Atypical bacterial pathogens are a relatively common cause of lower respiratory diseases, including community-acquired pneumonia.[1]Marchello C, Dale AP, Thai TN, et al. Prevalence of atypical pathogens in patients with cough and community-acquired pneumonia: a meta-analysis. Ann Fam Med. 2016 Nov;14(6):552-66.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5389400
http://www.ncbi.nlm.nih.gov/pubmed/28376442?tool=bestpractice.com
The incidence of atypical pathogens in community-acquired pneumonia is approximately 22% globally, but this varies with location.[2]Arnold FW, Summersgill JT, Ramirez JA. Role of atypical pathogens in the etiology of community-acquired pneumonia. Semin Respir Crit Care Med. 2016 Dec;37(6):819-28.
http://www.ncbi.nlm.nih.gov/pubmed/27960206?tool=bestpractice.com
Mycoplasma pneumoniae causes up to 20% of cases of community-acquired pneumonia and has been implicated in some hospital-based epidemics. Infection is common in children and young adults, and is often seen in close community settings such as boarding schools, universities, and military bases.[3]Jain S, Williams DJ, Arnold SR, et al; CDC EPIC Study Team. Community-acquired pneumonia requiring hospitalization among US children. N Engl J Med. 2015 Feb 26;372(9):835-45.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4697461
http://www.ncbi.nlm.nih.gov/pubmed/25714161?tool=bestpractice.com
It is the most commonly detected bacteria among children aged ≥5 years hospitalized with community-acquired pneumonia.[4]Kutty PK, Jain S, Taylor TH, et al. Mycoplasma pneumoniae among children hospitalized with community-acquired pneumonia. Clin Infect Dis. 2019 Jan 1;68(1):5-12.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6552676
http://www.ncbi.nlm.nih.gov/pubmed/29788037?tool=bestpractice.com
There is a relative increase in incidence during the late summer or fall. Epidemics occur at 3- to 6-year intervals.[1]Marchello C, Dale AP, Thai TN, et al. Prevalence of atypical pathogens in patients with cough and community-acquired pneumonia: a meta-analysis. Ann Fam Med. 2016 Nov;14(6):552-66.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5389400
http://www.ncbi.nlm.nih.gov/pubmed/28376442?tool=bestpractice.com
Previous exposure is protective while smoking poses a risk for disease.[5]Waites KB, Talkington DF. Mycoplasma pneumoniae and its role as a human pathogen. Clin Microbiol Rev. 2004 Oct;17(4):697-728.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC523564
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[6]File TM. Community-acquired pneumonia. Lancet. 2003 Dec 13;362(9400):1991-2001.
http://www.ncbi.nlm.nih.gov/pubmed/14683661?tool=bestpractice.com
[7]Klement E, Talkington DF, Wasserzug O, et al. Identification of risk factors for infection in an outbreak of Mycoplasma pneumoniae respiratory tract disease. Clin Infect Dis. 2006 Nov 15;43(10):1239-45.
https://academic.oup.com/cid/article/43/10/1239/514997
http://www.ncbi.nlm.nih.gov/pubmed/17051486?tool=bestpractice.com
[8]Feikin DR, Moroney JF, Talkington DF, et al. An outbreak of acute respiratory disease caused by Mycoplasma pneumoniae and adenovirus at a federal service training academy: new implications from an old scenario. Clin Infect Dis. 1999 Dec;29(6):1545-50.
https://academic.oup.com/cid/article/29/6/1545/307995
http://www.ncbi.nlm.nih.gov/pubmed/10585810?tool=bestpractice.com
Chlamydophila pneumoniae causes 3.5% to 10.0% of cases of community-acquired pneumonia. Like Mycoplasma pneumoniae, infection occurs mainly in children and young adults and is associated with close community settings.[1]Marchello C, Dale AP, Thai TN, et al. Prevalence of atypical pathogens in patients with cough and community-acquired pneumonia: a meta-analysis. Ann Fam Med. 2016 Nov;14(6):552-66.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5389400
http://www.ncbi.nlm.nih.gov/pubmed/28376442?tool=bestpractice.com
[3]Jain S, Williams DJ, Arnold SR, et al; CDC EPIC Study Team. Community-acquired pneumonia requiring hospitalization among US children. N Engl J Med. 2015 Feb 26;372(9):835-45.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4697461
http://www.ncbi.nlm.nih.gov/pubmed/25714161?tool=bestpractice.com
[6]File TM. Community-acquired pneumonia. Lancet. 2003 Dec 13;362(9400):1991-2001.
http://www.ncbi.nlm.nih.gov/pubmed/14683661?tool=bestpractice.com
[9]File TM Jr, Tan JS. Chlamydia pneumoniae pneumonia. Semin Respir Critical Care Med. 2000;21(4):285-94.
http://www.ncbi.nlm.nih.gov/pubmed/16088739?tool=bestpractice.com
[10]Conklin L, Adjemian J, Loo J, et al. Investigation of a Chlamydia pneumoniae outbreak in a Federal correctional facility in Texas. Clin Infect Dis. 2013 Sep;57(5):639-47.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4678872
http://www.ncbi.nlm.nih.gov/pubmed/23723194?tool=bestpractice.com
A Dutch study identified Chlamydia psittaci by polymerase chain reaction (PCR) of sputum (when available) as a cause of community-acquired pneumonia in 4.8% of cases, higher than that previously reported (2.1%).[11]Spoorenberg SM, Bos WJ, van Hannen EJ, et al. Chlamydia psittaci: a relevant cause of community-acquired pneumonia in two Dutch hospitals. Neth J Med. 2016 Feb;74(2):75-81.
http://www.njmonline.nl/getpdf.php?id=1676
http://www.ncbi.nlm.nih.gov/pubmed/26951352?tool=bestpractice.com
Legionella pneumophila is responsible for a low percentage of community-acquired pneumonia cases (around 2.7%),[1]Marchello C, Dale AP, Thai TN, et al. Prevalence of atypical pathogens in patients with cough and community-acquired pneumonia: a meta-analysis. Ann Fam Med. 2016 Nov;14(6):552-66.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5389400
http://www.ncbi.nlm.nih.gov/pubmed/28376442?tool=bestpractice.com
but it is responsible for up to 16% of cases that require hospitalization. It is generally associated with exposure to a new source of aerosolized water in showers or from cooling systems, especially those used after being stagnant for a period of time, such as in schools after a summer break. Smoking, chronic lung disease, immunosuppression, and immunomodulatory drugs are known risk factors.[12]Lanternier F, Tubach F, Ravaud P, et al. Incidence and risk factors of Legionella pneumophila pneumonia during anti-tumor necrosis factor therapy: a prospective French study. Chest. 2013 Sep;144(3):990-8.
http://www.ncbi.nlm.nih.gov/pubmed/23744173?tool=bestpractice.com
It may be associated with recent travel and may have a male predilection.[6]File TM. Community-acquired pneumonia. Lancet. 2003 Dec 13;362(9400):1991-2001.
http://www.ncbi.nlm.nih.gov/pubmed/14683661?tool=bestpractice.com
[13]Arcavi L, Benowitz NL. Cigarette smoking and infection. Arch Intern Med. 2004 Nov 8;164(20):2206-16.
https://jamanetwork.com/journals/jamainternalmedicine/fullarticle/217624
http://www.ncbi.nlm.nih.gov/pubmed/15534156?tool=bestpractice.com
[14]Den Boer JW, Nijhof J, Friesema I. Risk factors for sporadic community-acquired Legionnaires' disease. A 3-year national case-control study. Public Health. 2006 Jun;120(6):566-71.
http://www.ncbi.nlm.nih.gov/pubmed/16707144?tool=bestpractice.com
[15]England AC III, Fraser DW, Plikaytis BD, et al. Sporadic legionellosis in the United States: the first thousand cases. Ann Intern Med. 1981 Feb;94(2):164-70.
http://www.ncbi.nlm.nih.gov/pubmed/7469207?tool=bestpractice.com
Viruses (including influenza, adenovirus, respiratory syncytial virus, as well as others) may cause pneumonia that can fit atypical bacterial pneumonia features in up to 25% of the community-acquired pneumonia patients.[16]von Baum H, Schweiger B, Welte T, et al; the THE CAPNETZ STUDY GROUP. How deadly is seasonal influenza associated pneumonia? The German Competence Network for Community-acquired pneumonia (CAPNETZ). Eur Respir J. 2011 May;37(5):1151-7.
https://erj.ersjournals.com/content/37/5/1151.long
http://www.ncbi.nlm.nih.gov/pubmed/20817703?tool=bestpractice.com
[17]Niederman MS. Viral community-acquired pneumonia: if we do not diagnose it and do not treat it, can it still hurt us? Chest. 2010 Oct;138(4):767-9.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7130252
http://www.ncbi.nlm.nih.gov/pubmed/20923793?tool=bestpractice.com
[18]Metlay JP, Waterer GW, Long AC, et al. Diagnosis and treatment of adults with community-acquired pneumonia: an official clinical practice guideline of the American Thoracic Society and Infectious Diseases Society of America. Am J Respir Crit Care Med. 2019 Oct 1;200(7):e45-67.
https://www.atsjournals.org/doi/full/10.1164/rccm.201908-1581ST
http://www.ncbi.nlm.nih.gov/pubmed/31573350?tool=bestpractice.com
[19]Lieberman D, Shimoni A, Shemer-Avni Y, et al. Respiratory viruses in adults with community-acquired pneumonia. Chest. 2010 Oct;138(4):811-6.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7094496
http://www.ncbi.nlm.nih.gov/pubmed/20363845?tool=bestpractice.com
Influenza was the most frequently identified virus in adults with community-acquired pneumonia in one systematic review, accounting for 9% of cases.[20]Alimi Y, Lim WS, Lansbury L, et al. Systematic review of respiratory viral pathogens identified in adults with community-acquired pneumonia in Europe. J Clin Virol. 2017 Oct;95:26-35.
http://www.ncbi.nlm.nih.gov/pubmed/28837859?tool=bestpractice.com
Coxiella burnetii accounts for approximately 1% of pneumonia cases; however, higher incidence occurs in regions where there is high exposure to aerosols originated from livestock. It is a more common cause of pneumonia in Europe and certain regions of Canada.[21]Marrie TJ. Coxiella burnetii pneumonia. Eur Respir J. 2003 Apr;21(4):713-9.
https://erj.ersjournals.com/content/21/4/713.long
http://www.ncbi.nlm.nih.gov/pubmed/12762362?tool=bestpractice.com
The specific cause of community-acquired pneumonia can vary by season, location, and age.[3]Jain S, Williams DJ, Arnold SR, et al; CDC EPIC Study Team. Community-acquired pneumonia requiring hospitalization among US children. N Engl J Med. 2015 Feb 26;372(9):835-45.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4697461
http://www.ncbi.nlm.nih.gov/pubmed/25714161?tool=bestpractice.com
[22]Gadsby NJ, Russell CD, McHugh MP, et al. Comprehensive molecular testing for respiratory pathogens in community-acquired pneumonia. Clin Infect Dis. 2016 Apr 1;62(7):817-23.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4787606
http://www.ncbi.nlm.nih.gov/pubmed/26747825?tool=bestpractice.com
[23]Jain S, Self WH, Wunderink RG, et al; CDC EPIC Study Team. Community-acquired pneumonia requiring hospitalization among US adults. N Engl J Med. 2015 Jul 30;373(5):415-27.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4728150
http://www.ncbi.nlm.nih.gov/pubmed/26172429?tool=bestpractice.com
[24]Dumke R, Schnee C, Pletz MW, et al; Capnetz Study Group. Mycoplasma pneumoniae and Chlamydia spp. infection in community-acquired pneumonia, Germany, 2011-2012. Emerg Infect Dis. 2015 Mar;21(3):426-34.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4344269
http://www.ncbi.nlm.nih.gov/pubmed/25693633?tool=bestpractice.com