Lactose malabsorption is present in about 70% of the world's population, although not all demonstrate the symptoms of lactose intolerance.[4]Storhaug CL, Fosse SK, Fadnes LT. Country, regional, and global estimates for lactose malabsorption in adults: a systematic review and meta-analysis. Lancet Gastroenterol Hepatol. 2017 Oct;2(10):738-46.
https://www.sciencedirect.com/science/article/pii/S2468125317301541?via%3Dihub
http://www.ncbi.nlm.nih.gov/pubmed/28690131?tool=bestpractice.com
The prevalence of lactose intolerance is unknown as it is more difficult to measure.[5]Suchy FJ, Brannon PM, Carpenter TO, et al. National Institutes of Health Consensus Development Conference: lactose intolerance and health. Ann Intern Med. 2010 Jun 15;152(12):792-6.
http://annals.org/aim/fullarticle/745834/national-institutes-health-consensus-development-conference-lactose-intolerance-health
http://www.ncbi.nlm.nih.gov/pubmed/20404261?tool=bestpractice.com
[6]Misselwitz B, Butter M, Verbeke K, et al. Update on lactose malabsorption and intolerance: pathogenesis, diagnosis and clinical management. Gut. 2019 Nov;68(11):2080-91.
https://gut.bmj.com/content/68/11/2080
http://www.ncbi.nlm.nih.gov/pubmed/31427404?tool=bestpractice.com
[7]Harvey L, Ludwig T, Hou AQ, et al. Prevalence, cause and diagnosis of lactose intolerance in children aged 1-5 years: a systematic review of 1995-2015 literature. Asia Pac J Clin Nutr. 2018;27(1):29-46.
https://apjcn.nhri.org.tw/server/APJCN/27/1/29.pdf
http://www.ncbi.nlm.nih.gov/pubmed/29222879?tool=bestpractice.com
The primary form of lactase deficiency is the most common, while congenital lactase deficiency is extremely rare (<50 cases reported worldwide).[1]Matthews SB, Waud JP, Roberts AG, et al. Systemic lactose intolerance: a new perspective on an old problem. Postgrad Med J. 2005 Mar;81(953):167-73.
https://pmj.bmj.com/content/81/953/167.long
http://www.ncbi.nlm.nih.gov/pubmed/15749792?tool=bestpractice.com
[3]Lomer ME, Parkes GC, Sanderson JD. Lactose intolerance in clinical practice - myths and realities. Aliment Pharmacol Ther. 2008 Jan 15;27(2):93-103.
http://www.ncbi.nlm.nih.gov/pubmed/17956597?tool=bestpractice.com
[4]Storhaug CL, Fosse SK, Fadnes LT. Country, regional, and global estimates for lactose malabsorption in adults: a systematic review and meta-analysis. Lancet Gastroenterol Hepatol. 2017 Oct;2(10):738-46.
https://www.sciencedirect.com/science/article/pii/S2468125317301541?via%3Dihub
http://www.ncbi.nlm.nih.gov/pubmed/28690131?tool=bestpractice.com
In the US, primary lactase deficiency is far more common in African-American, American Indian, Hispanic, Latino, and Asian-American people than in white Americans.[2]Heyman MB; American Academy of Pediatrics, Committee on Nutrition. Lactose intolerance in infants, children, and adolescents. Pediatrics. 2006 Sep;118(3):1279-86.
http://pediatrics.aappublications.org/content/118/3/1279.long
http://www.ncbi.nlm.nih.gov/pubmed/16951027?tool=bestpractice.com
[8]Scrimshaw NS, Murray EB. The acceptability of milk and milk products in populations with a high prevalence of lactose intolerance. Am J Clin Nutr. 1988 Oct;48(4 Suppl):1079-159.
http://www.ncbi.nlm.nih.gov/pubmed/3140651?tool=bestpractice.com
[9]Paige DM, Bayless TM, Mellitis ED, et al. Lactose intolerance in preschool black children. Am J Clin Nutr. 1977 Jul;30(7):1018-22.
http://www.ncbi.nlm.nih.gov/pubmed/577654?tool=bestpractice.com
[10]Sahi T. Genetics and epidemiology of adult-type hypolactasia. Scand J Gastroenterol Suppl. 1994;202:7-20.
http://www.ncbi.nlm.nih.gov/pubmed/8042019?tool=bestpractice.com
North Americans, white Northern Europeans, and Australians have the lowest rates, ranging from 2% to 15%.[2]Heyman MB; American Academy of Pediatrics, Committee on Nutrition. Lactose intolerance in infants, children, and adolescents. Pediatrics. 2006 Sep;118(3):1279-86.
http://pediatrics.aappublications.org/content/118/3/1279.long
http://www.ncbi.nlm.nih.gov/pubmed/16951027?tool=bestpractice.com
[8]Scrimshaw NS, Murray EB. The acceptability of milk and milk products in populations with a high prevalence of lactose intolerance. Am J Clin Nutr. 1988 Oct;48(4 Suppl):1079-159.
http://www.ncbi.nlm.nih.gov/pubmed/3140651?tool=bestpractice.com
By contrast, the prevalence of lactase deficiency is 50% to 80% in South American people; around 60% to 80% in African and Jewish people; and almost 100% in American Indian and some East Asian populations.[2]Heyman MB; American Academy of Pediatrics, Committee on Nutrition. Lactose intolerance in infants, children, and adolescents. Pediatrics. 2006 Sep;118(3):1279-86.
http://pediatrics.aappublications.org/content/118/3/1279.long
http://www.ncbi.nlm.nih.gov/pubmed/16951027?tool=bestpractice.com
[9]Paige DM, Bayless TM, Mellitis ED, et al. Lactose intolerance in preschool black children. Am J Clin Nutr. 1977 Jul;30(7):1018-22.
http://www.ncbi.nlm.nih.gov/pubmed/577654?tool=bestpractice.com
[10]Sahi T. Genetics and epidemiology of adult-type hypolactasia. Scand J Gastroenterol Suppl. 1994;202:7-20.
http://www.ncbi.nlm.nih.gov/pubmed/8042019?tool=bestpractice.com
[11]Gilat T, Kuhn R, Gelman E, et al. Lactase deficiency in Jewish communities in Israel. Am J Dig Dis. 1970 Oct;15(10):895-904.
The age-related decline in lactase expression is usually complete during childhood, but the decline has also been reported to occur later, in adolescence, especially in white people.[10]Sahi T. Genetics and epidemiology of adult-type hypolactasia. Scand J Gastroenterol Suppl. 1994;202:7-20.
http://www.ncbi.nlm.nih.gov/pubmed/8042019?tool=bestpractice.com
[12]Sahi T, Launiala K, Laitinen H. Hypolactasia in a fixed cohort of young Finnish adults. A follow-up study. Scand J Gastroenterol. 1983 Oct;18(7):865-70.
http://www.ncbi.nlm.nih.gov/pubmed/6689563?tool=bestpractice.com
The eventual level and the time course of loss of lactase activity vary considerably according to ethnicity.[1]Matthews SB, Waud JP, Roberts AG, et al. Systemic lactose intolerance: a new perspective on an old problem. Postgrad Med J. 2005 Mar;81(953):167-73.
https://pmj.bmj.com/content/81/953/167.long
http://www.ncbi.nlm.nih.gov/pubmed/15749792?tool=bestpractice.com
[10]Sahi T. Genetics and epidemiology of adult-type hypolactasia. Scand J Gastroenterol Suppl. 1994;202:7-20.
http://www.ncbi.nlm.nih.gov/pubmed/8042019?tool=bestpractice.com
Chinese and Japanese people lose 80% to 90% of activity within 3-4 years after weaning; Jewish people and Asians lose 60% to 70% over several years after weaning; and in white Northern Europeans and North Americans it may take up to 18-20 years for lactase activity to reach its lowest levels.[1]Matthews SB, Waud JP, Roberts AG, et al. Systemic lactose intolerance: a new perspective on an old problem. Postgrad Med J. 2005 Mar;81(953):167-73.
https://pmj.bmj.com/content/81/953/167.long
http://www.ncbi.nlm.nih.gov/pubmed/15749792?tool=bestpractice.com
[3]Lomer ME, Parkes GC, Sanderson JD. Lactose intolerance in clinical practice - myths and realities. Aliment Pharmacol Ther. 2008 Jan 15;27(2):93-103.
http://www.ncbi.nlm.nih.gov/pubmed/17956597?tool=bestpractice.com
A lower prevalence of lactase non-persistence is observed in patients from mixed ethnicity, where a high prevalence is detected in the native ethnic group.[13]Johnson JD. The regional and ethnic distribution of lactose malabsorption. Genetic and adaptive hypothesis. Clinical and nutritional implications. Baltimore, MD: Johns Hopkins University Press; 1981:11-22.
Onset is typically subtle and progressive in primary lactase deficiency, and most people first experience intolerance symptoms in late adolescence and adulthood.[2]Heyman MB; American Academy of Pediatrics, Committee on Nutrition. Lactose intolerance in infants, children, and adolescents. Pediatrics. 2006 Sep;118(3):1279-86.
http://pediatrics.aappublications.org/content/118/3/1279.long
http://www.ncbi.nlm.nih.gov/pubmed/16951027?tool=bestpractice.com
[3]Lomer ME, Parkes GC, Sanderson JD. Lactose intolerance in clinical practice - myths and realities. Aliment Pharmacol Ther. 2008 Jan 15;27(2):93-103.
http://www.ncbi.nlm.nih.gov/pubmed/17956597?tool=bestpractice.com
Compared with white Northern Europeans, North Americans, and Australians, presentation is earlier in Native Americans, African-Americans, Asian-Americans, and Hispanics/Latinos.[2]Heyman MB; American Academy of Pediatrics, Committee on Nutrition. Lactose intolerance in infants, children, and adolescents. Pediatrics. 2006 Sep;118(3):1279-86.
http://pediatrics.aappublications.org/content/118/3/1279.long
http://www.ncbi.nlm.nih.gov/pubmed/16951027?tool=bestpractice.com
[3]Lomer ME, Parkes GC, Sanderson JD. Lactose intolerance in clinical practice - myths and realities. Aliment Pharmacol Ther. 2008 Jan 15;27(2):93-103.
http://www.ncbi.nlm.nih.gov/pubmed/17956597?tool=bestpractice.com
[9]Paige DM, Bayless TM, Mellitis ED, et al. Lactose intolerance in preschool black children. Am J Clin Nutr. 1977 Jul;30(7):1018-22.
http://www.ncbi.nlm.nih.gov/pubmed/577654?tool=bestpractice.com
[10]Sahi T. Genetics and epidemiology of adult-type hypolactasia. Scand J Gastroenterol Suppl. 1994;202:7-20.
http://www.ncbi.nlm.nih.gov/pubmed/8042019?tool=bestpractice.com
Secondary disease is more common in children, especially in developing countries where infections are the common cause.[14]Srinivasan R, Minocha A. When to suspect lactose intolerance. Symptomatic, ethnic, and laboratory clues. Postgrad Med. 1998 Sep;104(3):109-11,115-6,122-3.
http://www.ncbi.nlm.nih.gov/pubmed/9742907?tool=bestpractice.com
The sexes are affected equally.