Cancers of the anal region account for <1% of gastrointestinal tumours and <3% of all new cancer diagnoses.[4]Rao S, Guren MG, Khan K, et al. Anal cancer: ESMO clinical practice guidelines for diagnosis, treatment and follow-up. Ann Oncol. 2021 Sep;32(9):1087-100.
https://www.annalsofoncology.org/article/S0923-7534(21)02064-0/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/34175386?tool=bestpractice.com
It is estimated that there will be 10,540 new cases of cancers of the anus, anal canal, and anorectum in the US in 2024 and approximately 2190 deaths. Two-thirds of the new cases are expected to occur in women.[5]American Cancer Society. Cancer facts & figures 2024. 2024 [internet publication].
https://www.cancer.org/research/cancer-facts-statistics/all-cancer-facts-figures/2024-cancer-facts-figures.html
At least 80% of patients have squamous cell carcinomas.[6]Shiels MS, Kreimer AR, Coghill AE, et al. Anal cancer incidence in the United States, 1977-2011: distinct patterns by histology and behavior. Cancer Epidemiol Biomarkers Prev. 2015 Oct;24(10):1548-56.
https://www.doi.org/10.1158/1055-9965.EPI-15-0044
http://www.ncbi.nlm.nih.gov/pubmed/26224796?tool=bestpractice.com
[7]Grulich AE, Poynten IM, Machalek DA, et al. The epidemiology of anal cancer. Sex Health. 2012 Dec;9(6):504-8.
http://www.ncbi.nlm.nih.gov/pubmed/22958581?tool=bestpractice.com
Approximately 15% of patients have adenocarcinomas.[6]Shiels MS, Kreimer AR, Coghill AE, et al. Anal cancer incidence in the United States, 1977-2011: distinct patterns by histology and behavior. Cancer Epidemiol Biomarkers Prev. 2015 Oct;24(10):1548-56.
https://www.doi.org/10.1158/1055-9965.EPI-15-0044
http://www.ncbi.nlm.nih.gov/pubmed/26224796?tool=bestpractice.com
These have a similar natural history to that of rectal cancer and are treated in a similar way.[8]National Comprehensive Cancer Network. NCCN clinical practice guidelines in oncology: anal carcinoma [internet publication].
https://www.nccn.org/professionals/physician_gls/default.aspx
For treatment of rectal cancer, see Colorectal cancer.
The incidence of squamous cell carcinoma of the anus (SCCA) is increasing. One study reported an increase in incidence of SCCA in the US of 2.9% per year between 2000 and 2011.[6]Shiels MS, Kreimer AR, Coghill AE, et al. Anal cancer incidence in the United States, 1977-2011: distinct patterns by histology and behavior. Cancer Epidemiol Biomarkers Prev. 2015 Oct;24(10):1548-56.
https://www.doi.org/10.1158/1055-9965.EPI-15-0044
http://www.ncbi.nlm.nih.gov/pubmed/26224796?tool=bestpractice.com
The incidence rate for anal adenocarcinoma remained static during the same period. Another study reported an increase in incidence of SCCA of 2.7% per year between 2001 and 2015, with marked increases in incidence in people aged 50 years and older.[9]Deshmukh AA, Suk R, Shiels MS, et al. Recent trends in squamous cell carcinoma of the anus incidence and mortality in the United States, 2001-2015. J Natl Cancer Inst. 2020 Aug 1;112(8):829-38.
https://www.doi.org/10.1093/jnci/djz219
http://www.ncbi.nlm.nih.gov/pubmed/31742639?tool=bestpractice.com
In the UK, the annual incidence is 1 per 100,000, with approximately 500 new cases per year.[10]Association of Coloproctology of Great Britain and Ireland. Guidelines for the management of colorectal cancer. 3rd ed. London, UK: Association of Coloproctology of Great Britain and Ireland; 2007.
Human papillomavirus (HPV) is detectable in 95% of SCCAs.[11]Baricevic I, He X, Chakrabarty B, et al. High-sensitivity human papilloma virus genotyping reveals near universal positivity in anal squamous cell carcinoma: different implications for vaccine prevention and prognosis. Eur J Cancer. 2015 Apr;51(6):776-85.
http://www.ncbi.nlm.nih.gov/pubmed/25702585?tool=bestpractice.com
Immunosuppression likely facilitates persistent anal HPV infection, leading to increased cancer risk. There is a clear association between HIV and anal canal cancer. People living with HIV have a 19-fold increased incidence of anal cancer, compared with people without HIV.[12]Colón-López V, Shiels MS, Machin M, et al. Anal cancer risk among people with HIV infection in the United States. J Clin Oncol. 2018 Jan 1;36(1):68-75.
https://www.doi.org/10.1200/JCO.2017.74.9291
http://www.ncbi.nlm.nih.gov/pubmed/29140774?tool=bestpractice.com
Incidence increases with age and is highest in men who have sex with men and people with AIDS.[12]Colón-López V, Shiels MS, Machin M, et al. Anal cancer risk among people with HIV infection in the United States. J Clin Oncol. 2018 Jan 1;36(1):68-75.
https://www.doi.org/10.1200/JCO.2017.74.9291
http://www.ncbi.nlm.nih.gov/pubmed/29140774?tool=bestpractice.com
[13]Clifford GM, Georges D, Shiels MS, et al. A meta-analysis of anal cancer incidence by risk group: toward a unified anal cancer risk scale. Int J Cancer. 2021 Jan 1;148(1):38-47.
https://www.doi.org/10.1002/ijc.33185
http://www.ncbi.nlm.nih.gov/pubmed/32621759?tool=bestpractice.com
Solid organ transplant recipients have a 6.8-fold increased incidence of anal cancer, compared with the general population.[14]Albuquerque A, Stirrup O, Nathan M, et al. Burden of anal squamous cell carcinoma, squamous intraepithelial lesions and HPV16 infection in solid organ transplant recipients: a systematic review and meta-analysis. Am J Transplant. 2020 Dec;20(12):3520-8.
https://www.doi.org/10.1111/ajt.15942
http://www.ncbi.nlm.nih.gov/pubmed/32343489?tool=bestpractice.com
Patients with haematological malignancies and some autoimmune diseases (Crohn's disease, psoriasis, polyarteritis nodosa, and granulomatosis with polyangiitis), also have a higher risk of SCCA compared with the general population.[13]Clifford GM, Georges D, Shiels MS, et al. A meta-analysis of anal cancer incidence by risk group: toward a unified anal cancer risk scale. Int J Cancer. 2021 Jan 1;148(1):38-47.
https://www.doi.org/10.1002/ijc.33185
http://www.ncbi.nlm.nih.gov/pubmed/32621759?tool=bestpractice.com
[15]Sunesen KG, Nørgaard M, Thorlacius-Ussing O, et al. Immunosuppressive disorders and risk of anal squamous cell carcinoma: a nationwide cohort study in Denmark, 1978-2005. Int J Cancer. 2010 Aug 1;127(3):675-84.
https://www.doi.org/10.1002/ijc.25080
http://www.ncbi.nlm.nih.gov/pubmed/19960431?tool=bestpractice.com