The exact prevalence of medullary sponge kidney (MSK) in the general population is unknown. Most patients remain asymptomatic, and the condition can be an incidental finding on radiologic investigations for other reasons.[3]Imam TH, Patail H, Patail H. Medullary sponge kidney: current perspectives. Int J Nephrol Renovasc Dis. 2019;12:213-8.
https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-fulltext-article-IJNRD
http://www.ncbi.nlm.nih.gov/pubmed/31576161?tool=bestpractice.com
One study estimated the prevalence to be 5 per 100,000 population.[8]Mayall GF. The incidence of medullary sponge kidney. Clin Radiol. 1970 Apr;21(2):171-4.
http://www.ncbi.nlm.nih.gov/pubmed/5420265?tool=bestpractice.com
In patients examined with intravenous urography (IVU), the prevalence was estimated to be about 0.5% to 1%.[9]Palubinskas AJ. Medullary sponge kidney. Radiology. 1961 Jun;76:911-9.
http://www.ncbi.nlm.nih.gov/pubmed/13732350?tool=bestpractice.com
Other studies have estimated the prevalence to be about 3% to 5% in patients who are renal stone formers, although higher estimates (up to 20%) have been reported.[3]Imam TH, Patail H, Patail H. Medullary sponge kidney: current perspectives. Int J Nephrol Renovasc Dis. 2019;12:213-8.
https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-fulltext-article-IJNRD
http://www.ncbi.nlm.nih.gov/pubmed/31576161?tool=bestpractice.com
[10]Gambaro G, Feltrin GP, Lupo A, et al. Medullary sponge kidney (Lenarduzzi-Cacchi-Ricci disease): a Padua Medical School discovery in the 1930s. Kidney Int. 2006 Feb;69(4):663-70.
http://www.ncbi.nlm.nih.gov/pubmed/16395272?tool=bestpractice.com
Some studies have suggested MSK is more common in women, whereas others have found no difference between the sexes.[11]Parks JH, Coe FL, Strauss AL. Calcium nephrolithiasis and medullary sponge kidney in women. N Engl J Med. 1982 May 6;306(18):1088-91.
http://www.ncbi.nlm.nih.gov/pubmed/7070404?tool=bestpractice.com
While it is a developmental disorder, it is often not diagnosed until the third decade of life.[2]Forster JA, Taylor J, Browning AJ, et al. A review of the natural progression of medullary sponge kidney and a novel grading system based on intravenous urography findings. Urol Int. 2007;78(3):264-9.
http://www.ncbi.nlm.nih.gov/pubmed/17406139?tool=bestpractice.com
The disease most often presents in the 30- to 50-year age group. Epidemiologic studies have not shown any evidence that the prevalence is higher in certain ethnic or racial groups.
The differences in estimated prevalences are thought to be due to differences in the interpretation of radiologic findings and the characteristics of the populations studied. Furthermore, noncontrast computed tomography scan has replaced IVU as the diagnostic standard for renal stones, and this will probably lead to a decrease in the detection rate of MSK in the future.[3]Imam TH, Patail H, Patail H. Medullary sponge kidney: current perspectives. Int J Nephrol Renovasc Dis. 2019;12:213-8.
https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-fulltext-article-IJNRD
http://www.ncbi.nlm.nih.gov/pubmed/31576161?tool=bestpractice.com
[12]Pisani I, Giacosa R, Giuliotti S, et al. Ultrasound to address medullary sponge kidney: a retrospective study. BMC Nephrol. 2020 Oct 12;21(1):430.
https://bmcnephrol.biomedcentral.com/articles/10.1186/s12882-020-02084-1
http://www.ncbi.nlm.nih.gov/pubmed/33046028?tool=bestpractice.com