Occurs rarely in patients with type 3 VWD, usually in patients with large von Willebrand factor (VWF) gene deletions. May cause anaphylactic reactions to exogenous VWF. Successful treatment of bleeding with continuous infusion of high-purity factor VIII (recombinant or plasma derived) or with recombinant activated factor VII has been reported in these patients.[20]Laffan MA, Lester W, O'Donnell JS, et al. The diagnosis and management of von Willebrand disease: a United Kingdom Haemophilia Centre Doctors Organization guideline approved by the British
Committee for Standards in Haematology. Br J Haematol. 2014 Nov;167(4):453-65.
http://onlinelibrary.wiley.com/doi/10.1111/bjh.13064/full
http://www.ncbi.nlm.nih.gov/pubmed/25113304?tool=bestpractice.com
[23]Rodeghiero F, Castaman G. Treatment of von Willebrand disease. Semin Hematol. 2005;42:29-35.
http://www.ncbi.nlm.nih.gov/pubmed/15662613?tool=bestpractice.com