Outcome and outlook depend on the underlying aetiology of AVP-D or AVP-R, and associated comorbidities. While AVP-D or AVP-R are often lifelong conditions, AVP-D following pituitary surgery or traumatic brain injury may be transient.[3]Garrahy A, Moran C, Thompson CJ. Diagnosis and management of central diabetes insipidus in adults. Clin Endocrinol (Oxf). 2019 Jan;90(1):23-30.
https://onlinelibrary.wiley.com/doi/full/10.1111/cen.13866
http://www.ncbi.nlm.nih.gov/pubmed/30269342?tool=bestpractice.com
AVP-R secondary to hypercalcaemia or hypokalaemia commonly resolves following treatment of the underlying electrolyte disorder.[5]Kavanagh C, Uy NS. Nephrogenic diabetes insipidus. Pediatr Clin North Am. 2019 Feb;66(1):227-34.
http://www.ncbi.nlm.nih.gov/pubmed/30454745?tool=bestpractice.com
While AVP-R secondary to medication may resolve following drug discontinuation, this is often not the case in those with AVP-R secondary to lithium.[41]Ott M, Forssén B, Werneke U. Lithium treatment, nephrogenic diabetes insipidus and the risk of hypernatraemia: a retrospective cohort study. Ther Adv Psychopharmacol. 2019;9:2045125319836563.
https://journals.sagepub.com/doi/full/10.1177/2045125319836563
http://www.ncbi.nlm.nih.gov/pubmed/31007893?tool=bestpractice.com
[64]Bendz H, Aurell M. Drug-induced diabetes insipidus: incidence, prevention and management. Drug Saf. 1999 Dec;21(6):449-56.
http://www.ncbi.nlm.nih.gov/pubmed/10612269?tool=bestpractice.com
AVP-D developing in pregnancy typically resolves following delivery.
The majority of patients with chronic AVP-D are well controlled on the synthetic, long-acting arginine vasopressin (AVP) analogue desmopressin (also known as DDAVP). Patients require lifelong follow-up for any associated intracranial pathology that may have caused the AVP-D. Other anterior pituitary hormone replacement therapy must be monitored.
In patients with inherited AVP receptor pathway mutations and AVP-R, increased risks of hypernatraemia and other comorbidities have been noted. Optimal treatment can reduce the incidence of these complications.[65]Sharma S, Ashton E, Iancu D, et al. Long-term outcome in inherited nephrogenic diabetes insipidus. Clin Kidney J. 2019 Apr;12(2):180-7.
https://academic.oup.com/ckj/article/12/2/180/4969891
http://www.ncbi.nlm.nih.gov/pubmed/30976394?tool=bestpractice.com
Patients with large-volume polyuria will need regular renal or bladder imaging, to avoid occult bladder or renal tract abnormalities such as hydronephrosis and bladder dysfunction.[66]Shalev H, Romanovsky I, Knoers NV, et al. Bladder function impairment in aquaporin-2 defective nephrogenic diabetes insipidus. Nephrol Dial Transplant. 2004 Mar;19(3):608-13.
https://academic.oup.com/ndt/article/19/3/608/1810670
http://www.ncbi.nlm.nih.gov/pubmed/14767016?tool=bestpractice.com