About 15% of the white population has an RhD-negative blood type.[3]Mourant AE, Kopec AC, Domaniewska-Sobczak K. The distribution of the human blood groups and other biochemical polymorphisms. 2nd ed. London: Oxford University Press; 1976. Population data suggest that the incidence of RhD negativity is highest among Basques (36%).[3]Mourant AE, Kopec AC, Domaniewska-Sobczak K. The distribution of the human blood groups and other biochemical polymorphisms. 2nd ed. London: Oxford University Press; 1976. Around 6% to 7% of black people and less than 1% of American Indian and Asian people have an RhD-negative blood type.[3]Mourant AE, Kopec AC, Domaniewska-Sobczak K. The distribution of the human blood groups and other biochemical polymorphisms. 2nd ed. London: Oxford University Press; 1976.[4]Kanko TK, Woldemariam MK. Prevalence of Rhesus D negativity among reproductive age women in Southern Ethiopia: a cross-sectional study. BMC Womens Health. 2021 Apr 19;21(1):161.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8054355
http://www.ncbi.nlm.nih.gov/pubmed/33874938?tool=bestpractice.com
Rh alloimmunisation due to RhD has declined markedly as immunoprophylaxis has become routine practice.[5]Joseph KS, Kramer MS. The decline in Rh hemolytic disease: should Rh prophylaxis get all the credit? Am J Public Health. 1998 Feb;88(2):209-15.
https://ajph.aphapublications.org/doi/pdf/10.2105/AJPH.88.2.209
http://www.ncbi.nlm.nih.gov/pubmed/9491009?tool=bestpractice.com
[6]Van der Schoot CE, Soussan AA, Koelewijn J, et al. Non-invasive antenatal RHD typing. Transfus Clin Biol. 2006 Mar-Apr;13(1-2):53-7.
http://www.ncbi.nlm.nih.gov/pubmed/16564727?tool=bestpractice.com
Societal factors, such as delayed childbearing and smaller families, may also have contributed to this decline.[5]Joseph KS, Kramer MS. The decline in Rh hemolytic disease: should Rh prophylaxis get all the credit? Am J Public Health. 1998 Feb;88(2):209-15.
https://ajph.aphapublications.org/doi/pdf/10.2105/AJPH.88.2.209
http://www.ncbi.nlm.nih.gov/pubmed/9491009?tool=bestpractice.com
In the UK, about 16% of the white population is RhD-negative.[7]National Institute for Health and Care Excellence. Routine antenatal anti-D prophylaxis for women who are rhesus D negative. Aug 2008 [internet publication].
https://www.nice.org.uk/guidance/TA156
In 2013-2014, about 15% of births in England were to RhD-negative women; about 40% of these women had an RhD-negative fetus.[8]National Institute for Health and Care Excellence. High-throughput non-invasive prenatal testing for fetal RHD genotype. Nov 2016 [internet publication].
https://www.nice.org.uk/guidance/dg25
The estimated global prevalence of Rh haemolytic disease is 276/100,000 live births; in countries with well-established perinatal-neonatal care, the prevalence is approximately 2.5/100,000 live births.[9]Bhutani VK, Zipursky A, Blencowe H, et al. Neonatal hyperbilirubinemia and Rhesus disease of the newborn: incidence and impairment estimates for 2010 at regional and global levels. Pediatr Res. 2013 Dec;74(1 suppl):86-100.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3873706
http://www.ncbi.nlm.nih.gov/pubmed/24366465?tool=bestpractice.com
One survey in Canada estimated that 8/100,000 infants are affected by maternal anti-D antibodies.[10]Baker JM, Campbell DM, Pavenski K, et al. Infants affected by Rh sensitization: a 2-year Canadian National Surveillance Study. Paediatr Child Health. 2021 Jun;26(3):159-65.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8077204
http://www.ncbi.nlm.nih.gov/pubmed/33936335?tool=bestpractice.com
In the US, the reported incidence of Rh haemolytic disease ranges from 1.0 to 6.8/1000 live births; the higher rate may reflect improved identification and reporting of sensitised women and increasing prevalence of atypical, non-RhD antibodies for which immunoprophylaxis regimens are unavailable.[11]Chavez GF, Mulinare J, Edmonds LD. Epidemiology of Rh hemolytic disease of the newborn in the United States. JAMA. 1991 Jun 26;265(24):3270-4.
http://www.ncbi.nlm.nih.gov/pubmed/1904504?tool=bestpractice.com
[12]Martin JA, Hamilton BE, Sutton PD, et al. Births: final data for 2003. Natl Vital Stat Rep. 2005 Sep 8;54(2):1-116.
https://www.cdc.gov/nchs/data/nvsr/nvsr54/nvsr54_02.pdf
http://www.ncbi.nlm.nih.gov/pubmed/16176060?tool=bestpractice.com
[13]Ling L, Yu D, Gleeson CD, et al. 968 Estimation of hemolytic disease of the newborn in the United States from 1996-2010. Am J Obstet Gynecol. 2021 Feb;224(2 suppl):S600-1.
https://www.ajog.org/article/S0002-9378(20)32369-3/fulltext
The relative frequency has been reported for several of these non-RhD antibodies.[11]Chavez GF, Mulinare J, Edmonds LD. Epidemiology of Rh hemolytic disease of the newborn in the United States. JAMA. 1991 Jun 26;265(24):3270-4.
http://www.ncbi.nlm.nih.gov/pubmed/1904504?tool=bestpractice.com
In a large prospective series including over 300,000 consecutive patients, about 1% of pregnant women had alloantibodies detected in the first trimester.[14]Koelewijn JM, Vrijkotte TG, van der Schoot CE, et al. Effect of screening for red cell antibodies, other than anti-D, to detect hemolytic disease of the fetus and newborn: a population study in the Netherlands. Transfusion. 2008 May;48(5):941-52.
http://www.ncbi.nlm.nih.gov/pubmed/18248570?tool=bestpractice.com
Of these, the prevalence of alloantibodies other than anti-D was 328/100,000, of which 191/100,000 implied a risk for occurrence of haemolytic disease of the fetus and newborn as the father carried the antigen. The most common non-anti-D antibodies were anti-K and anti-c.[14]Koelewijn JM, Vrijkotte TG, van der Schoot CE, et al. Effect of screening for red cell antibodies, other than anti-D, to detect hemolytic disease of the fetus and newborn: a population study in the Netherlands. Transfusion. 2008 May;48(5):941-52.
http://www.ncbi.nlm.nih.gov/pubmed/18248570?tool=bestpractice.com