CES is a neurosurgical emergency. Patients are treated with urgent decompression of the spinal cord.[1]Todd NV, Dickson RA. Standards of care in cauda equina syndrome. Br J Neurosurg. 2016 Oct;30(5):518-22.
http://www.ncbi.nlm.nih.gov/pubmed/27240099?tool=bestpractice.com
Appropriate supportive care is provided by a multidisciplinary team.[3]Shivji F, Tsegaye M. Cauda equina syndrome: the importance of complete multidisciplinary team management. BMJ Case Rep. 2013 Mar 15;2013:bcr2012007806.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3618724
http://www.ncbi.nlm.nih.gov/pubmed/23505270?tool=bestpractice.com
Surgery
Decompression surgery should be performed as soon as possible. Although surgery within 48 hours of symptom onset has been used by some clinicians as a guide, this has been challenged, and remains controversial. It is likely that the level of neurological dysfunction at the time of surgery (rather than time since symptom onset) is the most significant determinant of prognosis.[38]Quaile A. Cauda equina syndrome-the questions. Int Orthop. 2019 Apr;43(4):957-61.
http://www.ncbi.nlm.nih.gov/pubmed/30374638?tool=bestpractice.com
[39]Chau AM, Xu LL, Pelzer NR, et al. Timing of surgical intervention in cauda equina syndrome: a systematic critical review. World Neurosurg. 2014 Mar-Apr;81(3-4):640-50.
https://www.sciencedirect.com/science/article/abs/pii/S1878875013014186?via%3Dihub
http://www.ncbi.nlm.nih.gov/pubmed/24240024?tool=bestpractice.com
[40]Epstein NE. Review/perspective: operations for cauda equina syndromes - "The sooner the better". 2022 Mar 25;13:100.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8986648
http://www.ncbi.nlm.nih.gov/pubmed/35399881?tool=bestpractice.com
One retrospective cohort study of 20,924 patients with CES reported that patients undergoing surgical decompression in hospital day 0 or 1 had better inpatient outcomes, including lower complication and mortality rates, than patients having surgery on day 2 or later.[41]Hogan WB, Kuris EO, Durand WM, et al. Timing of surgical decompression for cauda equina syndrome. World Neurosurg. 2019 Dec;132:e732-8.
http://www.ncbi.nlm.nih.gov/pubmed/31415897?tool=bestpractice.com
Evidence on the benefits of earlier surgery (e.g., within 24 hours) is equivocal.[4]Spector LR, Madigan L, Rhyne A, et al. Cauda equina syndrome. J Am Acad Orthop Surg. 2008 Aug;16(8):471-9.
http://www.ncbi.nlm.nih.gov/pubmed/18664636?tool=bestpractice.com
[38]Quaile A. Cauda equina syndrome-the questions. Int Orthop. 2019 Apr;43(4):957-61.
http://www.ncbi.nlm.nih.gov/pubmed/30374638?tool=bestpractice.com
[42]Shapiro S. Medical realities of cauda equina syndrome secondary to lumbar disc herniation. Spine (Phila Pa 1976). 2000 Feb 1;25(3):348-51.
http://www.ncbi.nlm.nih.gov/pubmed/10703108?tool=bestpractice.com
[40]Epstein NE. Review/perspective: operations for cauda equina syndromes - "The sooner the better". 2022 Mar 25;13:100.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8986648
http://www.ncbi.nlm.nih.gov/pubmed/35399881?tool=bestpractice.com
This may be due to differences in neurological dysfunction among participants; some studies suggest that surgery within 24 hours of symptom onset may reduce postoperative bladder dysfunction in patients with incomplete CES (CESI), but not in patients with CES with urinary retention (CESR), compared with surgery between 24 and 48 hours.[43]DeLong WB, Polissar N, Neradilek B. Timing of surgery in cauda equina syndrome with urinary retention: meta-analysis of observational studies. J Neurosurg Spine. 2008 Apr;8(4):305-20.
http://www.ncbi.nlm.nih.gov/pubmed/18377315?tool=bestpractice.com
[44]Srikandarajah N, Boissaud-Cooke MA, Clark S, et al. Does early surgical decompression in cauda equina syndrome improve bladder outcome? Spine (Phila Pa 1976). 2015 Apr 15;40(8):580-3.
http://www.ncbi.nlm.nih.gov/pubmed/25646751?tool=bestpractice.com
Therefore, as the 48-hour time window is controversial, urgent surgery should not be delayed, especially since the precise time of symptom onset can be difficult to define.[39]Chau AM, Xu LL, Pelzer NR, et al. Timing of surgical intervention in cauda equina syndrome: a systematic critical review. World Neurosurg. 2014 Mar-Apr;81(3-4):640-50.
https://www.sciencedirect.com/science/article/abs/pii/S1878875013014186?via%3Dihub
http://www.ncbi.nlm.nih.gov/pubmed/24240024?tool=bestpractice.com
[40]Epstein NE. Review/perspective: operations for cauda equina syndromes - "The sooner the better". 2022 Mar 25;13:100.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8986648
http://www.ncbi.nlm.nih.gov/pubmed/35399881?tool=bestpractice.com
British Association of Spine Surgeons guidelines recommend that surgery should take place as soon as possible, while taking into account the duration and clinical course of symptoms and signs, as well as the potential for increased morbidity when operating at night.[1]Todd NV, Dickson RA. Standards of care in cauda equina syndrome. Br J Neurosurg. 2016 Oct;30(5):518-22.
http://www.ncbi.nlm.nih.gov/pubmed/27240099?tool=bestpractice.com
[23]British Association of Spine Surgeons; The Society of British Neurological Surgeons. Standards of care for investigation and management of cauda equina syndrome. Dec 2018 [internet publication].
https://spinesurgeons.ac.uk/News/7773476
[24]Germon T, Ahuja S, Casey ATH, et al. British Association of Spine Surgeons standards of care for cauda equina syndrome. Spine J. 2015 Mar 2;15(3 suppl):S2-4.
http://www.ncbi.nlm.nih.gov/pubmed/25708139?tool=bestpractice.com
The goal of surgery is to alleviate compression of the cauda equina, which may be achieved through a number of surgical techniques, such as a wide-decompressive laminectomy or lumbar microdiskectomy. The appropriate surgical technique should be chosen based on pathology and the experience of the surgeon.[4]Spector LR, Madigan L, Rhyne A, et al. Cauda equina syndrome. J Am Acad Orthop Surg. 2008 Aug;16(8):471-9.
http://www.ncbi.nlm.nih.gov/pubmed/18664636?tool=bestpractice.com
Intra-operative monitoring of somatosensory and motor-evoked potentials allows for evaluation of radiculopathy and neuropathy, but is not a necessary part of urgent procedures.[45]Balzer JR, Rose RD, Welch WC, et al. Simultaneous somatosensory evoked potential and electromyographic recordings during lumbosacral decompression and instrumentation. Neurosurgery. 1998 Jun;42(6):1318-24.
http://www.ncbi.nlm.nih.gov/pubmed/9632191?tool=bestpractice.com
Outcomes after surgery tend to be worse for patients with CESR than for those with CESI. Pain, loss of perineal sensation, and bladder, bowel, and sexual dysfunction may persist, although significant recovery of function is possible.[1]Todd NV, Dickson RA. Standards of care in cauda equina syndrome. Br J Neurosurg. 2016 Oct;30(5):518-22.
http://www.ncbi.nlm.nih.gov/pubmed/27240099?tool=bestpractice.com
[4]Spector LR, Madigan L, Rhyne A, et al. Cauda equina syndrome. J Am Acad Orthop Surg. 2008 Aug;16(8):471-9.
http://www.ncbi.nlm.nih.gov/pubmed/18664636?tool=bestpractice.com
[46]Hazelwood JE, Hoeritzauer I, Pronin S, et al. An assessment of patient-reported long-term outcomes following surgery for cauda equina syndrome. Acta Neurochir (Wien). 2019 Sep;161(9):1887-94.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6704093
http://www.ncbi.nlm.nih.gov/pubmed/31263950?tool=bestpractice.com
Supportive care
A number of supportive therapies may be appropriate, depending on the patient’s circumstances.
Prevention of venous thromboembolism
All patients should be given prophylaxis to prevent venous thromboembolism and possible pulmonary embolism.[47]Gould MK, Garcia DA, Wren SM, et al. Prevention of VTE in nonorthopedic surgical patients: antithrombotic therapy and prevention of thrombosis, 9th ed: American College of Chest Physicians evidence-based clinical practice guidelines. Chest. 2012 Feb;141(2 suppl):e227S-77.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3278061
http://www.ncbi.nlm.nih.gov/pubmed/22315263?tool=bestpractice.com
Pharmacological prophylaxis should be used unless contraindicated; non-pharmacological measures (e.g., graduated compression stockings, intermittent pneumatic compression devices) may be used for patients at high risk for bleeding, especially in the preoperative phase.[48]Kahn SR, Lim W, Dunn AS, et al. Prevention of VTE in nonsurgical patients: antithrombotic therapy and prevention of thrombosis, 9th ed: American College of Chest Physicians evidence-based clinical practice guidelines. Chest. 2012 Feb;141(2 suppl):e195-226.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3278052
http://www.ncbi.nlm.nih.gov/pubmed/22315261?tool=bestpractice.com
See Venous thromboembolism (VTE) prophylaxis
Maintenance of volume and blood pressure
Treatment of autonomic dysfunction and prevention of resultant changes in blood pressure may be required, as this may contribute to further neurological impairment.
In the acute setting, treatment consists of central line placement with volume resuscitation and/or vasopressors.
Prevention of gastric stress ulcers
Prevention of stress ulceration with a proton-pump inhibitor (e.g., omeprazole) or an H2 antagonist (e.g., famotidine) is indicated for at least 4 weeks following surgery.[49]Toews I, George AT, Peter JV, et al. Interventions for preventing upper gastrointestinal bleeding in people admitted to intensive care units. Cochrane Database Syst Rev. 2018 Jun 4;(6):CD008687.
https://www.cochranelibrary.com/cdsr/doi/10.1002/14651858.CD008687.pub2/full
http://www.ncbi.nlm.nih.gov/pubmed/29862492?tool=bestpractice.com
Bladder and bowel management
Bladder and bowel function should be assessed and monitored.[32]Ginsberg DA, Boone TB, Cameron AP, et al. The AUA/SUFU guideline on adult neurogenic lower urinary tract dysfunction: diagnosis and evaluation. J Urol. 2021 Nov;206(5):1097-105.
https://www.auajournals.org/doi/10.1097/JU.0000000000002235
http://www.ncbi.nlm.nih.gov/pubmed/34495687?tool=bestpractice.com
If bladder catheterisation is needed, an intermittent catheter is preferred, as it is associated with lower rates of urinary tract infection and urethral trauma. An indwelling catheter may be used if intermittent catheterisation is not feasible.[50]Ginsberg DA, Boone TB, Cameron AP, et al. The AUA/SUFU guideline on adult neurogenic lower urinary tract dysfunction: treatment and follow-up. J Urol. 2021 Nov;206(5):1106-13.
https://www.auajournals.org/doi/10.1097/JU.0000000000002239
http://www.ncbi.nlm.nih.gov/pubmed/34495688?tool=bestpractice.com
[51]Taweel WA, Seyam R. Neurogenic bladder in spinal cord injury patients. Res Rep Urol. 2015;7:85-99.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4467746
http://www.ncbi.nlm.nih.gov/pubmed/26090342?tool=bestpractice.com
Anticholinergic medications are often part of management. Invasive procedures may be considered for ongoing problems.[50]Ginsberg DA, Boone TB, Cameron AP, et al. The AUA/SUFU guideline on adult neurogenic lower urinary tract dysfunction: treatment and follow-up. J Urol. 2021 Nov;206(5):1106-13.
https://www.auajournals.org/doi/10.1097/JU.0000000000002239
http://www.ncbi.nlm.nih.gov/pubmed/34495688?tool=bestpractice.com
A bowel programme (to help to prevent involuntary bowel movements, constipation, and impaction of the bowels), laxatives, and/or bowel evacuation may be required.[52]Emmanuel A. Neurogenic bowel dysfunction. F1000Res. 2019 Oct 28;8.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6820819
http://www.ncbi.nlm.nih.gov/pubmed/31700610?tool=bestpractice.com
Other supportive therapies
Risk assessment for pressure ulcers should be carried out. Preventive approaches include regular manual or automatic turning for patients on bed rest, encouraging patients who are not on bed rest to mobilise regularly (every few hours), and the use of pressure relieving devices. See Pressure ulcers.
Nutritional support should include isotonic feeds and evaluation of dysphagia.
Mechanically assisted ventilation or manually assisted cough may be required.