Sepsis
It is important to consider sepsis in any febrile unwell child with acute limp, not weight-bearing, or unable to move the joint (septic arthritis or osteomyelitis).[13]National Institute for Health and Care Excellence. Suspected sepsis: recognition, diagnosis and early management. Mar 2024 [internet publication].
https://www.nice.org.uk/guidance/ng51
Sepsis is a spectrum of disease, where there is a systemic and dysregulated host response to an infection.[14]Singer M, Deutschman CS, Seymour CW, et al. The third International Consensus Definitions for sepsis and septic shock (Sepsis-3). JAMA. 2016 Feb 23;315(8):801-10.
https://jamanetwork.com/journals/jama/fullarticle/2492881
http://www.ncbi.nlm.nih.gov/pubmed/26903338?tool=bestpractice.com
Presentation ranges from subtle, non-specific symptoms (e.g., feeling unwell with a normal temperature) to severe symptoms with evidence of multi-organ dysfunction and septic shock. Patients may have signs of tachycardia, tachypnoea, hypotension, fever or hypothermia, poor capillary refill, mottled or ashen skin, cyanosis, newly altered mental state or reduced urine output.[13]National Institute for Health and Care Excellence. Suspected sepsis: recognition, diagnosis and early management. Mar 2024 [internet publication].
https://www.nice.org.uk/guidance/ng51
Sepsis and septic shock are medical emergencies.
Risk factors for sepsis include: aged under 1 year, impaired immunity (due to illness or drugs), recent surgery or other invasive procedures, any breach of skin integrity (e.g., cuts, burns), and indwelling lines or catheters.[13]National Institute for Health and Care Excellence. Suspected sepsis: recognition, diagnosis and early management. Mar 2024 [internet publication].
https://www.nice.org.uk/guidance/ng51
Early recognition of sepsis is essential because early treatment improves outcomes.[13]National Institute for Health and Care Excellence. Suspected sepsis: recognition, diagnosis and early management. Mar 2024 [internet publication].
https://www.nice.org.uk/guidance/ng51
[15]Weiss SL, Peters MJ, Alhazzani W, et al. Surviving sepsis campaign international guidelines for the management of septic shock and sepsis-associated organ dysfunction in children. Intensive Care Med. 2020 Feb;46(suppl 1):10-67.
https://link.springer.com/article/10.1007/s00134-019-05878-6
http://www.ncbi.nlm.nih.gov/pubmed/32030529?tool=bestpractice.com
[Evidence C]a4f222a1-8306-4529-b663-eecf71072027guidelineCWhat are the effects of early versus late initiation of empiric antimicrobial treatment in children with or at risk of developing sepsis or severe sepsis?[13]National Institute for Health and Care Excellence. Suspected sepsis: recognition, diagnosis and early management. Mar 2024 [internet publication].
https://www.nice.org.uk/guidance/ng51
However, detection can be challenging because the clinical presentation of sepsis can be subtle and non-specific. The key to early recognition is the systematic identification of any patient who has signs or symptoms suggestive of infection and is at risk of deterioration due to organ dysfunction. Criteria to identify sepsis and septic shock in children and people under the age of 18 years have been developed.[16]Schlapbach LJ, Watson RS, Sorce LR, et al. International consensus criteria for pediatric sepsis and septic shock. JAMA. 2024 Feb 27;331(8):665-74.
https://jamanetwork.com/journals/jama/fullarticle/2814297
http://www.ncbi.nlm.nih.gov/pubmed/38245889?tool=bestpractice.com
Several other risk stratification approaches exist. All rely on a structured clinical assessment and recording of the patient’s vital signs.[13]National Institute for Health and Care Excellence. Suspected sepsis: recognition, diagnosis and early management. Mar 2024 [internet publication].
https://www.nice.org.uk/guidance/ng51
[16]Schlapbach LJ, Watson RS, Sorce LR, et al. International consensus criteria for pediatric sepsis and septic shock. JAMA. 2024 Feb 27;331(8):665-74.
https://jamanetwork.com/journals/jama/fullarticle/2814297
http://www.ncbi.nlm.nih.gov/pubmed/38245889?tool=bestpractice.com
[17]Royal College of Physicians. National Early Warning Score (NEWS) 2. Dec 2017 [internet publication].
https://www.rcplondon.ac.uk/projects/outputs/national-early-warning-score-news-2
[18]American College of Emergency Physicians (ACEP) Expert Panel on Sepsis. DART: an evidence-driven tool to guide the early recognition and treatment of sepsis and septic shock [internet publication].
https://poctools.acep.org/POCTool/Sepsis(DART)/276ed0a9-f24d-45f1-8d0c-e908a2758e5a
[19]Academy of Medical Royal Colleges. Reports and guidance: statement on the initial antimicrobial treatment of sepsis. Oct 2022 [internet publication].
https://www.aomrc.org.uk/reports-guidance
It is important to check local guidance for information on which approach your institution recommends. The timeline of ensuing investigations and treatment should be guided by this early assessment.[19]Academy of Medical Royal Colleges. Reports and guidance: statement on the initial antimicrobial treatment of sepsis. Oct 2022 [internet publication].
https://www.aomrc.org.uk/reports-guidance
Treatment guidelines have been produced by the Surviving Sepsis Campaign and remain the most widely accepted standards.[15]Weiss SL, Peters MJ, Alhazzani W, et al. Surviving sepsis campaign international guidelines for the management of septic shock and sepsis-associated organ dysfunction in children. Intensive Care Med. 2020 Feb;46(suppl 1):10-67.
https://link.springer.com/article/10.1007/s00134-019-05878-6
http://www.ncbi.nlm.nih.gov/pubmed/32030529?tool=bestpractice.com
Within the first hour:[15]Weiss SL, Peters MJ, Alhazzani W, et al. Surviving sepsis campaign international guidelines for the management of septic shock and sepsis-associated organ dysfunction in children. Intensive Care Med. 2020 Feb;46(suppl 1):10-67.
https://link.springer.com/article/10.1007/s00134-019-05878-6
http://www.ncbi.nlm.nih.gov/pubmed/32030529?tool=bestpractice.com
Follow institutional protocols for management of sepsis/septic shock in children; these improve the speed and reliability of care
Obtain blood cultures before administering antibiotics (provided this does not substantially delay antibiotic administration)
Administer broad-spectrum antibiotics
Administer crystalloid fluids, titrated to clinical signs of cardiac output and stopped if there is evidence of volume overload. Consult local protocols.
Use trends in blood lactate levels to guide resuscitation. If the child’s hypotension is refractory to fluid resuscitation, consider use of vasopressors.[15]Weiss SL, Peters MJ, Alhazzani W, et al. Surviving sepsis campaign international guidelines for the management of septic shock and sepsis-associated organ dysfunction in children. Intensive Care Med. 2020 Feb;46(suppl 1):10-67.
https://link.springer.com/article/10.1007/s00134-019-05878-6
http://www.ncbi.nlm.nih.gov/pubmed/32030529?tool=bestpractice.com
Several studies have demonstrated the importance of protocolised care and care bundles in paediatric sepsis.[15]Weiss SL, Peters MJ, Alhazzani W, et al. Surviving sepsis campaign international guidelines for the management of septic shock and sepsis-associated organ dysfunction in children. Intensive Care Med. 2020 Feb;46(suppl 1):10-67.
https://link.springer.com/article/10.1007/s00134-019-05878-6
http://www.ncbi.nlm.nih.gov/pubmed/32030529?tool=bestpractice.com
[20]Paul R, Neuman MI, Monuteaux MC, et al. Adherence to PALS sepsis guidelines and hospital length of stay. Pediatrics. 2012 Aug;130(2):e273-80.
https://publications.aap.org/pediatrics/article-abstract/130/2/e273/29960/Adherence-to-PALS-Sepsis-Guidelines-and-Hospital
http://www.ncbi.nlm.nih.gov/pubmed/22753559?tool=bestpractice.com
[21]Paul R, Melendez E, Stack A, et al. Improving adherence to PALS septic shock guidelines. Pediatrics. 2014 May;133(5):e1358-66.
https://publications.aap.org/pediatrics/article-abstract/133/5/e1358/32752/Improving-Adherence-to-PALS-Septic-Shock
http://www.ncbi.nlm.nih.gov/pubmed/24709937?tool=bestpractice.com
[22]Larsen GY, Mecham N, Greenberg R. An emergency department septic shock protocol and care guideline for children initiated at triage. Pediatrics. 2011 Jun;127(6):e1585-92.
https://publications.aap.org/pediatrics/article-abstract/127/6/e1585/30070/An-Emergency-Department-Septic-Shock-Protocol-and
http://www.ncbi.nlm.nih.gov/pubmed/21576304?tool=bestpractice.com
[23]Cruz AT, Perry AM, Williams EA, et al. Implementation of goal-directed therapy for children with suspected sepsis in the emergency department. Pediatrics. 2011 Mar;127(3):e758-66.
https://publications.aap.org/pediatrics/article-abstract/127/3/e758/65008/Implementation-of-Goal-Directed-Therapy-for
http://www.ncbi.nlm.nih.gov/pubmed/21339277?tool=bestpractice.com
[24]Chong SL, Ong GY, Venkataraman A, et al. The golden hours in paediatric septic shock--current updates and recommendations. Ann Acad Med Singap. 2014 May;43(5):267-74.
https://www.annals.edu.sg/pdf/43VolNo5May2014/V43N5p267.pdf
http://www.ncbi.nlm.nih.gov/pubmed/24919492?tool=bestpractice.com
For more information see the BMJ Best Practice topic Sepsis in children.
Inflammatory disorders
Inflammatory disorders may present with fatigue, rash, myalgia, arthralgia, pain, fever, malaise, and multisystem involvement. In some cases of inflammatory arthritis (such as JIA or inflammatory muscle disease), the presentation can be indolent with regression of motor milestones, with or without systemic upset. There is significant morbidity and mortality associated with delay in diagnosis and access to appropriate treatment. Where suspected, prompt referral to paediatric rheumatology is recommended and should not be delayed while waiting for investigations. Local pathways for referral may differ and it is important to be aware of how to seek advice when concerned.
Further information about paediatric musculoskeletal medicine, including red flags, clinical skills and guidance on musculoskeletal examinations (pGALS, pREMS), investigations, and referral guidance, is available at Paediatric Musculoskeletal Medicine (PMM).
Paediatric Musculoskeletal Matters (PMM): an e-resource to aid teaching and learning about the essentials of paediatric musculoskeletal medicine
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