Prognosis depends on the type of lymphoma, stage of disease, treatment, and comorbidities.
Worse prognosis is indicated by the following:
B symptoms (fever, weight loss, night sweats)
Lymphadenopathy
Organomegaly
Extranodal involvement
Poor Eastern Cooperative Oncology Group (ECOG) performance status.
A sizeable proportion of patients with aggressive lymphomas are curable with modern chemotherapy. Indolent lymphomas are generally not curable.
Prognosis by NHL subtype
Diffuse large B-cell lymphoma (DLBCL)
Five-year survival rates (stage at diagnosis, National Cancer Institute Surveillance, Epidemiology, and End Results Program data 2012 to 2018):[163]National Cancer Institute: Surveillance, Epidemiology, and End Results Program. Cancer stat facts: NHL - diffuse large B-cell lymphoma (DLBCL) [internet publication].
https://seer.cancer.gov/statfacts/html/dlbcl.html
Stage I: 79.5%
Stage II: 74.6%
Stage III: 65.5%
Stage IV: 54.7%.
Follicular lymphoma
Five-year survival rates (stage at diagnosis, National Cancer Institute Surveillance, Epidemiology, and End Results Program data 2012 to 2018):[164]National Cancer Institute: Surveillance, Epidemiology, and End Results Program. Cancer stat facts: NHL - follicular lymphoma [internet publication].
https://seer.cancer.gov/statfacts/html/follicular.html
Stage I: 97%
Stage II: 90.7%
Stage III: 88.8%
Stage IV: 84.3%.
Primary CNS
Methotrexate-based chemotherapy with whole-brain radiotherapy results in 2-year survival of 40% to 70%.[165]Ferreri AJ, Abrey LE, Blay J-Y, et al. Management of primary central nervous system lymphoma: a summary statement from the 8th International Conference on Malignant Lymphoma. J Clin Oncol. 2003 Jun 15;21(12):2407-14.
http://www.ncbi.nlm.nih.gov/pubmed/12805341?tool=bestpractice.com
Primary effusion lymphoma/body cavity lymphoma
Median survival is 6 months.[166]Simonelli C, Spina M, Cinelli R, et al. Clinical features and outcome of primary effusion lymphoma in HIV-infected patients: a single-institution study. J Clin Oncol. 2003 Nov 1;21(21):3948-54.
http://www.ncbi.nlm.nih.gov/pubmed/14581418?tool=bestpractice.com
Burkitt's lymphoma
Intensive multi-agent chemotherapy regimens such as hyper-CVAD (cyclophosphamide, vincristine, doxorubicin, and dexamethasone) and CODOX-M (cyclophosphamide, doxorubicin, vincristine, methotrexate, and folinic acid)/IVAC (ifosfamide, etoposide, and cytarabine) have improved prognosis significantly.
Addition of rituximab to intensive chemotherapy regimens may improve event-free survival.[167]Ribrag V, Koscielny S, Bosq J, et al. Rituximab and dose-dense chemotherapy for adults with Burkitt's lymphoma: a randomised, controlled, open-label, phase 3 trial. Lancet. 2016 Jun 11;387(10036):2402-11.
http://www.ncbi.nlm.nih.gov/pubmed/27080498?tool=bestpractice.com
[168]Minard-Colin V, Aupérin A, Pillon M, et al. Rituximab for high-risk, mature B-cell non-Hodgkin's lymphoma in children. N Engl J Med. 2020 Jun 4;382(23):2207-19.
https://www.doi.org/10.1056/NEJMoa1915315
http://www.ncbi.nlm.nih.gov/pubmed/32492302?tool=bestpractice.com
Mantle cell lymphoma
Subcutaneous panniculitis-like peripheral T-cell lymphoma
Systemic anaplastic large cell lymphoma
Breast implant-associated anaplastic large cell lymphoma (BIA-ALCL)
Has a slow (indolent) disease course, with excellent prognosis following surgery in patients with localised disease (i.e., confined to the fibrous scar capsule) with no mass.[169]Miranda RN, Aladily TN, Prince HM, et al. Breast implant-associated anaplastic large-cell lymphoma: long-term follow-up of 60 patients. J Clin Oncol. 2014 Jan 10;32(2):114-20.
https://www.doi.org/10.1200/JCO.2013.52.7911
http://www.ncbi.nlm.nih.gov/pubmed/24323027?tool=bestpractice.com
Patients presenting with a mass or advanced-stage disease have a poorer prognosis.[169]Miranda RN, Aladily TN, Prince HM, et al. Breast implant-associated anaplastic large-cell lymphoma: long-term follow-up of 60 patients. J Clin Oncol. 2014 Jan 10;32(2):114-20.
https://www.doi.org/10.1200/JCO.2013.52.7911
http://www.ncbi.nlm.nih.gov/pubmed/24323027?tool=bestpractice.com
[170]Ferrufino-Schmidt MC, Medeiros LJ, Liu H, et al. Clinicopathologic features and prognostic impact of lymph node involvement in patients with breast implant-associated anaplastic large cell lymphoma. Am J Surg Pathol. 2018 Mar;42(3):293-305.
https://www.doi.org/10.1097/PAS.0000000000000985
http://www.ncbi.nlm.nih.gov/pubmed/29194092?tool=bestpractice.com