Differentials

Common

Prolactinoma

History

symptoms of hyperprolactinaemia in both sexes (galactorrhoea, infertility, decreased libido, sexual dysfunction, osteoporosis), in women (oligo/amenorrhoea, menstrual disturbances, hirsutism, vaginal dryness, dyspareunia, habitual abortions, acne), in men (erectile dysfunction, gynaecomastia), in children (delayed puberty in both sexes; primary amenorrhoea, galactorrhoea in girls); symptoms of 'mass effect' (headaches, visual loss, seizures)

Exam

signs of hyperprolactinaemia (hirsutism and acne in women, gynaecomastia in men); signs of mass effect (visual field defects, cranial nerve neuropathies); signs of hypogonadism (testicular size and texture, pattern of body hair growth)

1st investigation
  • serum prolactin (PRL):

    usually >4348 picomol/L (100 micrograms/L or 2000 milliunits/L), macroprolactinomas >10,870 picomol/L (250 micrograms/L or 5000 milliunits/L)

    More
  • serum electrolytes and creatinine:

    within normal range

    More
  • urea:

    within normal range

    More
  • liver function tests and albumin:

    within normal range

    More
  • prothrombin time:

    within normal range

    More
  • thyroid-stimulating hormone and free thyroxine:

    within normal range

    More
  • pregnancy test:

    negative

    More
Other investigations
  • polyethylene glycol (PEG) precipitation:

    negative

    More
  • MRI of the pituitary gland:

    micro- or macroprolactinoma

    More
  • pituitary hormones (adrenocorticotrophic hormone, luteinising hormone, follicle-stimulating hormone, growth hormone):

    decreased in hypopituitarism

    More
  • glucose tolerance test:

    decreased in hypopituitarism

    More
  • cortisol:

    decreased in hypopituitarism

    More
  • serum testosterone:

    decreased in hypopituitarism

    More
  • serum estradiol:

    decreased in hypopituitarism

    More
  • serum dehydroepiandrosterone sulphate:

    decreased in hypopituitarism

    More
  • insulin-like growth factor 1:

    decreased in hypopituitarism

    More

Primary hypothyroidism

History

fatigue, sensitivity to cold, constipation, menstrual abnormalities (particularly menorrhagia), muscle cramps, weight gain

Exam

thyroid goitre; cool, rough, and dry skin; puffy face and hands; husky voice; slow reflexes; thin and brittle nails; carotenaemic skin colour

1st investigation
  • serum prolactin:

    <2174 picomol/L (50 micrograms/L or 1000 milliunits/L)

  • thyroid-stimulating hormone:

    elevated

  • free thyroxine:

    decreased

Other investigations

    Drug-induced hyperprolactinaemia

    History

    use of drugs known to elevate prolactin (PRL) (antipsychotics, antidepressants, opiates, cocaine, antihypertensives, gastrointestinal medicines, oestrogens, excessive alcohol intake), past medical history of conditions requiring these medicines

    Exam

    non-specific findings

    1st investigation
    • serum PRL:

      usually <4348 picomol/L (100 micrograms/L or 2000 milliunits/L)

      More
    Other investigations

      Macroprolactinaemia

      History

      usually asymptomatic; rarely presents with galactorrhoea, amenorrhoea, and infertility

      Exam

      non-specific findings

      1st investigation
      • serum prolactin (PRL):

        usually <4348 picomol/L (100 micrograms/L or 2000 milliunits/L)

        More
      Other investigations
      • polyethylene glycol (PEG) precipitation:

        percentage recovery of PRL between 40% and 60%

        More

      Pregnancy

      History

      amenorrhoea, nausea and vomiting, breast enlargement

      Exam

      non-specific findings

      1st investigation
      • serum prolactin (PRL):

        8696-21,739 picomol/L (200-500 micrograms/L or 4000-10,000 milliunits/L)

        More
      • pregnancy test:

        positive

      Other investigations

        Uncommon

        Acromegaly

        History

        symptoms of acromegaly (fatigue, paraesthesias, increased sweating, joint pain); symptoms of hyperprolactinaemia in both sexes (galactorrhoea, infertility, decreased libido, sexual dysfunction, osteoporosis), in women (oligo/amenorrhoea, menstrual disturbances, hirsutism, vaginal dryness, dyspareunia, habitual abortions, acne), in men (erectile dysfunction, gynaecomastia); symptoms of 'mass effect' (headaches, visual loss, seizures)

        Exam

        signs of acromegaly (acral enlargement, e.g., hands; tissue overgrowth, weight gain, thyroid goitre, hypertension); signs of hyperprolactinaemia (hirsutism and acne in women, gynaecomastia in men); signs of mass effect (visual field defects, cranial nerve neuropathies)

        1st investigation
        • serum prolactin (PRL):

          usually >8696 picomol/L (200 micrograms/L or 4000 milliunits/L)

          More
        Other investigations
        • serum growth hormone (GH):

          failure of GH suppression to glucose tolerance test

          More
        • insulin-like growth factor 1:

          elevated

        • MRI of the pituitary gland:

          macroadenoma

          More

        Hypothalamic mass compressing pituitary stalk

        History

        symptoms of hyperprolactinaemia in both sexes (galactorrhoea, infertility, decreased libido, sexual dysfunction, osteoporosis), in women (oligo/amenorrhoea, menstrual disturbances, hirsutism, vaginal dryness, dyspareunia, habitual abortions, acne), in men (erectile dysfunction, gynaecomastia), in children (delayed puberty in both sexes; primary amenorrhoea, galactorrhoea in girls); symptoms of 'mass effect' (headaches, visual loss, seizures)

        Exam

        signs of hyperprolactinaemia (hirsutism and acne in women, gynaecomastia in men); signs of mass effect (visual field defects, cranial nerve neuropathies); signs of hypogonadism (testicular size and texture, pattern of body hair growth)

        1st investigation
        • serum prolactin (PRL):

          usually <10,870 picomol/L (250 micrograms/L or 5000 milliunits/L)

          More
        • MRI of the pituitary gland:

          non-functioning adenomas, craniopharyngiomas, gliomas, metastatic disease

          More
        Other investigations
        • pituitary hormones (adrenocorticotrophic hormone, luteinising hormone, follicle-stimulating hormone, growth hormone):

          decreased in hypopituitarism

          More
        • glucose tolerance test:

          decreased in hypopituitarism

          More
        • cortisol:

          decreased in hypopituitarism

          More
        • serum testosterone:

          decreased in hypopituitarism

          More
        • serum estradiol:

          decreased in hypopituitarism

          More
        • serum dehydroepiandrosterone sulphate:

          decreased in hypopituitarism

          More
        • insulin-like growth factor 1:

          decreased in hypopituitarism

          More

        Multiple endocrine neoplasia syndrome type I (MEN I)

        History

        history of hyperparathyroidism, enteropancreatic tumours (insulinomas, gastrinomas), and/or adrenal adenomas; symptoms of hyperprolactinaemia (renal stones, polyuria, polydipsia, osteomalacia or rickets, fatigue, depression, constipation); symptoms of hyperprolactinaemia in both sexes (galactorrhoea, infertility, decreased libido, sexual dysfunction, osteoporosis), in women (oligo/amenorrhoea, menstrual disturbances, hirsutism, vaginal dryness, dyspareunia, habitual abortions, acne), in men (erectile dysfunction, gynaecomastia), in children (delayed puberty in both sexes; primary amenorrhoea, galactorrhoea in girls); symptoms of 'mass effect' (headaches, visual loss, seizures)

        Exam

        signs of hyperparathyroidism, insulinomas (hypoglycaemia), gastrinomas (gastric ulcers, Zollinger-Ellison syndrome), and/or adrenal adenomas (hypertension, Cushing syndrome); signs of hyperprolactinaemia (hirsutism and acne in women, gynaecomastia in men); signs of mass effect (visual field defects, cranial nerve neuropathies); signs of hypogonadism (testicular size and texture, pattern of body hair growth)

        1st investigation
        • serum prolactin (PRL):

          usually >4348 picomol/L (100 micrograms/L or 2000 milliunits/L), macroprolactinomas >10,870 picomol/L (250 micrograms/L or 5000 milliunits/L)

          More
        • MRI of the pituitary gland:

          micro- or macroprolactinoma

          More
        • serum calcium:

          elevated in hyperparathyroidism

        • parathyroid hormone:

          elevated in hyperparathyroidism

        • serum cortisol:

          elevated, loss of diurnal rhythm in Cushing syndrome

          More
        • urinary cortisol:

          elevated in Cushing syndrome

        • aldosterone/plasma renin activity ratio:

          elevated (>30) in adrenal adenoma

          More
        • serum aldosterone:

          elevated in adrenal adenoma

          More
        • plasma renin activity:

          suppressed in adrenal adenoma

          More
        Other investigations
        • overnight suppression test:

          failure of morning cortisol suppression in Cushing syndrome

          More
        • genetic testing:

          positive for menin gene (chromosome 11q13)

          More
        • sestamibi scintigraphy:

          positive in primary hyperparathyroidism

        • renal ultrasound:

          evidence of adrenal adenoma

        • fasting gastrin:

          elevated in gastrinomas

        • fasting insulin:

          elevated in insulinomas

        • CT or MRI scan abdomen:

          evidence of enteropancreatic tumours, adrenal adenomas

        Traumatic sectioning of pituitary stalk

        History

        history of surgery or radiotherapy for brain tumours; symptoms of hyperprolactinaemia in both sexes (galactorrhoea, infertility, decreased libido, sexual dysfunction, osteoporosis), in women (oligo/amenorrhoea, menstrual disturbances, hirsutism, vaginal dryness, dyspareunia, habitual abortions, acne), in men (erectile dysfunction, gynaecomastia); symptoms of 'mass effect' (headaches, visual loss, seizures); symptoms of diabetes insipidus (polyuria, polydipsia)

        Exam

        signs of hyperprolactinaemia (hirsutism and acne in women, gynaecomastia in men), signs of mass effect (visual field defects, cranial nerve neuropathies), signs of hypogonadism (testicular size and texture, pattern of body hair growth)

        1st investigation
        • serum prolactin (PRL):

          usually <4348 picomol/L (100 micrograms/L or 2000 milliunits/L)

          More
        • MRI of the pituitary gland:

          evidence of previous surgery/radiotherapy

        Other investigations
        • urine output:

          >2.5 L/day in diabetes insipidus

        • serum sodium:

          >46 mmol/L (mEq/L) in diabetes insipidus

        • antidiuretic hormone:

          undetectable in diabetes insipidus

        • serum osmolality:

          >287 mOsm/kg in diabetes insipidus

        • urine osmolality:

          <100 mOsm/kg in diabetes insipidus

        • urine specific gravity:

          <1.005 in diabetes insipidus

        • pituitary hormones (adrenocorticotrophic hormone, luteinising hormone, follicle-stimulating hormone, growth hormone):

          decreased in hypopituitarism

          More
        • glucose tolerance test:

          decreased in hypopituitarism

          More
        • cortisol:

          decreased in hypopituitarism

          More
        • serum testosterone:

          decreased in hypopituitarism

          More
        • serum estradiol:

          decreased in hypopituitarism

          More
        • serum dehydroepiandrosterone sulphate:

          decreased in hypopituitarism

          More
        • insulin-like growth factor 1:

          decreased in hypopituitarism

          More

        Lymphocytic hypophysitis

        History

        usually occurs at the end of gestation or in early post-partum period, possible history of other autoimmune diseases (e.g., Hashimoto's thyroiditis, Addison's disease, type 1 diabetes mellitus, hypoparathyroidism, autoimmune hepatitis)[1][2][17]

        Exam

        features of associated autoimmune disease (e.g., signs of hypothyroidism in Hashimoto's thyroiditis, adrenal insufficiency in Addison's disease, hypocalcaemia in hypoparathyroidism, chronic liver disease in autoimmune hepatitis)

        1st investigation
        • serum prolactin (PRL):

          usually <4348 picomol/L (100 micrograms/L or 2000 milliunits/L)

          More
        • thyroid-stimulating hormone:

          elevated in Hashimoto's thyroiditis

        • free thyroxine:

          decreased in Hashimoto's thyroiditis

        • anti-thyroid peroxidase auto-antibodies:

          positive in Hashimoto's thyroiditis

        • serum cortisol:

          decreased in Addison's disease

        • serum sodium:

          decreased in Addison's disease

        • serum potassium:

          elevated in Addison's disease

        • adrenocorticotrophic hormone (ACTH):

          elevated in Addison's disease

        • fasting glucose:

          elevated in type 1 diabetes mellitus

        • serum calcium:

          decreased in hypoparathyroidism

        • parathyroid hormone:

          decreased in hypoparathyroidism

        • aminotransferases:

          aspartate aminotransferase elevated, alanine aminotransferase elevated in autoimmune hepatitis

        • antinuclear antibodies:

          positive in autoimmune hepatitis

        • anti-smooth muscle antibodies:

          positive in autoimmune hepatitis

        • serum IgG:

          elevated in autoimmune hepatitis

        Other investigations
        • synacthen test:

          positive in Addison's disease

          More

        Granulomatous hypophysitis

        History

        history of systemic granulomatous disease (e.g., sarcoidosis, tuberculosis [TB], syphilis, or histiocytosis X)

        Exam

        signs of systemic granulomatous disease (sarcoidosis and TB: pyrexia, weight loss, lymphadenopathy, crackles on auscultation, shortness of breath, hepatosplenomegaly; syphilis: solitary painless chancre at site of infection, condyloma latum [flat skin lesion in moist skin folds], diffuse rash; histiocytosis X: bony tenderness, pyrexia, weight loss, shortness of breath)

        1st investigation
        • serum prolactin (PRL):

          usually <4348 picomol/L (100 micrograms/L or 2000 milliunits/L)

          More
        • serum ACE:

          elevated in sarcoidosis

        • chest x-ray (CXR):

          lung infiltration, hilar and mediastinal lymphadenopathy in sarcoidosis, TB, and histiocytosis X

          More
        • skeletal survey:

          lytic lesions in histiocytosis X

        • sputum smear and culture:

          smear positive for acid-fast bacilli, growth of mycobacteria on culture in TB

          More
        • tuberculin skin testing:

          positive in TB

          More
        • Venereal Disease Research Laboratory (VDRL) test:

          positive in syphilis

          More
        • rapid plasma reagin:

          positive in syphilis

          More
        Other investigations
        • high-resolution CT chest:

          lung infiltration, hilar and mediastinal lymphadenopathy in sarcoidosis and histiocytosis X

          More
        • transbronchial biopsy:

          non-caseating granulomas in sarcoidosis and TB, Langerhans cells in histiocytosis X

          More
        • lymph node biopsy:

          non-caseating granulomas in sarcoidosis and TB

        • skin biopsy:

          Langerhans cells in histiocytosis X

        • bone marrow biopsy:

          Langerhans cells in histiocytosis X

        Polycystic ovary syndrome

        History

        oligomenorrhoea (or anovulation) amenorrhoea

        Exam

        hirsutism, acne, obesity

        1st investigation
        • serum prolactin (PRL):

          <2174 picomol/L (50 micrograms/L or 1000 milliunits/L)

          More
        Other investigations
        • ultrasound of ovaries:

          polycystic ovaries

        • serum total and free testosterone:

          elevated

        • serum dehydroepiandrosterone sulphate:

          elevated

        • serum sex hormone-binding globulin:

          decreased

        • serum luteinising hormone/follicle-stimulating hormone ratio:

          elevated

        • insulin:

          elevated

        Chronic kidney disease

        History

        past medical history of chronic renal failure and dialysis

        Exam

        signs of uraemia (hypertension, yellow skin, uraemic frost [white/yellowish urea crystal depositions on face, neck, and trunk], uraemic fetor, decreased mental status)

        1st investigation
        • serum prolactin (PRL):

          <2174 picomol/L (50 micrograms/L or 1000 milliunits/L)

          More
        • serum creatinine:

          elevated (>97 micromol/L [1.1 mg/dL] in men, >106 micromol/L [1.2 mg/dL] in women)

        Other investigations
        • urinalysis:

          haematuria and/or proteinuria

        • ultrasound of kidneys:

          small size, presence of obstruction/hydronephrosis, kidney stones

        Cirrhosis

        History

        past medical history of chronic liver disease (e.g., hepatitis B or C viral infection, alcohol abuse, primary biliary cirrhosis, primary sclerosing cholangitis, autoimmune hepatitis)

        Exam

        hepatosplenomegaly, weight loss, ascites, jaundice, peripheral oedema, encephalopathy, pyrexia, dilation of superficial veins

        1st investigation
        • serum prolactin (PRL):

          <2174 picomol/L (50 micrograms/L or 1000 milliunits/L)

          More
        • aminotransferases:

          aspartate aminotransferase (AST) elevated, alanine aminotransferase (ALT) elevated

          More
        • albumin:

          decreased

          More
        • prothrombin time:

          prolonged

          More
        Other investigations
        • abdominal ultrasound:

          small liver with nodular surface; possible ascites, splenomegaly, dilated portal vein

        Chest wall trauma or surgery

        History

        history of trauma or surgery to chest wall

        Exam

        signs of trauma (e.g., burns, bruising), surgical scars on chest wall

        1st investigation
        • serum prolactin (PRL):

          usually <2174 picomol/L (50 micrograms/L or 1000 milliunits/L)

          More
        Other investigations

          Ectopic hyperprolactinaemia

          History

          exclusion of pathological, physiological, and pharmacological aetiologies of hyperprolactinaemia

          Exam

          signs of an extrapituitary tumour (e.g., ovarian)

          1st investigation
          • serum prolactin (PRL):

            usually <4348 picomol/L (100 micrograms/L or 2000 milliunits/L)

            More
          • MRI of the pituitary gland:

            no abnormality detected

          • CT chest and abdomen:

            evidence of extrapituitary tumour

          Other investigations

            Idiopathic hyperprolactinaemia

            History

            exclusion of pathological, physiological, and pharmacological aetiologies of hyperprolactinaemia

            Exam

            non-specific findings

            1st investigation
            • serum prolactin (PRL):

              usually <4348 picomol/L (100 micrograms/L or 2000 milliunits/L)

              More
            Other investigations
            • polyethylene glycol (PEG) precipitation:

              percentage recovery of PRL between 40% and 60%

              More

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