History and exam

Key diagnostic factors

common

exposure to avian protein antigen, especially excrement

Exposure to birds and cleaning cages may cause acute symptoms.

Where onset of symptoms is insidious, the timing of exposure is often missed and the pulmonary fibrosis may be dismissed as idiopathic.

mould in work environment

Exposure to mouldy air conditioners, humidifiers, or ventilation systems, or to organic products that are mouldy such as hay, grain, wood, wood dust, or sugar cane, may precipitate acute symptoms 6 to 18 hours later.

occupational exposure to chemicals

The patient may work with diisocyanates or acid anhydrides such as epoxy resins, polyurethane foam, plastic coatings, and spray paint for vehicles.[15][16][17]​ Occupational exposure to metal-working fluid has been reported as a possible cause of HP.[18]

dyspnoea

Almost always present; where symptoms present acutely, it is typically episodic, associated with fevers, cough, and malaise.

May be insidious.

cough

Cough is almost always present; where symptoms present acutely, it may be episodic and associated with fevers, dyspnoea, and malaise.

May be insidious.

Other diagnostic factors

common

fever/chills

More common with acute presentations of HP and non-fibrotic disease.

Fever is usually low grade.

malaise

Where symptoms present acutely, it is typically episodic, associated with fevers, cough, and dyspnoea.

May be insidious.

weight loss/anorexia

Weight loss and anorexia are common with advanced disease.

bibasilar rales

Typically present during acute symptomatic episodes of HP but not present between episodes.

Bibasilar or diffuse rales are usually present in patients with ongoing disease.

diffuse rales

Bibasilar or diffuse rales are usually present in patients with ongoing disease.

clubbing

Approximately 50% of patients with advanced disease will have clubbing.

Risk factors

weak

smoking

Reduces B7 co-stimulatory molecules on macrophages, thereby reducing the macrophage contribution to the inflammation.

viral infection

Increases B7 co-stimulatory molecules on macrophages, thereby increasing the macrophage contribution to the inflammation.

exposure to avian protein antigen

High levels of exposure to antigen are typically needed.

Associated with pigeon breeder's lung, bird fancier's lung, and budgerigar fancier's disease.

exposure to mould antigen

Including Aspergillus, Alternaria, Penicillium, and Trichosporum.

High levels of exposure to antigen are typically needed.

exposure to bacterial antigen

Including thermophilic Actinomycetes, Bacillus, Pseudomonas, Acinetobacter, and Klebsiella.

exposure to diisocyanate (e.g., epoxy resin)

High levels of exposure to antigen are typically needed.

exposure to acid anhydride antigen (e.g., paint refinisher)

High levels of exposure to antigen are typically needed.

exposure to metalworking fluid

Reported to account for about one-half of all cases of occupational HP in the UK.[18]

nitrofurantoin, methotrexate, roxithromycin, and rituximab

May cause drug-induced HP.[19]

e-cigarettes

Case reports indicate a possible association between the use of electronic nicotine delivery systems (vaping) and HP.[22]

sertraline

One case report describes the clinical presentation of HP associated with sertraline.[23]

ayurvedic medicine

HP has been reported in a person who consumed ayurvedic medicine.[20]

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