The major goals of therapy for patients with CPP arthritis are reduction in pain and improved function of the affected joints. There is little evidence that rapid therapy alters the natural history of the disease. Simple analgesics, such as acetaminophen, are used to control pain at any stage of the disease.[50]Zhang W, Doherty M, Pascual E, et al. EULAR recommendations for calcium pyrophosphate deposition. Part II: management. Ann Rheum Dis. 2011 Apr;70(4):571-5.
http://ard.bmj.com/content/70/4/571.long
http://www.ncbi.nlm.nih.gov/pubmed/21257614?tool=bestpractice.com
Cool packs, ice, and temporary joint rest may help to relieve symptoms. Comorbidities identified during symptom evaluation (e.g., hyperparathyroidism, hemochromatosis, hypomagnesemia, hypophosphatasia) should be treated.[50]Zhang W, Doherty M, Pascual E, et al. EULAR recommendations for calcium pyrophosphate deposition. Part II: management. Ann Rheum Dis. 2011 Apr;70(4):571-5.
http://ard.bmj.com/content/70/4/571.long
http://www.ncbi.nlm.nih.gov/pubmed/21257614?tool=bestpractice.com
See Hyperparathyroidism (Management) and Hemochromatosis (Management).
Monoarticular or oligoarticular disease
Intra-articular corticosteroids are the preferred treatment during an acute attack. They have been shown to reduce pain and limit the duration of inflammation.[51]O'Duffy JD. Clinical studies of acute pseudogout attacks: comments on prevalence, predispositions, and treatment. Arthritis Rheum. 1976 May-Jun;19(suppl 3):349-52.
http://www.ncbi.nlm.nih.gov/pubmed/181014?tool=bestpractice.com
[52]Creamer P. Intra-articular corticosteroid treatment in osteoarthritis. Curr Opin Rheumatol. 1999 Sep;11(5):417-21.
http://www.ncbi.nlm.nih.gov/pubmed/10503664?tool=bestpractice.com
They are generally well tolerated, although bleeding into the skin or joint and infection can rarely occur.[52]Creamer P. Intra-articular corticosteroid treatment in osteoarthritis. Curr Opin Rheumatol. 1999 Sep;11(5):417-21.
http://www.ncbi.nlm.nih.gov/pubmed/10503664?tool=bestpractice.com
Although their mechanism of action is not fully elucidated, their potent anti-inflammatory action is likely involved.
The treatment should be given at the time of diagnosis and can be repeated every 3 months. Before injection, synovial fluid should be removed from the affected joint to minimize dilution of the drug. Lidocaine is typically used as a local anesthetic.
For patients where intra-articular corticosteroid injections are not practical or declined, systemic therapies can be considered. Nonsteroidal anti-inflammatory drugs (NSAIDs) can be useful in reducing pain and inflammation but should be prescribed cautiously in the older population.[50]Zhang W, Doherty M, Pascual E, et al. EULAR recommendations for calcium pyrophosphate deposition. Part II: management. Ann Rheum Dis. 2011 Apr;70(4):571-5.
http://ard.bmj.com/content/70/4/571.long
http://www.ncbi.nlm.nih.gov/pubmed/21257614?tool=bestpractice.com
They should be used with preventive measures, such as proton-pump inhibitors, in patients at high risk of gastrointestinal complications.[53]Freedberg DE, Kim LS, Yang YX. The Risks and benefits of ong-term use of proton pump inhibitors: expert review and best practice advice From the American Gastroenterological Association. Gastroenterology. 2017 Mar;152(4):706-15.
https://www.gastrojournal.org/article/S0016-5085(17)30091-4/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/28257716?tool=bestpractice.com
COX-2 inhibitors (e.g., celecoxib) may be less likely to cause gastrointestinal bleeding than traditional NSAIDs in patients with a history of gastrointestinal bleeding or comorbidities.[54]García Rodríguez LA, Barreales Tolosa L. Risk of upper gastrointestinal complications among users of traditional NSAIDs and COXIBs in the general population. Gastroenterology. 2007 Feb;132(2):498-506.
https://www.gastrojournal.org/article/S0016-5085(06)02565-0/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/17258728?tool=bestpractice.com
All NSAIDs have been associated with increased risks of cardiovascular events.[55]Trelle S, Reichenbach S, Wandel S, et al. Cardiovascular safety of non-steroidal anti-inflammatory drugs: network meta-analysis. BMJ. 2011 Jan 11;342:c7086.
https://www.bmj.com/content/342/bmj.c7086
http://www.ncbi.nlm.nih.gov/pubmed/21224324?tool=bestpractice.com
Patients with osteoarthritis-like disease or rheumatoid-like disease (i.e., where there is an inflammatory component to the arthritis) who cannot take NSAIDs may benefit from low-dose colchicine therapy, if kidney and liver function are normal.[56]Meed SD, Spilberg I. Successful use of colchicine in acute polyarticular pseudogout. J Rheumatol. 1981 Jul-Aug;8(4):689-91.
http://www.ncbi.nlm.nih.gov/pubmed/7299772?tool=bestpractice.com
Evidence for colchicine use in CPPD is mostly extrapolated from evidence for the treatment of acute gout.[50]Zhang W, Doherty M, Pascual E, et al. EULAR recommendations for calcium pyrophosphate deposition. Part II: management. Ann Rheum Dis. 2011 Apr;70(4):571-5.
http://ard.bmj.com/content/70/4/571.long
http://www.ncbi.nlm.nih.gov/pubmed/21257614?tool=bestpractice.com
Colchicine has a narrow therapeutic window. To avoid adverse effects, particularly diarrhea, the minimum effective dose should be used because of the narrow benefit-to-risk index.[57]Neuss MN, McCallum RM, Brenckman WD, et al. Long-term colchicine administration leading to colchicine toxicity and death. Arthritis Rheum. 1986 Mar;29(3):448-9.
http://www.ncbi.nlm.nih.gov/pubmed/3964322?tool=bestpractice.com
Polyarticular disease
For patients with polyarticular disease, systemic therapies are first-line therapy, followed by intra-articular corticosteroids.
Treatment failure/contraindications
Systemic corticosteroids at moderate to low doses can be used when other therapies are not effective or are contraindicated.[58]Roane DW, Harris MD, Carpenter MT, et al. Prospective use of intramuscular triamcinolone acetonide in pseudogout. J Rheumatol. 1997 Jun;24(6):1168-70.
http://www.ncbi.nlm.nih.gov/pubmed/9195527?tool=bestpractice.com
Alternatively, a combination of pain medications, joint aspiration, splinting, and observation may be the safest option for some patients. One randomized controlled trial conducted between 2018 and 2022 found that, when compared with colchicine, prednisone showed equivalent short-term efficacy for the treatment of acute CPP crystal arthritis in hospitalized patients.[59]Tristan P, Pierre R, Sébastien O, et al. Evaluating the safety and short-term equivalence of colchicine versus prednisone in older patients with acute calcium pyrophosphate crystal arthritis (COLCHICORT): an open-label, multicentre, randomised trial. The Lancet Rheumatology. 2023 Sep;5(9):e523-31.
https://www.sciencedirect.com/science/article/abs/pii/S2665991323001650
Surgery
Patients with chronic or recurrent involvement of the knee, hip, or shoulder associated with severe joint degeneration may be good candidates for joint replacement surgery.[11]Rosenthal AK, Ryan LM. Calcium Pyrophosphate Deposition Disease. N Engl J Med. 2016 Jun 30;374(26):2575-84.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6240444
http://www.ncbi.nlm.nih.gov/pubmed/27355536?tool=bestpractice.com
Maintenance therapy
Patients with an inflammatory component to their disease who display a positive response to colchicine in terms of reduced severity or frequency of attacks may benefit from a low dose of colchicine to prevent further attacks.