JIA is the most common chronic rheumatic disorder of childhood.
There are several limitations in the methods applied to study the epidemiology, including the use of different classification criteria. Epidemiological studies focusing on children seen in hospitals and clinics report lower prevalences compared with community-based studies. A population-based study in Rochester, Minnesota demonstrated a prevalence of 86.1 and an incidence of 11.7 per 100,000 children aged under 16 years.[5]Peterson LS, Mason T, Nelson AM, et al. Juvenile rheumatoid arthritis in Rochester, Minnesota 1960-1993: is the epidemiology changing? Arthritis Rheum. 1996 Aug;39(8):1385-90.
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A study in Nordic countries found that the incidence was 15 per 100,000 children per year.[6]Berntson L, Andersson Gare B, Fasth A, et al. Incidence of juvenile idiopathic arthritis in the Nordic countries: a population based study with special reference to the validity of the ILAR and EULAR criteria. J Rheumatol. 2003 Oct;30(10):2275-82.
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One meta-analysis reported an incidence of 1.6 to 23 cases per 100,000 children per year and a prevalence of 3.8 to 400 cases per 100,000 children per year in Europe.[7]Thierry S, Fautrel B, Lemelle I, et al. Prevalence and incidence of juvenile idiopathic arthritis: a systematic review. Joint Bone Spine. 2014 Mar;81(2):112-7.
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JIA is 3 to 6.6 times more common in females than in males.[8]Cattalini M, Soliani M, Caparello MC, et al. Sex differences in pediatric rheumatology. Clin Rev Allergy Immunol. 2019 Jun;56(3):293-307.
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Oligoarticular JIA is the most common subtype (50% to 60% of cases), followed by polyarticular JIA (30% to 35% of cases).[9]Weiss JE, Ilowite NT. Juvenile idiopathic arthritis. Rheum Dis Clin North Am. 2007 Aug;33(3):441-70.
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Oligoarticular JIA and rheumatoid factor (RF)-negative JIA typically affect young, female children.[8]Cattalini M, Soliani M, Caparello MC, et al. Sex differences in pediatric rheumatology. Clin Rev Allergy Immunol. 2019 Jun;56(3):293-307.
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RF-positive polyarticular JIA is typically seen in teenage girls. Enthesitis-related JIA has male predominance, usually in boys after the age of 6 years.[10]Aggarwal A, Misra DP. Enthesitis-related arthritis. Clin Rheumatol. 2015 Nov;34(11):1839-46.
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Systemic-onset juvenile idiopathic arthritis (SoJIA) comprises 10% to 20% of all JIA and affects boys and girls equally.[9]Weiss JE, Ilowite NT. Juvenile idiopathic arthritis. Rheum Dis Clin North Am. 2007 Aug;33(3):441-70.
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Black, Indian, and Native American children are more likely to have polyarticular JIA.[11]Saurenmann RK, Rose JB, Tyrrell P, et al. Epidemiology of juvenile idiopathic arthritis in a multiethnic cohort: ethnicity as a risk factor. Arthritis Rheum. 2007 Jun;56(6):1974-84.
https://onlinelibrary.wiley.com/doi/10.1002/art.22709
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