While vitiligo is not life-threatening, the quality of life and self-esteem in patients with vitiligo may be severely compromised.[39]Ongenae K, Beelaert L, van Geel N, et al. Psychosocial effects of vitiligo. J Eur Acad Dermatol Venereol. 2006 Jan;20(1):1-8.
http://www.ncbi.nlm.nih.gov/pubmed/16405601?tool=bestpractice.com
[40]Ezzedine K, Eleftheriadou V, Whitton M, et al. Vitiligo. Lancet. 2015 Jul 4;386(9988):74-84.
http://www.ncbi.nlm.nih.gov/pubmed/25596811?tool=bestpractice.com
The therapeutic goal is to improve the appearance of the affected skin. This can be approached in different ways, depending on the type of vitiligo, extent of disease, and wishes of the patient.
Regardless of the chosen treatment, an assessment of the patient’s perspective should be included as part of the evaluation. An option of no treatment should be considered and discussed with the patient. Psychological or psychiatric support should be considered in all patients.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
Sun protection and camouflage advice
Patients should be advised to:[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Practice sun protection with high factor sunscreen offering UV-A and UV-B protection
Avoid cutaneous trauma where possible (e.g., physical trauma, surgical incisions, friction).
Cosmetic coverage may be an adequate choice of treatment in some patients. The strong contrast between affected and unaffected skin in people with darker pigmentation makes the disease more visible, for which make-up products can be customised to match the patient's skin tone.
Over-the-counter self-tanning products containing dihydroxyacetone may help to camouflage affected skin in patients with Fitzpatrick type I-IV skin.[43]Suga Y, Ikejima A, Matsuba S, et al. Medical pearl: DHA application for camouflaging segmental vitiligo and piebald lesions. J Am Acad Dermatol. 2002 Sep;47(3):436-8.
http://www.ncbi.nlm.nih.gov/pubmed/12196756?tool=bestpractice.com
Segmental vitiligo/limited vitiligo
Therapeutic options for this patient population include topical therapy, phototherapy, and surgery.
Topical therapies
In segmental or non-extensive/limited vitiligo, topical corticosteroids and calcineurin inhibitors are recommended as a first-line treatment.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
One Cochrane review found that topical corticosteroids are the most effective and safest treatment for localised vitiligo.[44]Whitton ME, Pinart M, Batchelor J, et al. Interventions for vitiligo. Cochrane Database Syst Rev. 2015 Feb 24;(2):CD003263.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD003263.pub5/full
http://www.ncbi.nlm.nih.gov/pubmed/25710794?tool=bestpractice.com
They work by suppressing the immune response against melanocytes, and can be used in adults and children. Topical corticosteroids have the best response on sun-exposed areas, in dark skin, and in recent lesions.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Potent corticosteroids (e.g., clobetasol, mometasone) should be tested for 3 months to evaluate the response.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
In some areas - particularly the face, genitals, axillae, and breasts - prolonged treatment with a topical corticosteroid may result in corticosteroid-induced atrophy and hypertrichosis. Therefore, patients should be evaluated regularly for adverse effects such as skin thinning, purpura, and striae distensae.[45]Westerhof W, Nieuweboer-Krobotova L, Mulder PG, et al. Left-right comparison study of the combination of fluticasone propionate and UV-A vs. either fluticasone propionate or UV-A alone for the long-term treatment of vitiligo. Arch Dermatol. 1999 Sep;135(9):1061-6.
https://jamanetwork.com/journals/jamadermatology/fullarticle/478009
http://www.ncbi.nlm.nih.gov/pubmed/10490110?tool=bestpractice.com
Therapy can be used on a discontinuous basis to provide benefit and potentially avoid adverse effects.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
One useful approach is to use topical corticosteroids twice daily for 1 week, and then no treatment for 1 week.
One systematic review and meta-analysis concluded that topical calcineurin inhibitor monotherapy is effective, particularly in children and on lesions on the face and neck.[46]Lee JH, Kwon HS, Jung HM, et al. Treatment outcomes of topical calcineurin inhibitor therapy for patients with vitiligo: a systematic review and meta-analysis. JAMA Dermatol. 2019 Aug 1;155(8):929-38.
https://www.ncbi.nlm.nih.gov/labs/pmc/articles/PMC6547091
http://www.ncbi.nlm.nih.gov/pubmed/31141108?tool=bestpractice.com
Topical tacrolimus can be used as an alternative to topical corticosteroid (particularly in patients with facial vitiligo), thereby avoiding corticosteroid-related adverse effects, or during the off-week when using corticosteroids discontinuously.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
[47]Lepe V, Moncada B, Castanedo-Cazares JP, et al. A double-blind randomized trial of 0.1% tacrolimus vs 0.05% clobetasol for the treatment of childhood vitiligo. Arch Dermatol. 2003 May;139(5):581-5.
https://jamanetwork.com/journals/jamadermatology/fullarticle/479322
http://www.ncbi.nlm.nih.gov/pubmed/12756094?tool=bestpractice.com
Phototherapy
Phototherapy devices that deliver light in the narrow-band UV-B range (peak at 308 nm) can be considered as second-line treatment in patients who do not respond to topical therapies.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
[48]Hofer A, Hassan AS, Legat FJ, et al. Optimal weekly frequency of 308-nm excimer laser treatment in vitiligo patients. Br J Dermatol. 2005 May;152(5):981-5.
http://www.ncbi.nlm.nih.gov/pubmed/15888156?tool=bestpractice.com
[49]Mavilia L, Mori M, Rossi R, et al. 308 nm monochromatic excimer light in dermatology: personal experience and review of the literature. G Ital Dermatol Venereol. 2008 Oct;143(5):329-37.
http://www.ncbi.nlm.nih.gov/pubmed/18833074?tool=bestpractice.com
Treatments are given 2 to 3 times weekly for several months. This avoids unnecessary adverse effects due to total body irradiation.
Surgery
Surgical options may be considered in areas that do not respond, especially those areas with a high cosmetic impact, if segmental vitiligo is stable.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Surgical procedures involve melanocyte transfer from a normally pigmented autologous donor site to the site of melanocyte loss. Several techniques are available to achieve this, including punch grafting, epidermal blister grafting, or ultrathin epidermal sheet grafting.
UK guidelines recommend that the disease be inactive for at least 12 months prior to surgery.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
In meta-regression analyses, successful surgical outcome (>90% repigmentation) was associated with stable segmental disease and younger patient age.[50]Ju HJ, Bae JM, Lee RW, et al. Surgical interventions for patients with vitiligo: a systematic review and meta-analysis. JAMA Dermatol. 2021 Mar 1;157(3):307-16.
http://www.ncbi.nlm.nih.gov/pubmed/33595599?tool=bestpractice.com
Surgery is relatively contraindicated in areas such as dorsum of hands.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Widespread vitiligo
Patients with extensive vitiligo may benefit from phototherapy (combined with topical or systemic therapy as necessary), systemic corticosteroids, surgery, or depigmentation therapy.
Phototherapy
Narrow-band UV-B therapy is a safe and effective treatment for widespread vitiligo and is recommended as a first-line treatment option in these patients.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
It should be continued for at least 3 months, and for up to 12 months if tolerated, to achieve maximal response.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Narrow-band UV-B therapy can be combined with topical therapies (i.e., corticosteroids or tacrolimus) or systemic (i.e., corticosteroids) therapies as necessary, which may result in improved efficacy.
Corticosteroids
Systemic corticosteroids are recommended to stabilise disease if the condition is progressing rapidly or progresses despite therapy.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
Minipulse therapy (i.e., the intermittent administration of larger doses) or alternate-day dosing has been advocated when using systemic corticosteroids.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
[51]Radakovic-Fijan S, Furnsinn-Friedl AM, Honigsmann H, et al. Oral dexamethasone pulse treatment for vitiligo. J Am Acad Dermatol. 2001 May;44(5):814-7.
http://www.ncbi.nlm.nih.gov/pubmed/11312430?tool=bestpractice.com
Surgery
Surgical options may be considered in areas that do not respond, especially those areas with a high cosmetic impact, if widespread (non-segmental) vitiligo is stable.[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Surgical procedures involve melanocyte transfer from a normally pigmented autologous donor site to the site of melanocyte loss. Several techniques are available to achieve this, including punch grafting, epidermal blister grafting, or ultrathin epidermal sheet grafting.
Guidelines recommend that the disease be inactive for at least 12 months prior to surgery, and that patients with widespread vitiligo should not have a history of Koebner's phenomenon.[6]Bergqvist C, Ezzedine K. Vitiligo: a review. Dermatology. 2020;236(6):571-92.
https://www.karger.com/Article/FullText/506103
http://www.ncbi.nlm.nih.gov/pubmed/32155629?tool=bestpractice.com
[41]Eleftheriadou V, Atkar R, Batchelor J, et al. British Association of Dermatologists guidelines for the management of people with vitiligo 2021. Br J Dermatol. 2022 Jan;186(1):18-29.
https://onlinelibrary.wiley.com/doi/10.1111/bjd.20596
http://www.ncbi.nlm.nih.gov/pubmed/34160061?tool=bestpractice.com
[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
In meta-regression analyses, successful surgical outcome (>90% repigmentation) was associated with stable segmental disease and younger patient age.[50]Ju HJ, Bae JM, Lee RW, et al. Surgical interventions for patients with vitiligo: a systematic review and meta-analysis. JAMA Dermatol. 2021 Mar 1;157(3):307-16.
http://www.ncbi.nlm.nih.gov/pubmed/33595599?tool=bestpractice.com
Surgery is relatively contraindicated in areas such as dorsum of hands.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Depigmentation therapy
Depigmentation techniques could be considered as a last option in patients with unresponsive, widespread (i.e., >50%), or highly visible recalcitrant vitiligo of face or hands.[42]Taieb A, Alomar A, Böhm M, et al; Vitiligo European Task Force (VETF); European Academy of Dermatology and Venereology (EADV); Union Européenne des Médecins Spécialistes (UEMS). Guidelines for the management of vitiligo: the European Dermatology Forum consensus. Br J Dermatol. 2013 Jan;168(1):5-19.
https://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2012.11197.x
http://www.ncbi.nlm.nih.gov/pubmed/22860621?tool=bestpractice.com
Monobenzone (the monobenzyl ether of hydroquinone) has been used to permanently depigment unaffected skin in patients with vitiligo.
Treatment induces depigmentation that usually starts at the application site, but eventually affects remote areas of the body. This may take up to 1 year and is not always permanent, although re-treatment is possible if repigmentation occurs. Depigmentation is associated with permanent photosensitivity.
Assessment of depigmentation success should be measured using percentage of repigmentation quartiles (0% to 25%, 26% to 50%, 51% to 79%, 80% to 100%) and the Vitiligo Noticeability Scale.[52]Eleftheriadou V, Hamzavi I, Pandya AG, et al. International Initiative for Outcomes (INFO) for vitiligo: workshops with patients with vitiligo on repigmentation. Br J Dermatol. 2019 Mar;180(3):574-9.
http://www.ncbi.nlm.nih.gov/pubmed/30030843?tool=bestpractice.com
Laser-assisted melanocyte removal may be considered for areas that do not respond to chemical depigmentation, or for small pigmented islands. The Q-switched ruby laser is well suited for this approach, and works much faster than chemical depigmentation.[53]Thissen M, Westerhof W. Laser treatment for further depigmentation in vitiligo. Int J Dermatol. 1997 May;36(5):386-8.
http://www.ncbi.nlm.nih.gov/pubmed/9199992?tool=bestpractice.com
[54]Njoo MD, Vodegel RM, Westerhof W. Depigmentation therapy in vitiligo universalis with topical 4-methoxyphenol and the Q-switched ruby laser. J Am Acad Dermatol. 2000 May;42(5 Pt 1):760-9.
http://www.ncbi.nlm.nih.gov/pubmed/10775851?tool=bestpractice.com