Treatment options for chronic rhinosinusitis with nasal polyps (CRSwNP) include topical medications, principally intranasal corticosteroids, nasal irrigations, systemic medications including biologics, and surgery.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
Nasal polyposis in children is rare, and should prompt additional investigations to exclude cystic fibrosis.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
Nasal polyps may also be a feature of the nasal and sinus inflammation seen in primary ciliary dyskinesia. Management of nasal polyposis in children is similar to that for adults; surgery is reserved for severe CRSwNP resistant to medical treatment.
Intranasal corticosteroids
Intranasal corticosteroids are the first-line treatment for patients with chronic rhinosinusitis. They are well tolerated and effectively reduce nasal polyp size, reduce symptoms, improve quality of life, and prevent polyp recurrence after endoscopic sinus surgery.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
For patients with mild to moderate symptoms (visual analogue scale [VAS] score 0-7), the first-line treatment is a 3-month course of an intranasal corticosteroid spray, such as fluticasone or mometasone. There is insufficient evidence to suggest one type of corticosteroid over another.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
The patient is reviewed at 3 months and, if there has been satisfactory improvement, the patient may continue to use the intranasal corticosteroid spray, at the lowest effective dose, with review every 6 months. Intranasal corticosteroid delivery using stents and exhalation delivery systems has also shown promise.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
For patients with severe symptoms (VAS score >7 to 10), the first-line treatment is an intranasal corticosteroid spray, plus consideration of a short course of an oral corticosteroid.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
[
]
In people with nasal polyps, how does giving short-course oral steroids alone compare with placebo?/cca.html?targetUrl=https://cochranelibrary.com/cca/doi/10.1002/cca.1365/fullShow me the answer A short course (7-21 days) of a systemic corticosteroid, with or without local corticosteroid treatment, results in a significant reduction in total symptom score and nasal polyp score in patients with CRSwNP.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
[36]Head K, Chong LY, Hopkins C, et al. Short-course oral steroids as an adjunct therapy for chronic rhinosinusitis. Cochrane Database Syst Rev. 2016 Apr 26;4:CD011992.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD011992.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/27115214?tool=bestpractice.com
[37]Head K, Chong LY, Hopkins C, et al. Short-course oral steroids alone for chronic rhinosinusitis. Cochrane Database Syst Rev. 2016 Apr 26;4:CD011991.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD011991.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/27113367?tool=bestpractice.com
One to two courses of systemic corticosteroids can be given every year along with intranasal corticosteroid treatment in patients with partial or uncontrolled disease.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
Following completion of the oral corticosteroid course, the patient then continues on the intranasal corticosteroid. The patient is reviewed at 1 month and, if there has been satisfactory improvement, the patient should continue on the intranasal corticosteroid with review at 3 months.
Adjunctive therapies
Doxycycline may have a modest effect in addition to intranasal corticosteroids when used for 3-12 weeks.[38]Van Zele T, Gevaert P, Holtappels G, et al. Oral steroids and doxycycline: two different approaches to treat nasal polyps. J Allergy Clin Immunol. 2010 May;125(5):1069-76.e4.
http://www.ncbi.nlm.nih.gov/pubmed/20451040?tool=bestpractice.com
[39]Pinto Bezerra Soter AC, Bezerra TF, Pezato R, et al. Prospective open-label evaluation of long-term low-dose doxycycline for difficult-to-treat chronic rhinosinusitis with nasal polyps. Rhinology. 2017 Jun 1;55(2):175-80.
http://www.ncbi.nlm.nih.gov/pubmed/28434014?tool=bestpractice.com
Nasal saline irrigation with isotonic saline or Ringer’s lactate can also be beneficial.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
[40]Chong LY, Head K, Hopkins C, et al. Saline irrigation for chronic rhinosinusitis. Cochrane Database Syst Rev. 2016;(4):CD011995.
http://onlinelibrary.wiley.com/doi/10.1002/14651858.CD011995.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/27115216?tool=bestpractice.com
Adding xylitol, sodium hyaluronate, and xyloglucan to nasal saline irrigation may have a positive effect.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
Leukotriene receptor antagonists (e.g., montelukast) are sometimes used as an adjunct to intranasal corticosteroids, particularly in patients with aspirin/non-steroidal anti-inflammatory drug (NSAID) hypersensitivity; however, clinical trial evidence for their efficacy is lacking, and they are not routinely recommended.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
Biologics
Biologics (e.g., dupilumab, mepolizumab, omalizumab) target specific inflammatory pathways which are important in disease pathophysiology. As most patients with CRSwNP have type 2 inflammation, biologics for managing CRSwNP are designed to modify the type 2 inflammatory response.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
The American Academy of Allergy, Asthma & Immunology (AAAAI)/American College of Allergy, Asthma & Immunology (ACAAI) Joint Task Force guideline panel suggests using biologics over no biologics, depending on the preferences of patients and/or their carers for individual outcomes, disease severity, and availability of other treatment options.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
Consider biologics in patients on intranasal corticosteroids for at least 4 weeks who do not show symptom improvement.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
Biologics may be preferred over other therapies in patients with high disease severity at presentation.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
Dosing for biologics for CRSwNP varies based on the type of biologic and may depend on patient’s weight, laboratory tests, or severity of disease.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
Do not use biologics in patients in whom symptoms improve with intranasal corticosteroids, surgery, or aspirin therapy after desensitisation (ATAD).[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
Individuals with symptoms impairing quality of life despite regular use of intranasal corticosteroids may be considered for treatment, while taking additional factors into consideration (e.g., previous sinus surgery, need for oral corticosteroids, comorbid asthma).[41]Fokkens WJ, Lund V, Bachert C, et al. EUFOREA consensus on biologics for CRSwNP with or without asthma. Allergy. 2019 Dec;74(12):2312-9.
https://www.doi.org/10.1111/all.13875
http://www.ncbi.nlm.nih.gov/pubmed/31090937?tool=bestpractice.com
Biologics are recommended in patients with bilateral polyps who have had sinus surgery or are not fit for surgery and who have three of the following characteristics:[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
Evidence of type 2 hypersensitivity (tissue eosinophils ≥10/high-power field or blood eosinophils ≥250 cells/microlitre or total IgE ≥100 IU/mL)
Contraindication to systemic corticosteroids, need for systemic corticosteroids or continuous use of systemic corticosteroids (≥2 courses per year or long term [>3 months] low-dose corticosteroids)
Significantly impaired quality of life (SNOT-22 score ≥40)
Anosmic on smell test, and/or
A diagnosis of comorbid asthma needing regular inhaled corticosteroids
Intranasal corticosteroid therapy should be continued in patients when biologics are introduced. If the biologic is sufficiently effective and symptoms become almost negligible/very mild, corticosteroid dose could be reduced and even stopped.
Dupilumab is directed against the interleukin-4 receptor alpha subunit, thereby blocking the activity of interleukin-4 and interleukin-13. It has been shown to reduce polyp size and improve symptoms, computed tomography (CT) appearances, and sense of smell in patients already on an intranasal corticosteroid.[22]Bachert C, Mannent L, Naclerio RM, et al. Effect of subcutaneous dupilumab on nasal polyp burden in patients with chronic sinusitis and nasal polyposis: a randomized clinical trial. JAMA. 2016 Feb 2;315(5):469-79.
https://jamanetwork.com/journals/jama/fullarticle/2484681
http://www.ncbi.nlm.nih.gov/pubmed/26836729?tool=bestpractice.com
Dupilumab is approved in the US as add-on maintenance treatment in adults with inadequately controlled CRSwNP. It is also approved in Europe as an add-on therapy with intranasal corticosteroids for adults with severe CRSwNP for whom therapy with systemic corticosteroids and/or surgery do not provide adequate disease control. Ocular adverse reactions have been reported; healthcare professionals should review new onset or worsening ocular symptoms and refer patients for ophthalmological examination as appropriate.[42]Safety update: dupilumab and ocular adverse reactions. Drug Ther Bull. 2023 Jan;61(1):6.
https://www.doi.org/10.1136/dtb.2022.000073
http://www.ncbi.nlm.nih.gov/pubmed/36543342?tool=bestpractice.com
Mepolizumab blocks the activity of the pro-eosinophilic cytokine interleukin-5.[20]Gevaert P, Van Bruaene N, Cattaert T, et al. Mepolizumab, a humanized anti-IL-5 mAb, as a treatment option for severe nasal polyposis. J Allergy Clin Immunol. 2011 Nov;128(5):989-95.e1-8.
http://www.ncbi.nlm.nih.gov/pubmed/21958585?tool=bestpractice.com
It has been shown to reduce the need for repeat surgery in those already taking an intranasal corticosteroid.[21]Bachert C, Sousa AR, Lund VJ, et al. Reduced need for surgery in severe nasal polyposis with mepolizumab: randomized trial. J Allergy Clin Immunol. 2017 Oct;140(4):1024-31.e14.
http://www.ncbi.nlm.nih.gov/pubmed/28687232?tool=bestpractice.com
Mepolizumab is approved in the US and Europe for four eosinophil-driven diseases, including CRSwNP.[22]Bachert C, Mannent L, Naclerio RM, et al. Effect of subcutaneous dupilumab on nasal polyp burden in patients with chronic sinusitis and nasal polyposis: a randomized clinical trial. JAMA. 2016 Feb 2;315(5):469-79.
https://jamanetwork.com/journals/jama/fullarticle/2484681
http://www.ncbi.nlm.nih.gov/pubmed/26836729?tool=bestpractice.com
Omalizumab inhibits IgE binding to the high-affinity IgE receptor on mast cells and basophils. It is approved in the US as add-on maintenance treatment for CRSwNP in adults with an inadequate response to intranasal corticosteroids, and in Europe as add-on therapy with intranasal corticosteroids for adults with severe CRSwNP in whom intranasal corticosteroids do not provide adequate disease control.
Aspirin therapy after desensitisation (ATAD)
ATAD can be considered in patients with CRSwNP with a convincing history of a respiratory reaction to aspirin/NSAIDs (as judged by the clinician) or the development of respiratory symptoms during an aspirin challenge.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
ATAD has been recommended for treating patients with CRSwNP and NSAID-exacerbated respiratory disease (NERD) who agree to comply with the therapy.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
The AAAAI/ACAAI Joint Task Force guideline panel suggests using ATAD over no ATAD in patients with NERD but not in those without NERD.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
Intranasal corticosteroid therapy should be continued in patients when ATAD is introduced. If ATAD is sufficiently effective and symptoms become almost negligible/very mild, corticosteroid dose could be reduced and even stopped.
ATAD is preferred in patients who are unable to tolerate NSAIDs but need them for other indications such as cardiovascular disease.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
In patients with NERD who do not require NSAIDs to manage other conditions and who wish to avoid the desensitisation procedure, biologics are preferred over ATAD.[4]Rank MA, Chu DK, Bognanni A, et al. The Joint Task Force on Practice Parameters GRADE guidelines for the medical management of chronic rhinosinusitis with nasal polyposis. J Allergy Clin Immunol. 2023 Feb;151(2):386-98.
https://www.jacionline.org/article/S0091-6749(22)01484-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/36370881?tool=bestpractice.com
ATAD involves desensitising patients with NERD to aspirin, followed by daily aspirin therapy. Desensitisation itself does not provide immediate clinical benefit for patients with NERD but is necessary to allow patients to take aspirin daily, which in turn may lead to improvement in chronic rhinosinusitis symptoms. Oral ATAD is effective in improving quality of life and total nasal symptom score in patients with NERD.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
Appropriate preventive measures (i.e., Helicobacter pylori eradication, proton-pump inhibitors, H2 antagonists) should be introduced and continued during ATAD to prevent adverse effects following aspirin treatment.[2]Fokkens WJ, Lund VJ, Hopkins C, et al. European position paper on rhinosinusitis and nasal polyps 2020. Rhinology. 2020 Feb 20;58(suppl s29):1-464.
http://www.ncbi.nlm.nih.gov/pubmed/32077450?tool=bestpractice.com
Refractory to medical therapy
If there is no or minimal improvement in symptoms at the initial 3-month follow-up, most clinicians suggest surgery for removal of polyps. This necessitates a preoperative CT scan to examine the local anatomy and the extent and location of the polyps, in order to make an accurate surgical plan.
Whichever surgical technique is employed, patients usually receive follow-up saline douching and intranasal corticosteroids.[43]Punekar YS, Ahmad A, Saleh HA. Estimating the effect of nasal steroid treatment on repeat polypectomies: survival time analysis using the General Practice Research Database. Rhinology. 2011 Jun;49(2):190-4.
http://www.ncbi.nlm.nih.gov/pubmed/21743875?tool=bestpractice.com
The evidence relating to the effectiveness of different types of surgery versus medical treatment for adults with chronic rhinosinusitis and nasal polyps is of very low quality. The evidence thus far does not show that one treatment is better than another in terms of patient-reported symptom scores and quality-of-life measurements.[44]Rimmer J, Fokkens W, Chong LY, et al. Surgical versus medical interventions for chronic rhinosinusitis with nasal polyps. Cochrane Database Syst Rev. 2014;(12):CD006991.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD006991.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/25437000?tool=bestpractice.com
Patients with CRSwNP and comorbid asthma are at a higher risk of undergoing revision surgery, and many of these patients experience poor symptom control, the need for repeated systemic corticosteroids and multiple surgeries.[45]Chong LY, Piromchai P, Sharp S, et al. Biologics for chronic rhinosinusitis. Cochrane Database Syst Rev. 2021 Mar 12;3:CD013513.
https://www.doi.org/10.1002/14651858.CD013513.pub3
http://www.ncbi.nlm.nih.gov/pubmed/33710614?tool=bestpractice.com
Postoperative doxycycline for 3 weeks or 12 weeks may have a beneficial effect.[38]Van Zele T, Gevaert P, Holtappels G, et al. Oral steroids and doxycycline: two different approaches to treat nasal polyps. J Allergy Clin Immunol. 2010 May;125(5):1069-76.e4.
http://www.ncbi.nlm.nih.gov/pubmed/20451040?tool=bestpractice.com
[39]Pinto Bezerra Soter AC, Bezerra TF, Pezato R, et al. Prospective open-label evaluation of long-term low-dose doxycycline for difficult-to-treat chronic rhinosinusitis with nasal polyps. Rhinology. 2017 Jun 1;55(2):175-80.
http://www.ncbi.nlm.nih.gov/pubmed/28434014?tool=bestpractice.com
Clinicians may also use a macrolide antibiotic.