History and exam

Key diagnostic factors

common

presence of risk factors

Risk factors include positive family history, recent viral illness, and autoimmune disorders.

vertigo

Recurrent episodes of vertigo, described as a spinning sensation lasting minutes to hours. Usually associated with nausea and vomiting. Attacks tend to cluster in groups.

hearing loss

Usually fluctuating and worsens during or around the vertigo spells in initial stages.

May become constant in later stages. Usually unilateral in the affected ear.

tinnitus

Usually described as roaring tinnitus. Usually unilateral in the affected ear.

aural fullness

Occurs in the affected ear.

May increase prior to an attack.

uncommon

drop attacks

Sudden loss of balance without loss of consciousness or other autonomic or neurological symptoms.

More common in older people but can occur at any age.

Tend to occur in late stages.

Other diagnostic factors

common

positive Romberg's test

Swaying or falling when asked to stand with feet together and eyes closed.

Fukuda's stepping test

Turning towards the affected side when asked to march in place with eyes closed.

uncommon

bilateral symptoms

Autoimmune inner-ear disease is suspected in patients with bilateral meniere's disease or history of other autoimmune systemic disorders.

nystagmus

Horizontal and/or rotatory nystagmus that can be suppressed by visual fixation.

Seen in acute attacks.

tandem walk

Inability to walk (heel-to-toe) in a straight line.

Risk factors

weak

recent viral infection

Viral infection with haematogenous spread, or direct spread through the round window membrane as a result of middle-ear infection or at the time of an upper respiratory tract infection, has been implicated in meniere's disease (MD).[15]

It is thought that viral infections cause inflammation in the inner ear and subsequently trigger a reactive immune response in the vicinity of the endolymphatic sac, causing damage to its function.

Evidence of viral aetiology is supported by demonstration of the presence of human cytomegalovirus by polymerase chain reaction in the endolymphatic sac tissues; antiviral immunoglobulin E in the sera of patients with MD; elevated anti-herpes simplex virus immunoglobulin G (IgG) in the perilymph of patients with MD; and higher titres of IgG against adenovirus and varicella zoster in patients when compared with controls.[19]

genetic predisposition

There have been several reports in the literature about a genetic predisposition in meniere's disease (MD). Hereditary factors have been found to play a role in 10% to 50% of cases.[15]

The most commonly reported mode of inheritance is autosomal dominant pattern, but X-linked inheritance has also been reported.

Higher frequency of histocompatibility antigen (HLA-DR, -DQ, and -DP) has been reported in patients with MD compared with controls.[15]

autoimmune disease

Patients with associated autoimmune disorders such as vasculitis, rheumatoid arthritis, and lupus may have an autoimmune inner-ear disorder.[20] This is especially likely when meniere's disease is bilateral at initial presentation. 

increasing age

Several studies indicate that prevalence and incidence rates increase with age, up to an age threshold of approximately 80 years.[6][21]​​ meniere's disease is reported almost exclusively in adults, with peak onset occurring between aged 40 to 50 years.[8][21]

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