Case history #1
A 19-year-old man is diagnosed with an aggressive diffuse large B-cell lymphoma. The disease is bulky, involving lymph nodes (above and below the diaphragm), the spleen, and the bone marrow. Serum lactate dehydrogenase is significantly elevated but renal function and electrolytes are within normal limits. Twenty-four hours after initiation of aggressive chemotherapy he complains of nausea, vomiting, diarrhea, and lethargy. He has become oliguric and is hypertensive and tachycardic. Biochemistry reveals hyperuricemia, hyperkalemia, hyperphosphatemia, elevated blood urea nitrogen, and elevated creatinine.
Case history #2
A 69-year-old woman with a 2-year history of chronic lymphocytic leukemia presents with a white blood cell (WBC) count of 41,000/microliter. She has a past medical history of hypertension and mild renal impairment related to the use of nonsteroidal anti-inflammatory drugs for osteoarthritis. Seven days after initiation of treatment with fludarabine, she complains of fatigue and weakness. The WBC count has fallen to within normal levels but serum biochemistry reveals hyperuricemia, hyperkalemia, hyperphosphatemia, hypocalcemia, and a significant deterioration in renal function.
Other presentations
Other clinical manifestations of TLS include edema, fluid retention, hematuria, flank pain, oliguria or anuria, cloudy urine, joint pain/discomfort, muscle cramps and spasms, paralysis, paresthesias, tetany, syncope, heart failure, cardiac dysrhythmias, bradycardia, seizures, confusion, delirium, hallucinations, and sudden death.[2]Cairo MS, Bishop M. Tumour lysis syndrome: new therapeutic strategies and classification. Br J Haematol. 2004 Oct;127(1):3-11.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2141.2004.05094.x
http://www.ncbi.nlm.nih.gov/pubmed/15384972?tool=bestpractice.com
Clinical manifestations of TLS typically occur within 12 to 72 hours after initiation of cancer treatment.[2]Cairo MS, Bishop M. Tumour lysis syndrome: new therapeutic strategies and classification. Br J Haematol. 2004 Oct;127(1):3-11.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2141.2004.05094.x
http://www.ncbi.nlm.nih.gov/pubmed/15384972?tool=bestpractice.com
[3]Mughal TI, Ejaz AA, Foringer JR, et al. An integrated clinical approach for the identification, prevention, and treatment of tumor lysis syndrome. Cancer Treat Rev. 2010 Apr;36(2):164-76.
http://www.ncbi.nlm.nih.gov/pubmed/20031331?tool=bestpractice.com
Laboratory signs of TLS may appear as early as 6 hours after treatment initiation.[4]Jones GL, Will A, Jackson GH, et al. Guidelines for the management of tumour lysis syndrome in adults and children with haematological malignancies on behalf of the British Committee for Standards in Haematology. Br J Haematol. 2015 Jun;169(5):661-71.
https://onlinelibrary.wiley.com/doi/full/10.1111/bjh.13403
http://www.ncbi.nlm.nih.gov/pubmed/25876990?tool=bestpractice.com
[5]Fischer K, Al-Sawaf O, Hallek M. Preventing and monitoring for tumor lysis syndrome and other toxicities of venetoclax during treatment of chronic lymphocytic leukemia. Hematology Am Soc Hematol Educ Program. 2020 Dec 4;2020(1):357-62.
https://www.doi.org/10.1182/hematology.2020000120
http://www.ncbi.nlm.nih.gov/pubmed/33275717?tool=bestpractice.com
[6]Tambaro FP, Wierda WG. Tumour lysis syndrome in patients with chronic lymphocytic leukaemia treated with BCL-2 inhibitors: risk factors, prophylaxis, and treatment recommendations. Lancet Haematol. 2020 Feb;7(2):e168-e176.
http://www.ncbi.nlm.nih.gov/pubmed/32004486?tool=bestpractice.com
[7]Medicines and Healthcare products Regulatory Agency. Venetoclax (Venclyxto): updated recommendations on tumour lysis syndrome (TLS). Dec 2021 [internet publication].
https://www.gov.uk/drug-safety-update/venetoclax-venclyxtov-updated-recommendations-on-tumour-lysis-syndrome-tls