Epidemiologic data for various forms of epilepsy can be quite difficult to ascertain due to variability in epilepsy classification and the age range of the population studied. It has been estimated, based on prior epidemiologic studies, that 4000 children (younger than 18 years) are diagnosed with absence epilepsy and 1500 children with juvenile myoclonic epilepsy (JME) annually in the US.[9]Hauser WA. The prevalence and incidence of convulsive disorders in children. Epilepsia. 1994;35(suppl 2):S1-6.
http://www.ncbi.nlm.nih.gov/pubmed/8275976?tool=bestpractice.com
Subsequent studies based on the newer classification of epilepsy syndromes find the following:
Childhood absence epilepsy (CAE):[2]Wylie E, ed. The treatment of epilepsy: principles & practice. Philadelphia, PA: Lippincott Williams & Wilkins; 2006:305-32, 391-440.[10]Joensen P. Prevalence, incidence, and classification of epilepsy in the Faroes. Acta Neurol Scand. 1986 Aug;74(2):150-5.
http://www.ncbi.nlm.nih.gov/pubmed/3776461?tool=bestpractice.com
[11]Blom S, Heijbel J, Bergfors PG. Incidence of epilepsy in children: a follow-up study three years after the first seizure. Epilepsia. 1978 Aug;19(4):343-50.
http://www.ncbi.nlm.nih.gov/pubmed/100316?tool=bestpractice.com
[12]Sidenvall R, Forsgren L, Blomquist HK, et al. A community-based prospective incidence study of epileptic seizures in children. Acta Paediatr. 1993 Jan;82(1):60-5.
http://www.ncbi.nlm.nih.gov/pubmed/8453224?tool=bestpractice.com
[13]Granieri E, Rosati G, Tola R, et al. A descriptive study of epilepsy in the district of Copparo, Italy, 1964-1978. Epilepsia. 1983 Aug;24(4):502-14.
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[14]Waaler PE, Blom BH, Skeidsvoll H, et al. Prevalence, classification, and severity of epilepsy in children in western Norway. Epilepsia. 2000 Jul;41(7):802-10.
http://www.ncbi.nlm.nih.gov/pubmed/10897150?tool=bestpractice.com
Incidence reported varies from of 0.7 to 8 per 100,000 in the general population
Prevalence of 0.1 to 0.7 per 1000 persons
Age: the highest prevalence is in patients aged 2 to 9 years
Sex: in general the male-to-female ratio for CAE averages 1:2 to 1:5.
Juvenile absence epilepsy (JAE):[2]Wylie E, ed. The treatment of epilepsy: principles & practice. Philadelphia, PA: Lippincott Williams & Wilkins; 2006:305-32, 391-440.[12]Sidenvall R, Forsgren L, Blomquist HK, et al. A community-based prospective incidence study of epileptic seizures in children. Acta Paediatr. 1993 Jan;82(1):60-5.
http://www.ncbi.nlm.nih.gov/pubmed/8453224?tool=bestpractice.com
Fewer data on JAE are available
Estimated prevalence of 0.1 per 100,000 persons in the general population
Age: onset averages at 10 to 17 years.
Juvenile myoclonic epilepsy (JME):[10]Joensen P. Prevalence, incidence, and classification of epilepsy in the Faroes. Acta Neurol Scand. 1986 Aug;74(2):150-5.
http://www.ncbi.nlm.nih.gov/pubmed/3776461?tool=bestpractice.com
[12]Sidenvall R, Forsgren L, Blomquist HK, et al. A community-based prospective incidence study of epileptic seizures in children. Acta Paediatr. 1993 Jan;82(1):60-5.
http://www.ncbi.nlm.nih.gov/pubmed/8453224?tool=bestpractice.com
[15]Loiseau J, Loiseau P, Guyot M, et al. Survey of seizure disorders in the French southwest. I. Incidence of epileptic syndromes. Epilepsia. 1990 Jul-Aug;31(4):391-6.
http://www.ncbi.nlm.nih.gov/pubmed/2369875?tool=bestpractice.com
[16]Delgado-Escueta AV, Enrile-Bacsal F. Juvenile myoclonic epilepsy of Janz. Neurology. 1984 Mar;34(3):285-94.
http://www.ncbi.nlm.nih.gov/pubmed/6422321?tool=bestpractice.com
[17]Mullins GM, O'Sullivan SS, Neligan A, et al. A study of idiopathic generalised epilepsy in an Irish population. Seizure. 2007 Apr;16(3):204-10.
http://www.ncbi.nlm.nih.gov/pubmed/17223580?tool=bestpractice.com
[18]Jallon P, Latour P. Epidemiology of idiopathic generalized epilepsies. Epilepsia. 2005 Nov 18;46(suppl 9):10-4.
https://onlinelibrary.wiley.com/doi/full/10.1111/j.1528-1167.2005.00309.x
http://www.ncbi.nlm.nih.gov/pubmed/16302871?tool=bestpractice.com
Incidence is approximately 1 per 100,000
Prevalence ranges from 0.1 to 0.2 per 1000
Age: onset peaks between ages 12 to 18 years
Sex: a female predominance in JME has been reported
JME appears to be less frequent in developing countries.
Lennox-Gastaut syndrome:[8]Bureau M, Tassinari CA. Epilepsy with myoclonic absences. Brain Dev. 2005 Apr;27(3):178-84.
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[19]Rantala H, Putkonen T. Occurrence, outcome, and prognostic factors of infantile spasms and Lennox-Gastaut syndrome. Epilepsia. 1999 Mar;40(3):286-9.
http://www.ncbi.nlm.nih.gov/pubmed/10080506?tool=bestpractice.com
[20]Trevathan E, Murphy CC, Yeargin-Allsopp M. Prevalence and descriptive epidemiology of Lennox-Gastaut syndrome among Atlanta children. Epilepsia. 1997 Dec;38(12):1283-8.
http://www.ncbi.nlm.nih.gov/pubmed/9578523?tool=bestpractice.com
Incidence in children younger than 15 years has been estimated at 1.93 per 100,000
Lifetime prevalence at age 10 years has been estimated at 0.26 per 1000
Sex: a slightly higher frequency in males over females has been reported.
Epilepsy with myoclonic absences:[8]Bureau M, Tassinari CA. Epilepsy with myoclonic absences. Brain Dev. 2005 Apr;27(3):178-84.
http://www.ncbi.nlm.nih.gov/pubmed/15737698?tool=bestpractice.com
[21]Durá-Travé T, Yoldi-Petri ME, Gallinas-Victoriano F. Incidence of epilepsies and epileptic syndromes among children in Navarre, Spain: 2002 through 2005. J Child Neurol. 2008 Aug;23(8):878-82.
http://www.ncbi.nlm.nih.gov/pubmed/18660472?tool=bestpractice.com
Minimal data are available on the incidence
Epilepsy with absences accounted for 0.5% to 1% of all epilepsies observed at Centre Saint-Paul in Marseille, France, with a 70% male preponderance
Incidence of epilepsy with myoclonic absences was reported to be 2.6% in a selected population of children (ages <15 years) with newly diagnosed epilepsy in Navarre, Spain.