In all patients with Pneumocystis pneumonia (PCP), overall survival has improved. In a large US death certificate database, the mortality rate declined from 0.470 deaths per 100,000 persons in 1999 to 0.154 per 100,000 persons in 2014.[113]Wickramasekaran RN, Jewell MP, Sorvillo F, et al. The changing trends and profile of pneumocystosis mortality in the United States, 1999-2014. Mycoses. 2017 Sep;60(9):607-15.
http://www.ncbi.nlm.nih.gov/pubmed/28568970?tool=bestpractice.com
More directly, in the Adult and Adolescent Spectrum HIV disease project, the 12-month survival increased from 40% in 1992/1993 to 63% in 1996/1998.[114]Dworkin MS, Hanson DL, Navin TR. Survival of patients with AIDS, after diagnosis of Pneumocystis carinii pneumonia, in the United States. J Infect Dis. 2001 May 1;183(9):1409-12.
http://jid.oxfordjournals.org/content/183/9/1409.full
http://www.ncbi.nlm.nih.gov/pubmed/11294675?tool=bestpractice.com
Factors associated with poor survival were a history of previous PCP, low CD4 cell count (<50 cells/microliter), CD4 cell percentage <15% and age >60 years. In HIV-positive patients admitted with PCP to three major academic centers between 1995 and 1997, the overall inpatient mortality was 11.3%.[115]Arozullah AM, Yarnols PR, Weinstein RA, et al. A new preadmission staging system for predicting inpatient mortality from HIV-associated Pneumocystis carinii pneumonia in the early highly active antiretroviral therapy (HAART) era. Am J Respir Crit Care Med. 2000 Apr;161(4 Pt 1):1081-6.
http://www.ncbi.nlm.nih.gov/pubmed/10764294?tool=bestpractice.com
Factors that were associated with an increased mortality were:
Elevated A-a gradient
Hypoalbuminemia
Illicit drug use
Increased respiratory rate
Prior Mycobacterium avium intracellulare infection prophylaxis
Prior AIDS diagnosis
Elevated WBC count
Elevated serum creatinine
Neurologic symptoms.
One 2008 study showed mortality from PCP between 1996 and 2006 was 9.7% and early predictors of mortality were:[116]Walzer PD, Evans HE, Copas AJ, et al. Early predictors of mortality from Pneumocystis jiroveci pneumonia in HIV-infected patients: 1985 to 2006. Clin Infect Dis. 2008 Feb 15;46(4):625-33.
http://www.ncbi.nlm.nih.gov/pubmed/18190281?tool=bestpractice.com
Increasing patient age
Subsequent episodes of PCP
Low hemoglobin level at hospital admission
Low partial pressure of oxygen breathing room air at hospital admission
Presence of medical comorbidity
Pulmonary Kaposi sarcoma.
Another study of 136 episodes of PCP between 2000 and 2013 found that mortality was 11%, and 5-year survival was 73% overall (88% in those compliant with combination antiretroviral therapy [ART], and 34% in those not adherent to ART).[16]López-Sánchez C, Falcó V, Burgos J, et al. Epidemiology and long-term survival in HIV-infected patients with Pneumocystis jirovecii pneumonia in the HAART era:experience in a university hospital and review of the literature. Medicine (Baltimore). 2015 Mar;94(12):e681.
http://journals.lww.com/md-journal/Fulltext/2015/03040/Epidemiology_and_Long_Term_Survival_in.14.aspx
http://www.ncbi.nlm.nih.gov/pubmed/25816039?tool=bestpractice.com
At San Francisco General Hospital, there has been a series of studies of outcomes and epidemiology of PCP in the intensive care unit (ICU) that span the entire HIV/AIDS epidemic at that institution.[117]Morris A, Creasman J, Turner J, et al. Intensive care of human immunodeficiency virus-infected patients during the era of highly active antiretroviral therapy. Am J Respir Crit Care Med. 2002 Aug 1;166(3):262-7.
http://www.ncbi.nlm.nih.gov/pubmed/12153955?tool=bestpractice.com
[118]Nickas G, Wachter RM. Outcomes of intensive care for patients with human immunodeficiency virus infection. Arch Intern Med. 2000 Feb 28;160(4):541-7.
http://www.ncbi.nlm.nih.gov/pubmed/10695695?tool=bestpractice.com
[119]Powell K, Davis JL, Morris AM, et al. Survival for patients with human immunodeficiency virus admitted to the intensive care unit continues to improve in the current era of highly active antiretroviral therapy. Chest. 2009 Jan;135(1):11-7.
http://www.ncbi.nlm.nih.gov/pubmed/18719058?tool=bestpractice.com
[120]Wachter RM, Luce JM, Safrin S, et al. Cost and outcome of intensive care for patients with AIDS, Pneumocystis carinii pneumonia, and severe respiratory failure. JAMA. 1995 Jan 18;273(3):230-5.
http://www.ncbi.nlm.nih.gov/pubmed/7807663?tool=bestpractice.com
[121]Wachter RM, Luce JM, Turner J, et al. Intensive care of patients with the acquired immunodeficiency syndrome. Outcome and changing patterns of utilization. Am Rev Respir Dis. 1986 Nov;134(5):891-6.
http://www.ncbi.nlm.nih.gov/pubmed/3777686?tool=bestpractice.com
[122]Wachter RM, Russi MB, Bloch DA, et al. Pneumocystis carinii pneumonia and respiratory failure in AIDS. Improved outcomes and increased use of intensive care units. Am Rev Respir Dis. 1991 Feb;143(2):251-6.
http://www.ncbi.nlm.nih.gov/pubmed/1990936?tool=bestpractice.com
Further studies in this series show survival in critically ill HIV-positive patients continued to improve in the era of ART and the incidence of PCP diagnosis for admission to the ICU continued to decrease.[117]Morris A, Creasman J, Turner J, et al. Intensive care of human immunodeficiency virus-infected patients during the era of highly active antiretroviral therapy. Am J Respir Crit Care Med. 2002 Aug 1;166(3):262-7.
http://www.ncbi.nlm.nih.gov/pubmed/12153955?tool=bestpractice.com
[119]Powell K, Davis JL, Morris AM, et al. Survival for patients with human immunodeficiency virus admitted to the intensive care unit continues to improve in the current era of highly active antiretroviral therapy. Chest. 2009 Jan;135(1):11-7.
http://www.ncbi.nlm.nih.gov/pubmed/18719058?tool=bestpractice.com
[123]Morris A, Wachter RM, Luce J, et al. Improved survival with highly active antiretroviral therapy in HIV-infected patients with severe Pneumocystis carinii pneumonia. AIDS. 2003 Jan 3;17(1):73-80.
http://www.ncbi.nlm.nih.gov/pubmed/12478071?tool=bestpractice.com
In critically ill HIV-positive patients admitted to the ICU, PCP was the most common cause of respiratory failure and was associated with decreased survival, although the incidence of PCP in patients on ART was much lower than in those not taking ART (3% versus 19%, P < 0.001).[119]Powell K, Davis JL, Morris AM, et al. Survival for patients with human immunodeficiency virus admitted to the intensive care unit continues to improve in the current era of highly active antiretroviral therapy. Chest. 2009 Jan;135(1):11-7.
http://www.ncbi.nlm.nih.gov/pubmed/18719058?tool=bestpractice.com
In patients admitted to the ICU with PCP, the use of ART was an independent predictor of improved survival and the need for mechanical ventilation and/or development of a pneumothorax. Delayed ICU admission was associated with increased mortality.[123]Morris A, Wachter RM, Luce J, et al. Improved survival with highly active antiretroviral therapy in HIV-infected patients with severe Pneumocystis carinii pneumonia. AIDS. 2003 Jan 3;17(1):73-80.
http://www.ncbi.nlm.nih.gov/pubmed/12478071?tool=bestpractice.com
In HIV-negative patients with PCP, morbidity and mortality is higher than in those who are HIV-positive.[25]Yale SH, Limper AH. Pneumocystis carinii pneumonia in patients without acquired immunodeficiency syndrome: associated illness and prior corticosteroid therapy. Mayo Clin Proc. 1996 Jan;71(1):5-13.
http://www.ncbi.nlm.nih.gov/pubmed/8538233?tool=bestpractice.com
[27]Bienvenu AL, Traore K, Plekhanova I, et al. Pneumocystis pneumonia suspected cases in 604 non-HIV and HIV patients. Int J Infect Dis. 2016 May;46:11-7.
http://www.ncbi.nlm.nih.gov/pubmed/27021532?tool=bestpractice.com
[28]Ling C, Qian S, Wang Q, et al. Pneumocystis pneumonia in non-HIV children: a 10-year retrospective study. Clin Respir J. 2018 Jan;12(1):16-22.
http://www.ncbi.nlm.nih.gov/pubmed/26878193?tool=bestpractice.com
[124]Mansharamani NG, Garland R, Delaney G, et al. Management and outcome patterns for adult Pneumocystis carinii pneumonia, 1985 to 1995: comparison of HIV-associated cases to other immunocompromised states. Chest. 2000 Sep;118(3):704-11.
http://www.ncbi.nlm.nih.gov/pubmed/10988192?tool=bestpractice.com
[125]Arend SM, Kroon FP, van't Wout JW. Pneumocystis carinii pneumonia in patients without AIDS, 1980 through 1993. An analysis of 78 cases. Arch Intern Med. 1995 Dec 11-25;155(22):2436-41.
http://www.ncbi.nlm.nih.gov/pubmed/7503602?tool=bestpractice.com
In one case series of HIV-negative patients who developed PCP, 97% required hospital admission, 69% were admitted to the ICU, 66% required mechanical ventilation, and mortality was 39%.[124]Mansharamani NG, Garland R, Delaney G, et al. Management and outcome patterns for adult Pneumocystis carinii pneumonia, 1985 to 1995: comparison of HIV-associated cases to other immunocompromised states. Chest. 2000 Sep;118(3):704-11.
http://www.ncbi.nlm.nih.gov/pubmed/10988192?tool=bestpractice.com
In another series, mortality was 69% and factors associated with mortality (i.e., Acute Physiology and Chronic Health Evaluation II score, acute lung injury/acute respiratory distress syndrome, late diagnosis, nosocomial infections) were high.[126]Cao B, Wang H, Wang P, et al. Clinical parameters and outcomes of Pneumocystis jiroveci pneumonia in non-HIV/AIDS patients. Chin Med J (Engl). 2006 Feb 5;119(3):234-7.
http://www.ncbi.nlm.nih.gov/pubmed/16537012?tool=bestpractice.com