Differentials

Common

Septic nongonococcal arthritis

History

acute onset, severe pain, fever, malaise; patients at risk include intravenous drug users, those with recent bacteremia, immunocompromised patients (e.g., those with HIV disease, on immunosuppressive agents, or with other immunocompromised states), patients with sickle cell disease or other hemoglobinopathies, patients with rheumatoid arthritis or those with prosthetic joints, those who have had recent arthroscopy or arthrocentesis

Exam

joint is warm and swollen, with severely limited range of motion

1st investigation
  • needle joint aspiration:

    identification and recovery of pyogenic bacteria on microscopic examination (Gram stain) of synovial fluid and culture; WBC count in synovial fluid is often >100,000/mm³ (polymorphonuclear leukocytes >75%)

    More
Other investigations
  • blood cultures:

    growth of causative organism - positive in 50% of cases[99]

  • ultrasound-guided joint aspiration:

    WBC count in synovial fluid is often >100,000/mm³ (polymorphonuclear leukocytes >75%)

  • CT-guided joint aspiration:

    WBC count in synovial fluid is often >100,000/mm³ (polymorphonuclear leukocytes >75%)

Gonococcal arthritis

History

fever, chills, malaise, involvement of predominantly lower-extremity joints (knees, ankles), urethritis

Exam

mono- or oligoarthritis, tenosynovitis (wrists, fingers, ankles, toes), pustular or vesiculopustular skin lesions

1st investigation
  • needle joint aspiration:

    identification and recovery ofNeisseria gonorrhoeae from synovial fluid (extremely uncommon); microscopic examination and culture of synovial fluid in Thayer-Martin medium

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  • blood cultures:

    recovery ofN gonorrhoeae

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  • culture of skin lesion aspirate; urethral, cervical, rectal, or oropharyngeal cultures:

    recovery ofN gonorrhoeae

  • urethral discharge Gram stain:

    gram-negative diplococci

Other investigations

    Rheumatoid arthritis

    History

    pain, swelling, and morning stiffness for at least 30-60 minutes

    Exam

    swelling and tenderness of metacarpophalangeal (MCP) and proximal interphalangeal (PIP) joints; symmetric polyarthritis of small and large joints; rheumatoid nodules; later characteristic deformities include subluxations at wrist and MCP joints, ulnar deviation of fingers, swan-neck and boutonniere deformities of fingers, Z-deformities of thumbs

    1st investigation
    • serum rheumatoid factor (RF):

      positive

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    • serum antibodies to cyclic citrullinated peptides (CCP):

      positive

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    • ESR:

      elevated in untreated cases

    • serum CRP:

      elevated in untreated cases

    • hand x-ray:

      soft tissue swelling, periarticular osteopenia, joint space narrowing, erosions of cartilage and bone around metacarpophalangeal (MCP) and proximal interphalangeal (PIP) joints

      More
    Other investigations
    • ultrasound scan:

      synovial proliferation; joint effusion; joint erosion; increased power Doppler signal (increased vascularity in synovitis)[92][102]

    • hand MRI scan:

      bone edema; synovial enhancement; bone erosion

    • multibiomarker disease activity (MBDA) score:

      predicts radiographic joint damage at baseline and during disease course; low disease activity (<30), moderate disease activity (30-44), and high disease activity (>44)[103][104]

    Gout

    History

    typically an obese, hypertensive man age between 30 and 50 years, may have history of frequent alcohol consumption

    Exam

    redness, warmth, swelling, and exquisite tenderness of the affected joint(s)

    1st investigation
    • compensated polarized light microscopy of synovial fluid:

      negatively birefringent, needle-shaped intra- and extracellular monosodium urate (MSU) crystals

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    • serum urate:

      >360 micromol/L (6 mg/dL)

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    • x-ray of hand, foot:

      bone erosions may be subtle; characteristic overhanging edges

    Other investigations
    • ultrasound scan:

      synovial proliferation; joint effusion; joint erosion; increased power Doppler signal (increased vascularity in synovitis); characteristic "double contour" sign, indicating chronic urate frosting on the surface of articular cartilage; intra-articular and extra-articular (tendons, ligaments, and soft tissues) tophi ("wet sugar clumps" or "snow storm" appearance)[108][109][110]

    • dual energy CT (DECT) scan:

      distinct attenuation of MSU deposits color-coded in green[108][111]

    Pseudogout

    History

    acute onset; mono- or oligoarthralgia; may be preceded by trauma, surgery, intercurrent illness

    Exam

    knee most often affected; also wrists, metacarpophalangeal joints, shoulders, elbows; joints are warm, swollen, often with effusions

    1st investigation
    • needle joint aspiration:

      WBC 15,000-30,000/mm³, 90% neutrophils

    • compensated polarized light microscopy of synovial fluid:

      weakly positively birefringent crystals of calcium pyrophosphate dihydrate (CPPD), crystals phagocytosed within polymorphonuclear leukocytes

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    • x-ray of joint:

      chondrocalcinosis (calcification in fibrocartilage and hyaline cartilage)

      More
    Other investigations
    • ultrasound scan:

      synovial proliferation; joint effusion; joint erosion; increased power Doppler signal (increased vascularity in synovitis); characteristic "pseudo double contour" sign, indicating chronic calcium pyrophosphate deposition within the substance of the articular cartilage; hyperechoic sparkling spots within articular fibrocartilage or mobile intra-articular hyperechoic deposits also suggest calcium pyrophosphate dihydrate crystal deposition disease[112]

    Psoriatic arthritis

    History

    joint pain and swelling, morning stiffness lasting >30 minutes

    Exam

    asymmetric small and/or large joint oligo- or polyarthritis (clinical synovitis), nail pitting, and hyperkeratosis, onycholysis

    1st investigation
    • x-ray of hand, foot:

      acro-osteolysis, fluffy periostitis, and new bone formation at the site of entheses; gross destruction of isolated joints, pencil-in-cup appearance (arthritis mutilans), both joint lysis and ankylosis[113]

    Other investigations
    • ultrasound scan:

      proliferative synovitis shows as joint space widening with clusters of soft echoes (bushy and villous appearance) and/or homogeneous synovial thickening; bone erosion shows as intra-articular discontinuity of the bone surface visible in two perpendicular planes[113][114][115]

    • MRI:

      subchondral bone edema is characteristically observed[113]

      More

    Uncommon

    Indolent infections

    History

    chronic infection, joint pain and swelling

    Exam

    joint swelling and tenderness, usually monoarthropathy

    1st investigation
    • joint aspiration:

      may show acid-fast bacillus with special preparation and stains, fungal elements

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    • blood culture:

      growth of causative organism

    Other investigations
    • synovial biopsy:

      identification of organism (on special stains and culture); caseating or noncaseating granulomas may be seen

    Parvoviral syndrome

    History

    acute onset, pain in multiple joints, flu-like prodrome, rash

    Exam

    arthralgia in symmetric rheumatoid arthritis-like distribution, erythematous macular rash

    1st investigation
    • serum IgM and IgG antibodies:

      positive

      More
    Other investigations
    • qualitative polymerase chain reaction testing:

      Additional testing may include detection of viral nucleic acid (parvovirus B19 DNA) in blood by qualitative polymerase chain reaction (PCR) testing[100]

      More

    Lyme disease

    History

    intermittent knee pain and swelling, antecedent tick bite, rash

    Exam

    bull's-eye rash (erythema migrans), central clearing, vesicles; monoarthritis involving knee, shoulder, ankle, elbow, temporomandibular joint, wrist

    1st investigation
    • sensitive enzyme immunoassay or immunofluorescence assay:

      positive for Borrelia antibodies. A positive result should be confirmed by a Western blot immunoassay or a second sensitive enzyme immunoassay[84]

    Other investigations
    • Western blot testing for Borrelia burgdorferi:

      positive (confirmatory)

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    Juvenile idiopathic arthritis (oligo-articular type)

    History

    more likely to be female, joint pain >6 weeks' duration, seen in childhood

    Exam

    ≤4 joints, rash, enthesitis, uveitis

    1st investigation
    • CBC:

      normal or reduced hemoglobin and elevated platelets

    • ESR:

      normal or elevated

    • CRP:

      normal or elevated

    • serum antinuclear antibodies (ANA):

      positive or negative

    Other investigations
    • x-ray of affected joint:

      soft-tissue swelling; joint-space narrowing or erosions

    Acute rheumatic fever (ARF)

    History

    latent period following sore throat; adult or child; joints affected serially in quick succession

    Exam

    joint pain and swelling; knees and ankles are usually involved first; subcutaneous nodules, rash (erythema marginatum)

    1st investigation
    • throat culture for group A beta-hemolytic streptococci or rapid streptococcal antigen test:

      positive for group A beta-hemolyticStreptococcus

    • serum antistreptolysin O (ASO):

      elevated or rising titer

      More
    • x-ray of chest:

      cardiomegaly

    Other investigations
    • ECG:

      heart block, prolonged PR interval

    • echocardiography:

      cardiomegaly[78]

    • serum anti-DNAse B, antistreptokinase, and antihyaluronidase:

      positive

    Sarcoidosis

    History

    joint pain in knees or ankles

    Exam

    warm, swollen, and tender joints; tendinitis, enthesopathy (inflammation of the entheses, the location where a bone has an insertion to a tendon or a ligament), dactylitis (sausage digit); erythema nodosum

    1st investigation
    • serum ACE:

      level elevated

    • x-ray of chest:

      bilateral hilar adenopathy, right paratracheal adenopathy, pulmonary reticular opacities

      More
    Other investigations
    • PET scan:

      may reveal occult sarcoid lesions

    • synovial biopsy:

      may be nonspecific, or show typical sarcoid granulomata

    Spondyloarthropathy

    History

    back pain, associated enteropathy, more common in males, onset is typically in late teens to early 20s

    Exam

    asymmetric joint tenderness and swelling in lower extremities; uveitis

    1st investigation
    • x-ray of pelvis:

      sacroiliac joint irregularity (especially lower part), widening, erosions, and ankylosis at a later stage

    Other investigations
    • MRI scan of pelvis:

      evidence of sacroiliitis (bone edema, erosions)[105]

    Systemic lupus erythematosus (SLE)

    History

    commonly females (typical onset at age 20-30 years); polyarthralgia, with minimal swelling

    Exam

    moderate tenderness and stiffness with joint manipulation, malar rash, discoid rash, alopecia, oral ulcers

    1st investigation
    • antinuclear antibodies (ANA):

      ≥1:160 dilution

      More
    • antibodies to double-stranded DNA:

      positive

      More
    • anti-Smith (Sm) antibodies:

      positive

      More
    Other investigations
    • x-ray of hand:

      ulnar deviation of the MCP joints, swan neck deformities, but no erosions (Jaccoud arthropathy)

    • urinalysis:

      presence of blood and protein (in lupus nephritis)

    • urine microscopy:

      RBC or mixed casts, dysmorphic RBCs (in lupus nephritis)

    Adult-onset Still disease (AOSD)

    History

    daily fever ≥102°F (≥39°C); sore throat, joint pain and swelling

    Exam

    nonpruritic, macular or maculopapular truncal rash of salmon pink color with Koebner phenomenon; pericardial rub

    1st investigation
    • CBC with differential:

      WBC ≥10,000/mm³, with at least 80% neutrophils; thrombocytosis, anemia

    • serum albumin:

      hypoalbuminemia

    • serum hepatic enzymes:

      often there is elevation in aspartate and alanine aminotransferase and lactate dehydrogenase

    • serum ferritin:

      >3000 nanograms/mL (normal 40-200 nanograms/mL)

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    • x-ray of wrist:

      nonerosive narrowing of carpometacarpal and intercarpal joint spaces of wrist

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    • x-ray of chest:

      pleural effusion and/or transient pulmonary infiltrate

      More
    Other investigations
    • bone marrow biopsy:

      numerous, well-differentiated macrophages (histiocytes) that are involved in phagocytosis of hematopoietic elements

      More

    Reactive arthritis

    History

    lag period between infection and onset of arthralgia; dysuria, pelvic pain

    Exam

    asymmetric mono- or oligoarthritis, most commonly in lower extremities; dactylitis, conjunctivitis, anterior uveitis, oral ulcers, keratoderma blennorrhagica, circinate balanitis

    1st investigation
    • urine screen for Chlamydia:

      may be positive

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    • stool cultures for enteric microbes:

      may grow causative organism

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    • serology for etiologic organism:

      Yersinia,Salmonella,Campylobacter, andChlamydia cause strong antibody responses

    Other investigations
    • HLA-B27 testing:

      positive

      More

    Ankylosing spondylitis (AS)

    History

    low back pain for >3 months, stiffness, improves with exercise but not with rest

    Exam

    groin pain (indicating hip arthritis), shoulder pain and shoulder stiffness, sacroiliac (SI) tenderness with limited range of motion and pain on movement; SI joint pain with flexion, abduction, and external rotation of the corresponding hip joint (Patrick test)

    1st investigation
    • HLA-B27 testing:

      positive

      More
    • x-ray of sacroiliac (SI) joint:

      SI joint irregularity, widening, erosions, sclerosis; ankylosis in advanced disease, with complete obliteration of SI joint space

    • x-ray of lumbar, thoracic, and cervical spine:

      squaring of vertebral bodies, bridging syndesmophytes, ankylosis of facet joints and calcification of anterior longitudinal ligament, anterior atlantoaxial (C1-C2) subluxation

    Other investigations
    • MRI of sacroiliac (SI) joint:

      increased T2-weighted signal from bone and bone marrow adjacent to SI joint (bone marrow edema)

      More

    Osteoarthritis

    History

    joint pain, age commonly >50 years, obesity, minimal morning stiffness (gelling phenomenon)

    Exam

    PIP, DIP, first CMC joint, hip, and knee tenderness; limited range of motion, misalignment of joints

    1st investigation
    • CRP:

      normal

    • ESR:

      normal

    • x-ray of affected joint:

      joint-space narrowing, new bone formation (osteophytes), subchondral sclerosis, cysts; in erosive osteoarthritis: erosions, gull-wing deformity; saw-tooth deformity; ankylosis

    Other investigations

      Trauma

      History

      prior trauma, joint pain and swelling

      Exam

      joint swelling, ecchymosis, tenderness with manipulation of extremity, restricted and painful range of motion

      1st investigation
      • x-ray of affected joint:

        fracture through joint line, subluxation, soft-tissue swelling

      • needle aspiration of joint:

        hemorrhagic effusion (red, pink, or brown)

      • MRI of affected joint:

        may demonstrate cartilage injury, ligament rupture

      Other investigations
      • aspiration of joint:

        lipohemarthrosis (presence of lipid globules and blood)

      • CT of affected joint:

        may show bony and/or soft-tissue injury

      • MRI of affected joint:

        may show bony and/or soft-tissue injury; better visualization of soft tissues than CT

      Nontraumatic hemarthrosis

      History

      joint pain; may be history of underlying bleeding disorder, sickle cell anemia, pigmented villonodular synovitis, synovioma, ruptured aneurysm, AV fistula, hemangioma, Charcot joint, anticoagulant therapy, scurvy

      Exam

      swollen, warm, very painful joint; restricted and painful range of motion

      1st investigation
      • needle aspiration of joint:

        hemorrhagic effusion (red, pink, or brown)

      Other investigations
      • arthroscopy and synovial biopsy:

        intra-articular abnormality

        More

      Hypertrophic osteoarthropathy

      History

      painful and swollen joints (wrists, ankles, knees), distal long bone pain

      Exam

      clubbing, roughening of skin, swollen joints, pachydermoperiostosis

      1st investigation
      • CBC:

        may show anemia

      • x-ray of affected joint:

        periosteal reaction; hypervascularization of digits

      Other investigations
      • isotope bone scan:

        increased uptake in areas of periosteal reaction

      Intra-articular metastatic cancer

      History

      joint pain and swelling >6 weeks, known malignancy

      Exam

      joint swelling, warmth, and tenderness; typically monoarthritis

      1st investigation
      • joint fluid cytology:

        positive

      Other investigations
      • synovial biopsy:

        pathology of underlying malignancy

      Synovial sarcoma

      History

      age 30-40 years, joint pain and swelling

      Exam

      joint swelling in lower extremities

      1st investigation
      • joint fluid cytology:

        positive

      Other investigations
      • synovial biopsy:

        synovial sarcoma

      Arbovirus infections (e.g., chikungunya)

      History

      history of travel to endemic areas; fever, rash, myalgias, headache, and arthralgias 2-10 days after mosquito bite (typicallyAedes albopictus)

      Exam

      fever and rash at early stage; arthritis resembling rheumatoid arthritis involving small joints of hands, feet, wrists, and ankles

      1st investigation
      • viral culture:

        positive

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      • reverse transcriptase (RT)-PCR to detect viral RNA:

        positive

        More
      Other investigations
      • antibody tests:

        positive

        More

      Inflammatory bowel disease (ulcerative colitis and Crohn disease)

      History

      abdominal pain, bloody diarrhea, tenesmus, mucus in stool, peripheral large joint oligoarthritis, inflammatory back pain (sacroiliitis) may be present, enthesitis, dactylitis

      Exam

      pallor, abdominal tenderness and distension, perianal and abdominal wall fistulas; peripheral large joint clinical synovitis (knees, ankles); clinical evidence of sacroiliitis joint pain, enthesitis, dactylitis

      1st investigation
      • colonic biopsy and/or small bowel biopsy:

        continuous distal disease, mucin depletion, basal plasmacytosis, diffuse mucosal atrophy, absence of granulomata, and anal sparing (ulcerative colitis); mucosal bowel biopsies demonstrate transmural involvement with noncaseating granulomas (Crohn disease)

      Other investigations
      • ESR:

        elevated

      • CRP:

        elevated

      • CBC:

        reduced hemoglobin and elevated platelets

      • stool studies:

        fecal RBCs and leukocytes; elevated fecal calprotectin

      Celiac disease

      History

      weight loss, fatigue, bloating, failure to thrive, diarrhea, fatty stools, blistering itchy rash

      Exam

      low BMI, pallor, abdominal distension; blistering rash over elbows, knees, sacral area, and buttocks (dermatitis herpetiformis)

      1st investigation
      • serum anti-transglutaminase, anti-endomysial, and anti-gliadin antibodies:

        positive

      Other investigations
      • small bowel (duodenal) biopsy:

        subtotal villous atrophy, reversible with gluten-free diet

        More

      Whipple disease

      History

      arthralgias, oligo- or polyarthritis, hyperpigmentation, weight loss, abdominal pain, fatigue, bloating, failure to thrive, diarrhea, neurologic manifestations

      Exam

      low BMI, pallor, abdominal distension, hyperpigmentation, lymphadenopathy, joint tenderness with or without frank clinical synovitis in multiple joints

      1st investigation
      • upper endoscopy with duodenal biopsy:

        duodenal mucosa may appear macroscopically pale yellow with clumsy and dilated villi and ectatic lymph vessels

        More
      Other investigations
      • Tropheryma whipplei PCR on blood:

        positive

      Bowel-associated dermatosis arthritis syndrome

      History

      prior history of a gastric or intestinal bypass procedure (e.g., roux-en-Y gastric bypass, jejuno-ileal bypass, bilio-pancreatic diversion, or Billroth II gastrectomy); polyarthralgia/joint swelling, fever[116][117]

      Exam

      clinical synovitis of small and large joints (symmetric or asymmetric); tenosynovitis may also occur; skin lesions may develop (ulcerating lesions and pustules on the trunk and extremities)[116][117] 

      1st investigation
      • ESR and CRP:

        elevated

      • rheumatoid factor (RF) and antinuclear antibodies (ANA):

        usually negative

      Other investigations
      • x-rays:

        may rarely show erosive arthritis

      • skin biopsy:

        evidence of neutrophilic dermatosis

      • synovial fluid analysis:

        mild to moderate inflammation (with lymphocyte or neutrophil predominance)

      Synovitis, acne, pustulosis, hyperostosis, and osteitis (SAPHO) syndrome

      History

      presents with joint pain and swelling; back pain; palmoplantar pustulosis; acne

      Exam

      sternoclavicular joint swelling, redness, tenderness; palmoplantar pustulosis; acne

      1st investigation
      • radiography:

        suggestive

        More
      Other investigations
      • isotope bone scan:

        positive

        More
      • MRI:

        positive

        More

      Drug-induced

      History

      history of exposure to relevant drugs: procainamide, hydralazine, minocycline, isoniazid, tumor necrosis factor inhibitors, etc. (drug-induced lupus); various oral and parenteral pharmacologic agents, including plasma-derived products and biologics (serum sickness-like reaction); aromatase inhibitors, clopidogrel, quinolone antibiotics, statins, and dipeptidyl peptidase (DPP)-4 inhibitors (arthralgia, inflammatory arthritis, and tendinitis); immune checkpoint inhibitors (inflammatory arthritis and tenosynovitis)

      Exam

      rash, fever, urticaria (serum sickness); other features of lupus (if drug-induced lupus); tendinitis and tendon rupture (quinolone antibiotics); inflammatory arthritis and tenosynovitis (immune checkpoint inhibitors)

      1st investigation
      • ANA:

        positive in drug-induced lupus

      • antihistone antibodies:

        positive in drug-induced lupus

      • double-stranded DNA:

        negative

        More
      Other investigations

        Remitting seronegative symmetrical synovitis with pitting edema (RS3PE) syndrome

        History

        acute-onset polyarthritis; males ≥50 years of age

        Exam

        clinical synovitis; significant pitting edema of the dorsal surface of hands and feet

        1st investigation
        • ESR:

          elevated

        • CRP:

          elevated

        • serum rheumatoid factor (RF):

          negative

        Other investigations
        • x-ray of affected joint:

          usually no erosions

        Ebola virus

        History

        history of residence in or travel to an Ebola-endemic area in the 21 days before onset of illness; secondary exposure (human-to-human or primate-to-human exposure)

        Exam

        fever, pharyngitis, myalgia, severe headache, abdominal pain, vomiting, diarrhea, or unexplained bleeding or bruising; maculopapular rash on trunk (may be present around day 5 of infection); bilateral conjunctival infection; bleeding from intravenous puncture sites and mucous membranes

        1st investigation
        • reverse transcriptase (RT)- PCR to detect viral DNA:

          positive

        Other investigations
        • antigen-capture enzyme-linked immunosorbent assay (ELISA):

          positive for Ebola virus RNA

          More
        • CBC:

          thrombocytopenia; marked lymphopenia; decreased hemoglobin (if bleeding manifestations)

        • IgM and IgG antibodies:

          positive

        Diffuse tenosynovial giant cell tumor (formerly, diffuse pigmented villonodular synovitis)

        History

        twice as common in males; age 20-50 years; sudden onset; entire synovium affected; typically occurs in large joints such as the knee (80% of cases) or hip

        Exam

        unexplained joint swelling (effusion), pain, warmth, and tenderness; decreased motion; increased pain and locking of the joint occur with disease progression

        1st investigation
        • MRI scan:

          nodular intra-articular masses that demonstrate low signal intensity on T1-, T2-, and proton-density sequences

        Other investigations
        • plain x-ray:

          detects calcifications

        • CT:

          hyperdense soft-tissue mass in the joint or tendon sheath

        • histopathology:

          nodules and/or villi with abundant (pigmented) hemosiderin-laden macrophages

        Localized tenosynovial giant cell tumor (formerly, localized pigmented villonodular synovitis)

        History

        predominantly occurs in females; age 20-50 years; sudden onset; typically occurs in small joints such as the hands and feet

        Exam

        slow-growing mass; painless, becoming symptomatic

        1st investigation
        • MRI scan:

          nodular intra-articular masses that demonstrate low signal intensity on T1-, T2-, and proton-density sequences

        Other investigations
        • plain x-ray:

          detects calcifications

        • CT:

          hyperdense soft-tissue mass in the joint or tendon sheath

        • histopathology:

          nodules and/or villi with abundant (pigmented) hemosiderin-laden macrophages

        Synovial osteochondromatosis

        History

        chronic, progressive pain; swelling of the affected joint exacerbated by physical activity; locking of the affected joint can occur

        Exam

        joint effusion; tenderness; limited range of motion; clicking, grating, or locking (due to intra-articular bodies within the affected joint); grinding and popping; osteochondral nodules (close to the skin) in knee, ankle, or elbow

        1st investigation
        • CT scan with radiography:

          multiple, smooth, oval-shaped calcified masses within the joint space or bursa

        Other investigations
        • histopathology:

          cartilaginous bodies or osteocartilaginous bodies with central ossification, typically spherical

        Amyloid arthropathy

        History

        commonly presents as shoulder pain or carpal tunnel syndrome

        Exam

        juxta-articular soft-tissue swelling; osteolytic bone lesions (amyloidomas); symptoms commonly bilateral

        1st investigation
        • synovial biopsy and synovial fluid analysis:

          positive on Congo red staining

        Other investigations
        • x-ray:

          demonstrates erosive and destructive arthropathy; osteolytic bone lesions (amyloidomas)

        • MRI:

          extensive deposition of an abnormal soft tissue that has low or intermediate signal intensity on T1- and T2-weighted images

        Fibroblastic rheumatism

        History

        relatively acute onset; appearance of cutaneous nodules, flexion contractures, and polyarthritis[118][119]

        Exam

        multiple erythematous cutaneous nodules; multiple joint swelling, tenderness, and flexion contractures

        1st investigation
        • skin and synovial biopsy:

          fibroblastic proliferation associated with a collagenous stroma

        Other investigations
        • x-ray of small joints of hands and feet:

          demonstrates an erosive arthropathy

        Multicentric reticulohistiocytosis (MRH)

        History

        progressive painful and deforming arthropathy of hands and feet and more proximal joints; multiple skin nodules[118]

        Exam

        tender and swollen MCP, PIP, and DIP joints; multiple firm reddish-brown papules and nodules over the dorsum of the hands and in the fingers, with the classical “coral beads” appearance around the nailbeds

        1st investigation
          Other investigations
          • skin and synovial biopsy:

            biopsy of cutaneous nodules shows mononuclear histiocytes and multinucleated giant cells 50–100 mm in diameter, with eosinophilic, periodic acid-Schiff (PAS) positive cytoplasm, that has a fine granular appearance

          • x-ray of small joints of hands and feet:

            demonstrates a severe erosive arthropathy affecting wrists, MCP, PIP, and DIP joints

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