The lack of readily available serological tests means the worldwide prevalence of hepatitis D virus (HDV) infection is difficult to accurately ascertain. Studies suggest a wide range from 12 to 72 million people, with an estimated 10% to 15% of people with chronic hepatitis B virus (HBV) infection also having chronic HDV infection.[5]Majeed NA, Hitawala AA, Heller T, et al. Diagnosis of HDV: from virology to non-invasive markers of fibrosis. Liver Int. 2023 Aug;43(suppl 1):31-46.
https://www.doi.org/10.1111/liv.15515
http://www.ncbi.nlm.nih.gov/pubmed/36621853?tool=bestpractice.com
Around 5% of people infected with HBV (at least 12 million people) are estimated to also have HDV infection.[9]Gaeta GB, Stroffolini T, Chiaramonte M, et al. Chronic hepatitis D: a vanishing disease? An Italian multicenter study. Hepatology. 2000 Oct;32(4 pt 1):824-7.
https://www.doi.org/10.1053/jhep.2000.17711
http://www.ncbi.nlm.nih.gov/pubmed/11003629?tool=bestpractice.com
[10]Urban S, Neumann-Haefelin C, Lampertico P. Hepatitis D virus in 2021: virology, immunology and new treatment approaches for a difficult-to-treat disease. Gut. 2021 Sep;70(9):1782-94.
https://www.doi.org/10.1136/gutjnl-2020-323888
http://www.ncbi.nlm.nih.gov/pubmed/34103404?tool=bestpractice.com
These patients are at high risk of developing liver cirrhosis and hepatocellular carcinoma within a few years.[10]Urban S, Neumann-Haefelin C, Lampertico P. Hepatitis D virus in 2021: virology, immunology and new treatment approaches for a difficult-to-treat disease. Gut. 2021 Sep;70(9):1782-94.
https://www.doi.org/10.1136/gutjnl-2020-323888
http://www.ncbi.nlm.nih.gov/pubmed/34103404?tool=bestpractice.com
A systematic review and meta-analysis of HDV prevalence in the six World Health Organization (WHO) regions estimated a global prevalence of HDV infection of 4.5% (95% CI 3.6% to 5.7%) among people positive for hepatitis B surface antigen (HBsAg) and 0.16% (95% CI 0.11% to 0.25%) overall, representing 12 million HDV seropositive individuals globally (95% CI 8.7 to 18.7 million).[11]Stockdale AJ, Kreuels B, Henrion MYR, et al. The global prevalence of hepatitis D virus infection: systematic review and meta-analysis. J Hepatol. 2020 Sep;73(3):523-32.
https://www.doi.org/10.1016/j.jhep.2020.04.008
http://www.ncbi.nlm.nih.gov/pubmed/32335166?tool=bestpractice.com
The geographical distribution of HDV infection does not mirror that of HBV infection, however, particularly the relatively low prevalence of HDV infection in many Asian countries. The highest prevalence of HDV infection is seen in parts of western and mid-Africa, Mongolia, eastern Europe, and parts of the Mediterranean.[11]Stockdale AJ, Kreuels B, Henrion MYR, et al. The global prevalence of hepatitis D virus infection: systematic review and meta-analysis. J Hepatol. 2020 Sep;73(3):523-32.
https://www.doi.org/10.1016/j.jhep.2020.04.008
http://www.ncbi.nlm.nih.gov/pubmed/32335166?tool=bestpractice.com
HDV infection is uncommon in North America, northern Europe, and Japan, and confined to at-risk groups such as those with increased likelihood of sexual exposure, injection drug users, and immigrants from endemic areas.[1]European Association for the Study of the Liver. EASL clinical practice guidelines on hepatitis delta virus. J Hepatol. 2023 Aug;79(2):433-60.
https://www.doi.org/10.1016/j.jhep.2023.05.001
http://www.ncbi.nlm.nih.gov/pubmed/37364791?tool=bestpractice.com
[12]Centers for Disease Control and Prevention. Hepatitis D questions and answers for health professionals. Jul 2024 [internet publication].
https://www.cdc.gov/hepatitis/hdv/index.htm
Vaccination against HBV and immigration patterns have affected the prevalence of HDV infection.[11]Stockdale AJ, Kreuels B, Henrion MYR, et al. The global prevalence of hepatitis D virus infection: systematic review and meta-analysis. J Hepatol. 2020 Sep;73(3):523-32.
https://www.doi.org/10.1016/j.jhep.2020.04.008
http://www.ncbi.nlm.nih.gov/pubmed/32335166?tool=bestpractice.com
There are eight different genotypes of HDV, with genotype 1 being found mainly in North America, Europe, the Middle East, and north Africa; genotypes 2 and 4 in east Asia; genotype 3 in the Amazon Basin and South America; and genotypes 5, 6, 7, and 8 in west and central Africa.[3]Kamili S, Drobeniuc J, Mixson-Hayden T, et al. Delta hepatitis: toward improved diagnostics. Hepatology. 2017 Dec;66(6):1716-8.
https://www.doi.org/10.1002/hep.29564
http://www.ncbi.nlm.nih.gov/pubmed/28961326?tool=bestpractice.com
[12]Centers for Disease Control and Prevention. Hepatitis D questions and answers for health professionals. Jul 2024 [internet publication].
https://www.cdc.gov/hepatitis/hdv/index.htm