Criteria

Clinical severity[2][21][88][89]

Mild disease: elevated serum bile acid concentrations ≥10 micromol/L (or nonfasting, ≥19 micromol/L) and <40 micromol/L

Moderate disease: elevated serum bile acid concentrations ≥40 micromol/L and <100 micromol/L

Severe disease: elevated serum bile acid concentrations ≥100 micromol/L.

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