The most difficult aspect of treating a rickettsial infection is considering that the patient may have a rickettsial infection in the first place. Therefore it is important to start appropriate empirical antibiotic therapy as soon as rickettsial infection is reasonably considered in the differential, without waiting for the results of tests to confirm the diagnosis. Prompt treatment is essential as it results in improved outcomes.
Antibiotic therapy
The first-line treatment for all rickettsial diseases in people of all ages is doxycycline (a tetracycline class antibiotic).[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
Doxycycline can be given as oral or intravenous therapy depending on the severity of symptoms. A clinical response, including abatement of fever, should be evident in 48 to 72 hours.[29]Toumi A, Aouam A, Ben Romdhane F, et al. Single-dose doxycycline for the treatment of Mediterranean spotted fever. Clin Microbiol Infect. 2011 May;17 Suppl 4:S1-895, A1-4.
http://www.ncbi.nlm.nih.gov/pubmed/22069786?tool=bestpractice.com
Doxycycline should be continued for at least 3 days after clinical improvement is seen, with a typical course being 5 to 7 days.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
Tetracycline may also be used; however, doxycycline has a more convenient dosing schedule and is the preferred option.
If the patient is allergic to tetracyclines, an infectious disease consultant and/or an allergy and immunology specialist should be consulted. Azithromycin is a suitable alternative in patients with scrub typhus and a severe doxycycline allergy.[30]Centers for Disease Control and Prevention. Typhus fevers: information for healthcare providers. Mar 2021 [internet publication].
https://www.cdc.gov/typhus/healthcare-providers/index.html
Low-quality evidence suggests that it is as effective as doxycycline and tetracycline for the treatment of scrub typhus in terms of treatment failure and time to defervescence.[31]El Sayed I, Liu Q, Wee I, et al. Antibiotics for treating scrub typhus. Cochrane Database Syst Rev. 2018 Sep 24;(9):CD002150.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD002150.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/30246875?tool=bestpractice.com
Rifampicin is an alternative option for patients with scrub typhus and a severe doxycycline allergy.[30]Centers for Disease Control and Prevention. Typhus fevers: information for healthcare providers. Mar 2021 [internet publication].
https://www.cdc.gov/typhus/healthcare-providers/index.html
Chloramphenicol is another option, but is generally not recommended as it is associated with numerous adverse effects.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
Chloramphenicol was associated with the highest cure rate for scrub typhus in children in one network meta-analysis.[32]Zeng BS, Zeng BY, Hung CM, et al. The efficacy and tolerability of antibiotics in scrub typhus: an updated network meta-analysis of randomized controlled trials. Int J Infect Dis. 2022 Sep;122:461-8.
https://www.ijidonline.com/article/S1201-9712(22)00358-7/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/35724826?tool=bestpractice.com
Commonly used antibiotics (e.g., penicillins and cephalosporins) do not work against rickettsiae because of the unusual chemical nature of their bacterial cell wall, and sulfonamides have been associated with an increased disease severity and death.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
Treatment in children
Doxycycline is the drug of choice for children with rickettsial infections.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
Although repeated courses of tetracycline were associated with staining of permanent teeth in young children, no evidence suggests that doxycycline causes any such tooth staining.[33]Volovitz B, Shkap R, Amir J, et al. Absence of tooth staining with doxycycline treatment in young children. Clin Pediatr (Phila). 2007 Mar;46(2):121-6.
http://www.ncbi.nlm.nih.gov/pubmed/17325084?tool=bestpractice.com
[34]Todd SR, Dahlgren FS, Traeger MS, et al. No visible dental staining in children treated with doxycycline for suspected Rocky Mountain Spotted Fever. J Pediatr. 2015 May;166(5):1246-51.
https://www.jpeds.com/article/S0022-3476(15)00135-3/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/25794784?tool=bestpractice.com
[35]Cross R, Ling C, Day NP, et al. Revisiting doxycycline in pregnancy and early childhood - time to rebuild its reputation? Expert Opin Drug Saf. 2016;15(3):367-82.
https://www.tandfonline.com/doi/full/10.1517/14740338.2016.1133584
http://www.ncbi.nlm.nih.gov/pubmed/26680308?tool=bestpractice.com
Tetracycline may also be used in children >8 years of age; however, doxycycline has a more convenient dosing schedule and can be used in younger children, so is the preferred option.
CDC: research on doxycycline and tooth staining
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Treatment in pregnant or breastfeeding women
The care of pregnant women with rickettsial infection should be undertaken in consultation with an infectious disease consultant. Maternal infection with scrub typhus has been associated with poor maternal and neonatal outcomes (including high miscarriage rates).[5]Bonell A, Lubell Y, Newton PN, et al. Estimating the burden of scrub typhus: a systematic review. PLoS Negl Trop Dis. 2017 Sep;11(9):e0005838.
https://journals.plos.org/plosntds/article?id=10.1371/journal.pntd.0005838
http://www.ncbi.nlm.nih.gov/pubmed/28945755?tool=bestpractice.com
Tetracyclines as a group are generally contraindicated in pregnant women, due to their potential toxicity to both fetus and mother.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
However, a review of the evidence suggested that the safety profile of doxycycline is significantly different to other tetracyclines and that there was no correlation between use of doxycycline and teratogenic effects.[35]Cross R, Ling C, Day NP, et al. Revisiting doxycycline in pregnancy and early childhood - time to rebuild its reputation? Expert Opin Drug Saf. 2016;15(3):367-82.
https://www.tandfonline.com/doi/full/10.1517/14740338.2016.1133584
http://www.ncbi.nlm.nih.gov/pubmed/26680308?tool=bestpractice.com
Low levels of doxycycline are excreted in breast milk. The use of a short course (5 to 7 days) of doxycycline typically recommended for treatment of rickettsial diseases is probably safe during lactation.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
There are limited data to support the use of other antimicrobial agents in the treatment of tick-borne rickettsial diseases during pregnancy. Treatment alternatives for pregnant women may include azithromycin, chloramphenicol, or rifampicin; however, a specialist should decide the most appropriate regimen on a case by case basis. Caution is advised when using chloramphenicol late in the third trimester of pregnancy due to a theoretical risk of grey baby syndrome.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
Critically ill patients
Some patients with rickettsial infection may be extremely unwell and close to death. This is particularly true of patients with scrub typhus (caused by Orientia tsutsugamushi). Intensive medical support in the intensive care unit is urgently required, including appropriate antibiotics. Fluid balance and serum electrolytes should be monitored closely. Some patients may need transfusions of packed red blood cells or platelets. Critically ill patients might require adjunctive therapies for seizures, intracranial hypertension, shock, or disseminated intravascular coagulation.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
[36]Lantos PM, McKinney R. Rickettsial and ehrlichial diseases. In: Cherry JD, Harrison GJ, Kaplan SL, et al, eds. Feigin and Cherry’s textbook of pediatric infectious diseases. 7th ed. Philadelphia, PA: Elsevier Saunders; 2014:2647‐66.
Other bacterial infections
For patients whose presentation may be consistent with a serious, different bacterial infection, therapy needs to begin presumptively, and empirical antibiotics are indicated until blood cultures or clinical course rule out the alternative diagnosis. An antibiotic active against Neisseria meningitidis, such as a parenteral third-generation cephalosporin, is also appropriate for other bacterial infections that can occasionally mimic rickettsial spotted fevers (e.g., pneumococcal bacteraemia in asplenic hosts).[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
If sepsis or toxic shock syndrome caused by Staphylococcus aureus cannot be excluded, empirical therapy is appropriate.
Patients with rickettsial infection who receive therapy within the first week of illness will generally show signs of improvement, including abatement of fever, within 72 hours of initiating doxycycline therapy. Lack of improvement suggests the need to search for an alternative diagnosis.[22]Biggs HM, Behravesh CB, Bradley KK, et al. Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever and other spotted fever group rickettsioses, ehrlichioses, and anaplasmosis - United States. MMWR Recomm Rep. 2016 May 13;65(2):1-44.
https://www.cdc.gov/mmwr/volumes/65/rr/rr6502a1.htm
http://www.ncbi.nlm.nih.gov/pubmed/27172113?tool=bestpractice.com
[37]Buckingham SC, Marshall GS, Schutze GE, et al. Clinical and laboratory features, hospital course, and outcome of Rocky Mountain spotted fever in children. J Pediatr. 2007 Feb;150(2):180-4, 184.e1.
http://www.ncbi.nlm.nih.gov/pubmed/17236897?tool=bestpractice.com