Ductal carcinoma in situ (DCIS) in women is typically asymptomatic and diagnosed during routine screening mammography. Less commonly, women with DCIS may present with a breast lump, nipple discharge, or Paget's disease of the breast. Lobular carcinoma in situ (LCIS) is usually discovered incidentally, often in conjunction with other clinically identified malignant or benign lesions such as fibroadenoma, cysts, papilloma, papillomatosis, fat necrosis, or breast abscesses.
There are no classic mammographic findings for LCIS, whereas DCIS often presents with clustered microcalcifications.[2]Cocquyt V, Van Belle S. Lobular carcinoma in situ and invasive lobular cancer of the breast. Curr Opin Obstet Gynecol. 2005 Feb;17(1):55-60.
http://www.ncbi.nlm.nih.gov/pubmed/15711412?tool=bestpractice.com
Clinical assessment
DCIS and LCIS are typically asymptomatic.
Rarely, DCIS may present as an eczematous-like rash on the nipple if presenting as Paget's disease. In the absence of medical attention, a woman may present with ulceration. Other uncommon presenting symptoms of DCIS include nipple discharge or a breast lump.
The first symptom in males diagnosed with DCIS is generally bloody nipple discharge.[46]Cutuli B, Dilhuydy JM, De Lafontan B, et al. Ductal carcinoma in situ of the male breast: analysis of 31 cases. Eur J Cancer. 1997 Jan;33(1):35-8.
http://www.ncbi.nlm.nih.gov/pubmed/9071896?tool=bestpractice.com
Imaging
National Comprehensive Cancer Network (NCCN) guidelines recommend digital breast tomosynthesis (three-dimensional mammography) alongside conventional two-dimensional mammography for screening and diagnosis, which may reduce the need for additional imaging.[47]National Comprehensive Cancer Network. NCCN clinical practice guidelines in oncology: breast cancer screening and diagnosis [internet publication].
https://www.nccn.org/guidelines/category_2
A mammographic finding in one breast of clustered microcalcifications and absence of a soft-tissue abnormality indicates DCIS. Calcifications may be linear, branching, or bizarre in comedo DCIS. Non-comedo DCIS may not be calcified or may present as fine granular powdery calcifications.
LCIS does not have classic mammographic findings.
If microcalcifications are not detected by mammography, then compression mammography, mammographic magnification views, ultrasonography, and/or magnetic resonance imaging (MRI) may be considered. For non-specific lesions magnification views, with or without ultrasound, are generally performed. To differentiate cystic from solid lesions, ultrasound is performed.
Mammographic sensitivity is lower in women with dense breasts, therefore supplemental imaging (e.g., ultrasound, MRI) may be warranted in these women.[47]National Comprehensive Cancer Network. NCCN clinical practice guidelines in oncology: breast cancer screening and diagnosis [internet publication].
https://www.nccn.org/guidelines/category_2
[48]Monticciolo DL, Malak SF, Friedewald SM, et al. Breast cancer screening recommendations inclusive of all women at average risk: update from the ACR and Society of Breast Imaging. J Am Coll Radiol. 2021 Sep;18(9):1280-8.
https://www.jacr.org/article/S1546-1440(21)00383-5/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/34154984?tool=bestpractice.com
[49]Weinstein SP, Slanetz PJ, Lewin AA, et al; Expert Panel on Breast Imaging. ACR appropriateness criteria® supplemental breast cancer screening based on breast density. J Am Coll Radiol. 2021 Nov;18(11s):S456-73.
https://www.jacr.org/article/S1546-1440(21)00725-0/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/34794600?tool=bestpractice.com
[50]Chen HL, Zhou JQ, Chen Q, et al. Comparison of the sensitivity of mammography, ultrasound, magnetic resonance imaging and combinations of these imaging modalities for the detection of small (≤2 cm) breast cancer. Medicine (Baltimore). 2021 Jul 2;100(26):e26531.
https://journals.lww.com/md-journal/Fulltext/2021/07020/Comparison_of_the_sensitivity_of_mammography,.48.aspx
http://www.ncbi.nlm.nih.gov/pubmed/34190189?tool=bestpractice.com
MRI may be especially helpful in detecting high-grade DCIS.[51]Kuhl CK, Schrading S, Bieling HB, et al. MRI for diagnosis of pure ductal carcinoma in situ: a prospective observational study. Lancet. 2007 Aug 11;370(9586):485-92.
http://www.ncbi.nlm.nih.gov/pubmed/17693177?tool=bestpractice.com
[52]Tajima CC, de Sousa LLC, Venys GL, et al. Magnetic resonance imaging of the breast: role in the evaluation of ductal carcinoma in situ. Radiol Bras. 2019 Jan-Feb;52(1):43-7.
https://pmc.ncbi.nlm.nih.gov/articles/PMC6383537
http://www.ncbi.nlm.nih.gov/pubmed/30804615?tool=bestpractice.com
[53]Greenwood HI, Wilmes LJ, Kelil T, et al. Role of breast MRI in the evaluation and detection of DCIS: opportunities and challenges. J Magn Reson Imaging. 2020 Sep;52(3):697-709.
http://www.ncbi.nlm.nih.gov/pubmed/31746088?tool=bestpractice.com
Although MRI can accurately detect additional lesions and contralateral cancer not identified using conventional imaging in primary breast cancer, MRI findings should be pathologically verified because of the high false-positive rate.[54]Plana MN, Carreira C, Muriel A, et al. Magnetic resonance imaging in the preoperative assessment of patients with primary breast cancer: systematic review of diagnostic accuracy and meta-analysis. Eur Radiol. 2012 Jan;22(1):26-38.
http://www.ncbi.nlm.nih.gov/pubmed/21847541?tool=bestpractice.com
[55]Wright JL, Rahbar H, Obeng-Gyasi S, et al. Overcoming barriers in ductal carcinoma in situ management: from overtreatment to optimal treatment. J Clin Oncol. 2022 Jan 20;40(3):225-30.
https://ascopubs.org/doi/10.1200/JCO.21.01674
http://www.ncbi.nlm.nih.gov/pubmed/34813345?tool=bestpractice.com
Breast MRI should not be used routinely for the preoperative workup of patients with DCIS.[56]Peters NH, van Esser S, van den Bosch MA, et al. Preoperative MRI and surgical management in patients with nonpalpable breast cancer: the MONET - randomised controlled trial. Eur J Cancer. 2011 Apr;47(6):879-86.
http://www.ncbi.nlm.nih.gov/pubmed/21195605?tool=bestpractice.com
[57]Fancellu A, Turner RM, Dixon JM, et al. Meta-analysis of the effect of preoperative breast MRI on the surgical management of ductal carcinoma in situ. Br J Surg. 2015 Jul;102(8):883-93.
https://academic.oup.com/bjs/article/102/8/883/6136370
http://www.ncbi.nlm.nih.gov/pubmed/25919321?tool=bestpractice.com
[58]van Bekkum S, Ter Braak BPM, Plaisier PW, et al. Preoperative breast MRI in management of patients with needle biopsy-proven ductal carcinoma in situ (DCIS). Eur J Surg Oncol. 2020 Oct;46(10 pt a):1854-60.
http://www.ncbi.nlm.nih.gov/pubmed/32624292?tool=bestpractice.com
Biopsy
Core needle or excisional biopsy techniques are used when breast cancer is suspected. The choice depends on the purpose of the procedure.
Core needle biopsy is often a good option. However, results are only diagnostic and not definitive, and may underestimate the extent of disease.[59]Hussain M, Cunnick GH. Management of lobular carcinoma in-situ and atypical lobular hyperplasia of the breast: a review. Eur J Surg Oncol. 2011 Apr;37(4):279-89.
http://www.ncbi.nlm.nih.gov/pubmed/21306860?tool=bestpractice.com
Architecturally, papillomas can cause false-positives. Furthermore, many breast malignancies contain elements of both in situ and invasive carcinoma. As such, a core biopsy demonstrating one component does not exclude the other.
Stereotactic (mammographically guided) core needle biopsy is the diagnostic procedure of choice in the setting of microcalcifications, as it is nearly as accurate as excisional biopsy, with fewer complications.[60]Bruening W, Fontanarosa J, Tipton K, et al. Systematic review: comparative effectiveness of core-needle and open surgical biopsy to diagnose breast lesions. Ann Intern Med. 2010 Feb 16;152(4):238-46.
http://www.ncbi.nlm.nih.gov/pubmed/20008742?tool=bestpractice.com
Ultrasound-guided core biopsy is preferred if a non-palpable mass is found on laboratory.
Excisional biopsy provides a complete diagnosis and the opportunity for treatment. However, it is associated with poorer cosmesis than needle biopsies, is more costly, and necessitates surgery. Excisional biopsy is recommended:[47]National Comprehensive Cancer Network. NCCN clinical practice guidelines in oncology: breast cancer screening and diagnosis [internet publication].
https://www.nccn.org/guidelines/category_2
if core needle biopsy cannot be performed
when core needle biopsy results are indeterminate, or benign and discordant with imaging
for non-classic LCIS (pleomorphic or florid).
Pathological analysis of biopsy is necessary for scoring by nuclear grade and architecture.
Ductal lavage or nipple aspirate fluid collection analysis may prove to be useful for diagnosis.[61]Jiwa N, Gandhewar R, Chauhan H, et al. Diagnostic accuracy of nipple aspirate fluid cytology in asymptomatic patients: a meta-analysis and systematic review of the literature. Ann Surg Oncol. 2021 Jul;28(7):3751-60.
https://link.springer.com/article/10.1245/s10434-020-09313-9
http://www.ncbi.nlm.nih.gov/pubmed/33165721?tool=bestpractice.com
However, concomitant use of detection markers may be required to improve sensitivity (e.g., basic fibroblast growth factor). More evidence is needed.
Sentinel lymph node biopsy
Sentinel lymph node biopsy (SLNB) should be strongly considered if the patient is undergoing mastectomy, or if tumour excision occurs in an anatomical location making it difficult to perform a future SLNB.[62]National Comprehensive Cancer Network. NCCN clinical practice guidelines in oncology: breast cancer [internet publication].
https://www.nccn.org/guidelines/category_1
Performing an SLNB after mastectomy is impractical. Guidelines do not recommend SLNB in women with DCIS who are undergoing breast-conserving surgery.[62]National Comprehensive Cancer Network. NCCN clinical practice guidelines in oncology: breast cancer [internet publication].
https://www.nccn.org/guidelines/category_1
[63]National Institute for Health and Care Excellence. Early and locally advanced breast cancer: diagnosis and management. Recommendations 1.4: surgery to the axilla. Jul 2018 [internet publication].
https://www.nice.org.uk/guidance/ng101/chapter/Recommendations#surgery-to-the-axilla
Hormone receptor testing
Oestrogen and progesterone receptor status is measured by immunohistochemical staining of fixed tumour tissue. Results can help to guide treatment.[64]Allison KH, Hammond MEH, Dowsett M, et al. Estrogen and progesterone receptor testing in breast cancer: American Society of Clinical Oncology/College of American Pathologists guideline update. Arch Pathol Lab Med. 2020 May;144(5):545-63.
https://meridian.allenpress.com/aplm/article/144/5/545/427509/Estrogen-and-Progesterone-Receptor-Testing-in
http://www.ncbi.nlm.nih.gov/pubmed/31928354?tool=bestpractice.com
Genetic evaluation
Genetic counselling and testing for high-penetrance breast cancer susceptibility genes (e.g., BRCA1, BRCA2, CDH1, PALB2, PTEN, STK11, and TP53) should be considered for women at high risk for hereditary breast cancer (e.g., based on personal and/or family history).[65]National Comprehensive Cancer Network. NCCN clinical practice guidelines in oncology: genetic/familial high-risk assessment: breast, ovarian, and pancreatic [internet publication].
https://www.nccn.org/guidelines/category_2
[66]Manahan ER, Kuerer HM, Sebastian M, et al. Consensus guidelines on genetic testing for hereditary breast cancer from the American Society of Breast Surgeons. Ann Surg Oncol. 2019 Oct;26(10):3025-31.
https://link.springer.com/article/10.1245/s10434-019-07549-8
http://www.ncbi.nlm.nih.gov/pubmed/31342359?tool=bestpractice.com
[67]Owens DK, Davidson KW, Krist AH, et al; US Preventive Services Task Force. Risk assessment, genetic counseling, and genetic testing for BRCA-related cancer: US Preventive Services Task Force recommendation statement. JAMA. 2019 Aug 20;322(7):652-65.
https://jamanetwork.com/journals/jama/fullarticle/2748515
http://www.ncbi.nlm.nih.gov/pubmed/31429903?tool=bestpractice.com
[68]American College of Obstetricians and Gynecologists Committee on Gynecologic Practice. ACOG committee opinion no. 727. Cascade testing: testing women for known hereditary genetic mutations associated with cancer. Obstet Gynecol. 2018 Jan;131(1):e31-4.
https://www.acog.org/clinical/clinical-guidance/committee-opinion/articles/2018/01/cascade-testing-testing-women-for-known-hereditary-genetic-mutations-associated-with-cancer
http://www.ncbi.nlm.nih.gov/pubmed/29266077?tool=bestpractice.com
[69]Bedrosian I, Somerfield MR, Achatz MI, et al. Germline testing in patients with breast cancer: ASCO-Society of Surgical Oncology guideline. J Clin Oncol. 2024 Feb 10;42(5):584-604.
https://ascopubs.org/doi/10.1200/JCO.23.02225?url_ver=Z39.88-2003&rfr_id=ori:rid:crossref.org&rfr_dat=cr_pub%20%200pubmed
http://www.ncbi.nlm.nih.gov/pubmed/38175972?tool=bestpractice.com
See Primary invasive breast cancer (Screening) topic for specific criteria for genetic counselling and testing.