non-alcoholic fatty liver disease: A systematic review and meta-analysis. Biomed Rep. 2018 Jul;9(1):90-6.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6007047
http://www.ncbi.nlm.nih.gov/pubmed/29930810?tool=bestpractice.com
Patients with a BMI >40 kg/m² or patients with a BMI >35 kg/m², and at least one or more obesity-related comorbidity, should be considered for bariatric surgery, which facilitates sustained weight loss. An overwhelming majority of patients undergoing bariatric surgery will have MASLD.[82]Xanthakos SA, Jenkins TM, Kleiner DE, et al. High prevalence of nonalcoholic fatty liver disease in adolescents undergoing bariatric surgery. Gastroenterology. 2015 Sep;149(3):623-34;e8.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4654456
http://www.ncbi.nlm.nih.gov/pubmed/26026390?tool=bestpractice.com
The American Association for the Study of Liver Diseases (AASLD) recommends bariatric surgery in patients meeting the criteria for metabolic weight loss surgery.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
In patients with MASLD, roux-en-Y gastric bypass demonstrated significant improvement in both steatosis and fibrosis.[83]Fakhry TK, Mhaskar R, Schwitalla T, et al. Bariatric surgery improves nonalcoholic fatty liver disease: a contemporary systematic review and meta-analysis. Surg Obes Relat Dis. 2019 Mar;15(3):502-11.
http://www.ncbi.nlm.nih.gov/pubmed/30683512?tool=bestpractice.com
One systematic review reported biopsy-confirmed resolution of steatosis in 66% of patients with MASLD following bariatric surgery.[84]Lee Y, Doumouras AG, Yu J, et al. Complete resolution of nonalcoholic fatty liver disease after bariatric surgery: a systematic review and meta-analysis. Clin Gastroenterol Hepatol. 2019 May;17(6):1040-60;e11.
https://www.cghjournal.org/article/S1542-3565(18)31138-8/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/30326299?tool=bestpractice.com
Randomised controlled trials (RCTs) comparing bariatric surgery with any intervention in patients with MASLD are, however, rare; most data are derived from observational studies.[83]Fakhry TK, Mhaskar R, Schwitalla T, et al. Bariatric surgery improves nonalcoholic fatty liver disease: a contemporary systematic review and meta-analysis. Surg Obes Relat Dis. 2019 Mar;15(3):502-11.
http://www.ncbi.nlm.nih.gov/pubmed/30683512?tool=bestpractice.com
[84]Lee Y, Doumouras AG, Yu J, et al. Complete resolution of nonalcoholic fatty liver disease after bariatric surgery: a systematic review and meta-analysis. Clin Gastroenterol Hepatol. 2019 May;17(6):1040-60;e11.
https://www.cghjournal.org/article/S1542-3565(18)31138-8/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/30326299?tool=bestpractice.com
[85]Chavez-Tapia NC, Tellez-Avila FI, Barrientos-Gutierrez T, et al. Bariatric surgery for non-alcoholic steatohepatitis in obese patients. Cochrane Database Syst Rev. 2010 Jan 20;(1):CD007340.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD007340.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/20091629?tool=bestpractice.com
Patients need to be selected cautiously and evaluated thoroughly for obesity-related comorbidities and cirrhosis. Patients with cirrhosis need to be risk stratified by a hepatologist prior to surgery. Patients should also be followed carefully after surgery, as a minority may develop worsening steatohepatitis or mild fibrosis.
Thiazolidinediones
Meta-analyses have found that pioglitazone improves liver histological scores in patients with MASLD.[86]Boettcher E, Csako G, Pucino F, et al. Meta-analysis: pioglitazone improves liver histology and fibrosis in patients with non-alcoholic steatohepatitis. Aliment Pharmacol Ther. 2012 Jan;35(1):66-75.
http://onlinelibrary.wiley.com/doi/10.1111/j.1365-2036.2011.04912.x/full
http://www.ncbi.nlm.nih.gov/pubmed/22050199?tool=bestpractice.com
[87]Said A, Akhter A. Meta-analysis of randomized controlled trials of pharmacologic agents in non-alcoholic steatohepatitis. Ann Hepatol. 2017 Jul-Aug;16(4):538-47.
http://www.ncbi.nlm.nih.gov/pubmed/28611274?tool=bestpractice.com
[88]Sawangjit R, Chongmelaxme B, Phisalprapa P, et al. Comparative efficacy of interventions on nonalcoholic fatty liver disease (NAFLD): a PRISMA-compliant systematic review and network meta-analysis. Medicine (Baltimore). 2016 Aug;95(32):e4529.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4985329
http://www.ncbi.nlm.nih.gov/pubmed/27512874?tool=bestpractice.com
[89]Mahady SE, Webster AC, Walker S, et al. The role of thiazolidinediones in non-alcoholic steatohepatitis: a systematic review and meta analysis. J Hepatol. 2011 Dec;55(6):1383-90.
http://www.ncbi.nlm.nih.gov/pubmed/21703200?tool=bestpractice.com
[90]Mantovani A, Byrne CD, Targher G. Efficacy of peroxisome proliferator-activated receptor agonists, glucagon-like peptide-1 receptor agonists, or sodium-glucose cotransporter-2 inhibitors for treatment of non-alcoholic fatty liver disease: a systematic review. Lancet Gastroenterol Hepatol. 2022 Apr;7(4):367-78.
http://www.ncbi.nlm.nih.gov/pubmed/35030323?tool=bestpractice.com
Long-term treatment may be required as beneficial effects seem to reverse after discontinuation.[91]Lutchman G, Modi A, Kleiner DE, et al. The effects of discontinuing pioglitazone in patients with nonalcoholic steatohepatitis. Hepatology. 2007 Aug;46(2):424-9.
http://onlinelibrary.wiley.com/doi/10.1002/hep.21661/full
http://www.ncbi.nlm.nih.gov/pubmed/17559148?tool=bestpractice.com
Pioglitazone is generally well tolerated, but adverse effects typical of thiazolidinediones (universal weight gain [2-5 kg], osteoporosis in postmenopausal women on long-term therapy, and lower extremity oedema) can limit its use.[92]Musso G, Cassader M, Paschetta E, et al. Thiazolidinediones and advanced liver fibrosis in nonalcoholic steatohepatitis: a meta-analysis. JAMA Intern Med. 2017 May 1;177(5):633-40.
https://www.doi.org/10.1001/jamainternmed.2016.9607
http://www.ncbi.nlm.nih.gov/pubmed/28241279?tool=bestpractice.com
[93]McDonough AK, Rosenthal RS, Cao X, et al. The effect of thiazolidinediones on BMD and osteoporosis. Nat Clin Pract Endocrinol Metab. 2008 Sep;4(9):507-13.
http://www.ncbi.nlm.nih.gov/pubmed/18695700?tool=bestpractice.com
Congestive heart failure has rarely been reported with thiazolidinediones.[94]Lago RM, Singh PP, Nesto RW. Congestive heart failure and cardiovascular death in patients with prediabetes and type 2 diabetes given thiazolidinediones: a meta-analysis of randomised clinical trials. Lancet. 2007 Sep 29;370(9593):1129-36.
http://www.ncbi.nlm.nih.gov/pubmed/17905165?tool=bestpractice.com
US and European Guidelines recommend that treatment with pioglitazone may be considered for patients with biopsy-proven MASH with and without type 2 diabetes mellitus. The risks and benefits should be discussed with each patient before starting therapy.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
[41]European Association for the Study of the Liver (EASL), European Association for the Study of Diabetes (EASD), European Association for the Study of Obesity (EASO). EASL-EASD-EASO clinical practice guidelines for the management of non-alcoholic fatty liver disease. J Hepatol. 2016 Jun;64(6):1388-402.
https://www.doi.org/10.1016/j.jhep.2015.11.004
http://www.ncbi.nlm.nih.gov/pubmed/27062661?tool=bestpractice.com
Use of pioglitazone for this indication is off-label. Data regarding pioglitazone use in Asian patients are lacking. Asia-Pacific guidelines advise it may be used short-term in patients with pre-diabetes or type 2 diabetes, following a careful assessment of comorbid conditions that may influence its suitability for the patient.[69]Chitturi S, Wong VW, Chan WK, et al. The Asia-Pacific Working Party on Non-alcoholic Fatty Liver Disease guidelines 2017 - part 2: management and special groups. J Gastroenterol Hepatol. 2018 Jan;33(1):86-98.
https://www.doi.org/10.1111/jgh.13856
http://www.ncbi.nlm.nih.gov/pubmed/28692197?tool=bestpractice.com
Rosiglitazone decreases steatosis and aminotransferase levels in patients with MASH. It has been associated with improvement in histological features of MASH in some trials; however, results are conflicting.[95]Ratziu V, Giral P, Jacqueminet S, et al. Rosiglitazone for nonalcoholic steatohepatitis: one-year results of the randomized placebo-controlled Fatty Liver Improvement with Rosiglitazone Therapy (FLIRT) trial. Gastroenterology. 2008;135:100-110.
http://www.ncbi.nlm.nih.gov/pubmed/18503774?tool=bestpractice.com
[96]Neuschwander-Tetri BA, Brunt EM, Wehmeier KR, et al. Improved nonalcoholic steatohepatitis after 48 weeks of treatment with the PPAR-gamma ligand rosiglitazone. Hepatology. 2003 Oct;38(4):1008-17.
http://www.ncbi.nlm.nih.gov/pubmed/14512888?tool=bestpractice.com
Rosiglitazone has been associated with serious adverse cardiovascular events in patients with type 2 diabetes.[97]Nissen SE, Wolski K. Effect of rosiglitazone on the risk of myocardial infarction and death from cardiovascular causes. N Engl J Med. 2007 Jun 14;356(24):2457-71.
http://www.nejm.org/doi/full/10.1056/NEJMoa072761#t=article
http://www.ncbi.nlm.nih.gov/pubmed/17517853?tool=bestpractice.com
For this reason, rosiglitazone has been withdrawn from the market in Europe. Although it is still available in some other locations, including the US, it is generally not recommended in practice.
Vitamin E
Meta-analyses indicate that vitamin E significantly improves liver function and histological changes in patients with MASLD/MASH.[87]Said A, Akhter A. Meta-analysis of randomized controlled trials of pharmacologic agents in non-alcoholic steatohepatitis. Ann Hepatol. 2017 Jul-Aug;16(4):538-47.
http://www.ncbi.nlm.nih.gov/pubmed/28611274?tool=bestpractice.com
[98]Sato K, Gosho M, Yamamoto T, et al. Vitamin E has a beneficial effect on nonalcoholic fatty liver disease: a meta-analysis of randomized controlled trials. Nutrition. 2015 Jul-Aug;31(7-8):923-30.
http://www.ncbi.nlm.nih.gov/pubmed/26059365?tool=bestpractice.com
[99]Ji HF, Sun Y, Shen L. Effect of vitamin E supplementation on aminotransferase levels in patients with NAFLD, NASH, and CHC: results from a meta-analysis. Nutrition. 2014 Sep;30(9):986-91.
http://www.ncbi.nlm.nih.gov/pubmed/24976430?tool=bestpractice.com
One subsequent study of 263 patients with biopsy-proven MASH and bridging fibrosis demonstrated that vitamin E was associated with improved clinical outcomes.[100]Vilar-Gomez E, Vuppalanchi R, Gawrieh S, et al. Vitamin E improves transplant-free survival and hepatic decompensation among patients with nonalcoholic steatohepatitis and advanced fibrosis. Hepatology. 2018 Dec 1.
http://www.ncbi.nlm.nih.gov/pubmed/30506586?tool=bestpractice.com
Meta-analyses have suggested that vitamin E supplementation may increase risk of mortality and haemorrhagic stroke.[101]Bjelakovic G, Nikolova D, Gluud LL, et al. Mortality in randomized trials of antioxidant supplements for primary and secondary prevention: systematic review and meta-analysis. JAMA. 2007 Feb 28;297(8):842-57.
http://www.ncbi.nlm.nih.gov/pubmed/17327526?tool=bestpractice.com
[102]Schürks M, Glynn RJ, Rist PM, et al. Effects of vitamin E on stroke subtypes: meta-analysis of randomised controlled trials. BMJ. 2010 Nov 4;341:c5702.
https://www.doi.org/10.1136/bmj.c5702
http://www.ncbi.nlm.nih.gov/pubmed/21051774?tool=bestpractice.com
One RCT reported an increased risk of prostate cancer in healthy men who took vitamin E, compared with placebo (hazard ratio 1.17, absolute risk increase 1.6 per 1000 person-years).[103]Klein EA, Thompson IM Jr, Tangen CM, et al. Vitamin E and the risk of prostate cancer: the Selenium and Vitamin E Cancer Prevention Trial (SELECT). JAMA. 2011 Oct 12;306(14):1549-56.
https://www.doi.org/10.1001/jama.2011.1437
http://www.ncbi.nlm.nih.gov/pubmed/21990298?tool=bestpractice.com
Vitamin E treatment may be considered for adults with biopsy-proven MASH who do not have diabetes or cirrhosis.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
[41]European Association for the Study of the Liver (EASL), European Association for the Study of Diabetes (EASD), European Association for the Study of Obesity (EASO). EASL-EASD-EASO clinical practice guidelines for the management of non-alcoholic fatty liver disease. J Hepatol. 2016 Jun;64(6):1388-402.
https://www.doi.org/10.1016/j.jhep.2015.11.004
http://www.ncbi.nlm.nih.gov/pubmed/27062661?tool=bestpractice.com
The risks and benefits should be discussed with each patient before starting therapy.
Vitamin E and pioglitazone may be given in combination.[41]European Association for the Study of the Liver (EASL), European Association for the Study of Diabetes (EASD), European Association for the Study of Obesity (EASO). EASL-EASD-EASO clinical practice guidelines for the management of non-alcoholic fatty liver disease. J Hepatol. 2016 Jun;64(6):1388-402.
https://www.doi.org/10.1016/j.jhep.2015.11.004
http://www.ncbi.nlm.nih.gov/pubmed/27062661?tool=bestpractice.com
Management of comorbid conditions
Patients with MASLD have an increased risk of fatal and non-fatal cardiovascular events, particularly if they have advanced fibrosis, independent of other cardiovascular risk factors.[104]Mantovani A, Csermely A, Petracca G, et al. Non-alcoholic fatty liver disease and risk of fatal and non-fatal cardiovascular events: an updated systematic review and meta-analysis. Lancet Gastroenterol Hepatol. 2021 Nov;6(11):903-13.
http://www.ncbi.nlm.nih.gov/pubmed/34555346?tool=bestpractice.com
In patients with MASLD without advanced fibrosis, cardiovascular disease and non-hepatic malignancies are the most common causes of death, whereas in patients with MASLD with advanced fibrosis, liver disease is the most common cause of death.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
Risk factors for cardiovascular disease should be sought and treated.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
[41]European Association for the Study of the Liver (EASL), European Association for the Study of Diabetes (EASD), European Association for the Study of Obesity (EASO). EASL-EASD-EASO clinical practice guidelines for the management of non-alcoholic fatty liver disease. J Hepatol. 2016 Jun;64(6):1388-402.
https://www.doi.org/10.1016/j.jhep.2015.11.004
http://www.ncbi.nlm.nih.gov/pubmed/27062661?tool=bestpractice.com
[51]McPherson S, Armstrong MJ, Cobbold JF, et al. Quality standards for the management of non-alcoholic fatty liver disease (NAFLD): consensus recommendations from the British Association for the Study of the Liver and British Society of Gastroenterology NAFLD Special Interest Group. Lancet Gastroenterol Hepatol. 2022 Aug;7(8):755-69.
https://www.thelancet.com/journals/langas/article/PIIS2468-1253(22)00061-9/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/35490698?tool=bestpractice.com
Post hoc analysis of a randomised study of patients with coronary heart disease suggests that statin treatment is safe and effective for primary prevention of cardiovascular disease in a group of patients with MASLD with mild to moderately elevated liver function tests.[105]Athyros VG, Tziomalos K, Gossios TD, et al. Safety and efficacy of long-term statin treatment for cardiovascular events in patients with coronary heart disease and abnormal liver tests in the Greek Atorvastatin and Coronary Heart Disease Evaluation (GREACE) Study: a post-hoc analysis. Lancet. 2010 Dec 4;376(9756):1916-22.
http://www.ncbi.nlm.nih.gov/pubmed/21109302?tool=bestpractice.com
Meta-analysis has shown that statin therapy is safe in patients with MASLD and mild elevations in liver enzymes.[106]Pastori D, Pani A, Di Rocco A, et al. Statin liver safety in non-alcoholic fatty liver disease: a systematic review and metanalysis. Br J Clin Pharmacol. 2022 Feb;88(2):441-51.
https://www.doi.org/10.1111/bcp.14943
http://www.ncbi.nlm.nih.gov/pubmed/34133035?tool=bestpractice.com
The AASLD recommends statins to reduce risk of cardiovascular events in patients with MASLD.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
Lipid-lowering therapy should be offered to patients with MASLD who meet current criteria.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
Statins should be used with caution in patients with acute liver failure or decompensated cirrhosis because of a theoretical risk of rhabdomyolysis.[107]Chalasani N. Statins and hepatotoxicity: focus on patients with fatty liver. Hepatology. 2005 Apr;41(4):690-5.
http://onlinelibrary.wiley.com/doi/10.1002/hep.20671/full
http://www.ncbi.nlm.nih.gov/pubmed/15789367?tool=bestpractice.com
Statins have been investigated as a treatment for MASLD and MASH. Study results are inconsistent and statin use solely to treat MASLD or MASH is not recommended.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
[108]Eslami L, Merat S, Malekzadeh R, et al. Statins for non-alcoholic fatty liver disease and non-alcoholic steatohepatitis. Cochrane Database Syst Rev. 2013 Dec 27;(12):CD008623.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD008623.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/24374462?tool=bestpractice.com
[109]Foster T, Budoff MJ, Saab S, et al. Atorvastatin and antioxidants for the treatment of nonalcoholic fatty liver disease: the St Francis Heart Study randomized clinical trial. Am J Gastroenterol. 2011;106:71-77.
http://www.nature.com/ajg/journal/v106/n1/full/ajg2010299a.html
http://www.ncbi.nlm.nih.gov/pubmed/20842109?tool=bestpractice.com
European guidelines mandate screening all patients diagnosed with MASLD for type 2 diabetes mellitus. Patients who are diagnosed with diabetes should be referred to a diabetes clinic to optimise management.[41]European Association for the Study of the Liver (EASL), European Association for the Study of Diabetes (EASD), European Association for the Study of Obesity (EASO). EASL-EASD-EASO clinical practice guidelines for the management of non-alcoholic fatty liver disease. J Hepatol. 2016 Jun;64(6):1388-402.
https://www.doi.org/10.1016/j.jhep.2015.11.004
http://www.ncbi.nlm.nih.gov/pubmed/27062661?tool=bestpractice.com
Metformin may be used as the first-line antidiabetic drug in patients with MASLD and type 2 diabetes. It leads to weight reduction, and reduced glycosylated haemoglobin and fasting plasma glucose, in patients with MASLD.[110]Shyangdan D, Clar C, Ghouri N, et al. Insulin sensitisers in the treatment of non-alcoholic fatty liver disease: a systematic review. Health Technol Assess. 2011 Nov;15(38):1-110.
https://www.ncbi.nlm.nih.gov/books/NBK98342
http://www.ncbi.nlm.nih.gov/pubmed/22059955?tool=bestpractice.com
Metformin is not recommended for treating MASH in the absence of diabetes because it does not improve histological scores or fibrosis.[87]Said A, Akhter A. Meta-analysis of randomized controlled trials of pharmacologic agents in non-alcoholic steatohepatitis. Ann Hepatol. 2017 Jul-Aug;16(4):538-47.
http://www.ncbi.nlm.nih.gov/pubmed/28611274?tool=bestpractice.com
[111]Li Y, Liu L, Wang B, et al. Metformin in non-alcoholic fatty liver disease: a systematic review and meta-analysis. Biomed Rep. 2013 Jan;1(1):57-64.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3956897
http://www.ncbi.nlm.nih.gov/pubmed/24648894?tool=bestpractice.com
Ursodeoxycholic acid
Ursodeoxycholic acid is one of the secondary bile acids, which are metabolic byproducts of intestinal bacteria. Enthusiasm for its potential use in patients with MASH was curbed by a large multicentre trial in which patients with MASH were treated with the drug for 2 years. Although safe and well tolerated, it was found to be no better than placebo with regard to changes in steatosis, necro-inflammation, or fibrosis and it is not recommended for the treatment of MASLD or MASH.[3]Rinella ME, Neuschwander-Tetri BA, Siddiqui MS, et al. AASLD practice guidance on the clinical assessment and management of nonalcoholic fatty liver disease. Hepatology. 2023 May 1;77(5):1797-835.
https://journals.lww.com/hep/fulltext/2023/05000/aasld_practice_guidance_on_the_clinical_assessment.31.aspx
http://www.ncbi.nlm.nih.gov/pubmed/36727674?tool=bestpractice.com
[112]Lindor KD, Kowdley KV, Heathcote EJ, et al. Ursodeoxycholic acid for the treatment of nonalcoholic steatohepatitis: results of a randomized trial. Hepatology. 2004 Mar;39(3):770-8.
http://onlinelibrary.wiley.com/doi/10.1002/hep.20092/full
http://www.ncbi.nlm.nih.gov/pubmed/14999696?tool=bestpractice.com
[113]Leuschner UF, Lindenthal B, Herrmann G, et al. High-dose ursodeoxycholic acid therapy for nonalcoholic steatohepatitis: a double-blinded randomized, placebo-controlled trial. Hepatology. 2010 Aug;52(2):472-9.
https://aasldpubs.onlinelibrary.wiley.com/doi/full/10.1002/hep.23727
http://www.ncbi.nlm.nih.gov/pubmed/20683947?tool=bestpractice.com
Presence of end-stage liver failure
Transjugular intrahepatic portosystemic shunt (TIPS)
TIPS is an effective means of treating specific complications of end-stage liver disease and has been well studied in patients with refractory ascites and oesophageal variceal bleeding not amenable to endoscopic treatment; it is also commonly used to treat hepatic hydrothorax and gastric variceal bleeding.[114]Boyer TD, Haskal ZJ, American Association for the Study of Liver Diseases. The role of transjugular intrahepatic portosystemic shunt (TIPS) in the management of portal hypertension: update 2009. Hepatology. 2010 Jan;51(1):306.
https://www.doi.org/10.1002/hep.23383
http://www.ncbi.nlm.nih.gov/pubmed/19902484?tool=bestpractice.com
Liver transplantation
End-stage liver disease secondary to MASH is projected to become the primary indication for liver transplant. One single-centre study showed that 5-year outcomes were similar when compared with age-, sex-, and model for end-stage liver disease (MELD)-matched controls.[115]Angulo P. Nonalcoholic fatty liver disease and liver transplantation. Liver Transpl. 2006 Apr;12(4):523-34.
http://onlinelibrary.wiley.com/doi/10.1002/lt.20738/full
http://www.ncbi.nlm.nih.gov/pubmed/16555318?tool=bestpractice.com
[
MELDNa scores (for liver transplantation listing purposes, not appropriate for patients under age 12 years) (SI units)
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]
This study was confirmed by a larger analysis of the Scientific Registry of Transplant Recipients (SRTR) database.[116]Charlton MR, Burns JM, Pedersen RA, et al. Frequency and outcomes of liver transplantation for nonalcoholic steatohepatitis in the United States. Gastroenterology. 2011 Oct;141(4):1249-53.
http://www.ncbi.nlm.nih.gov/pubmed/21726509?tool=bestpractice.com
A subset of patients with MASH (aged >60 years, BMI >30 kg/m², and pre-liver transplant diabetes and hypertension) were deemed high risk and had a 1-year mortality of 50%.[115]Angulo P. Nonalcoholic fatty liver disease and liver transplantation. Liver Transpl. 2006 Apr;12(4):523-34.
http://onlinelibrary.wiley.com/doi/10.1002/lt.20738/full
http://www.ncbi.nlm.nih.gov/pubmed/16555318?tool=bestpractice.com
[117]Malik SM, deVera ME, Fontes P, et al. Outcome after liver transplantation for NASH cirrhosis. Am J Transplant. 2009 Apr;9(4):782-93.
https://onlinelibrary.wiley.com/doi/full/10.1111/j.1600-6143.2009.02590.x
http://www.ncbi.nlm.nih.gov/pubmed/19344467?tool=bestpractice.com
Patients transplanted for MASH may be at an increased risk for postoperative cardiovascular events.[118]Vanwagner LB, Bhave M, Te HS, et al. Patients transplanted for nonalcoholic steatohepatitis (NASH) are at increased risk for post-operative cardiovascular events. Hepatology. 2012 Nov;56(5):1741-50.
https://aasldpubs.onlinelibrary.wiley.com/doi/full/10.1002/hep.25855
http://www.ncbi.nlm.nih.gov/pubmed/22611040?tool=bestpractice.com
Typically, transplant candidates with MASH have concurrent obesity, metabolic, and cardiovascular risks, which directly impact patient evaluation and selection, waitlist morbidity and mortality, and eventually post-transplant outcomes.[119]Tsochatzis E, Coilly A, Nadalin S, et al. International liver transplantation consensus statement on end-stage liver disease due to nonalcoholic steatohepatitis and liver transplantation. Transplantation. 2019 Jan;103(1):45-56.
http://www.ncbi.nlm.nih.gov/pubmed/30153225?tool=bestpractice.com