Aetiology

A genetic predisposition may contribute to recurrent aphthous stomatitis (RAS). A positive family history may be found in up to 40% of patients.[1][10] Studies show a high correlation between stress, depression and anxiety, and RAS.[11]

An association with a variety of human leukocyte antigen (HLA) haplotypes has been reported.[12] Further clarification is required.[13]

In addition, further predisposing factors such as cytokine polymorphism have been suggested.[14]

Patients with RAS are usually non-smokers, and there is a lower prevalence and severity of ulcers in heavy compared with moderate smokers.[15][16] Some patients report an onset of ulcers parallel to smoking cessation, whereas others report control on re-initiation of smoking. The use of smokeless tobacco is also associated with a significantly lower prevalence of ulcers. Nicotine-containing tablets also appear to control the frequency of aphthae.[6]

Haematinic (iron, folic acid, or vitamin B12) deficiencies may be twice as common in some groups of patients with RAS as in healthy control subjects.[1][6][17][18]

There are patients whose ulcers coincide with the luteal phase of the menstrual cycle and often remit with oral contraceptives or during pregnancy.[6]

Local trauma may trigger ulcers in susceptible people.[1][6][19] Increased level of anxiety has been reported in some patients with RAS.[6]

RAS may be more prevalent in cows' milk-fed children.[20] Certain foods (e.g., chocolate, peanuts, coffee, and gluten products) have been reported to trigger episodes of RAS.[3] An increased frequency of RAS related to sodium lauryl sulfate-containing dentifrice has been reported, although other studies found no such association.[21] In another trial, researchers found that sodium lauryl sulfate-free toothpaste did not reduce the number or frequency of ulcers, but the participants self-reported feeling less pain and that they thought the ulcers healed slightly faster.[22]

Pathophysiology

A mononuclear (lymphocytic) cell infiltrate in the epithelium in the pre-ulcerative stage is followed by a localised papular swelling as a result of keratinocyte vacuolisation surrounded by a reactive, erythematous halo representing vasculitis.[23] The lesion then ulcerates and a fibrous membrane covers the ulcer, which is infiltrated mainly by neutrophils, lymphocytes, and plasma cells. Finally, there is healing with epithelial regeneration.

Evidence suggests that immunopathogenesis may involve cell-mediated responses, involving T cells and tumour necrosis factor alpha (TNF-alpha) production by these and other infiltrating leukocytes (macrophages and mast cells).[24] TNF-alpha induces inflammation by its effect on endothelial cell adhesion and neutrophil chemotaxis.[25] There has also been evidence of the association of toll-like receptors (TLR).[26][27]

Other cytokines, such as interleukin (IL)-2 and IL-10, and natural killer cells activated by IL-2 also have a role in RAS.[1][23]

Classification

Clinical classification[1][2][3]

There are three clinical presentations of recurrent aphthous stomatitis (RAS), which suggests disease heterogeneity.

Minor aphthous ulcers (around 75% to 85% of all RAS cases): [Figure caption and citation for the preceding image starts]: Recurrent aphthous stomatitis (RAS): minor aphthaeFrom the personal collection of Crispian Scully, MD, PhD, FDSRCS, FRCPath [Citation ends].com.bmj.content.model.Caption@3e792159

  • Small round or ovoid ulcers less than 10 mm in diameter (usually less than 5 mm in diameter)

  • Occur in groups of 1 to 6 at a time

  • Found mainly on the non-keratinised mucosa of the lips, cheeks, floor of the mouth, sulci, or ventrum of the tongue

  • Heal in 7-10 days without scarring

  • Frequency of episodes varies and patients can experience ulcer-free periods

  • Occur mainly in people aged between 10 and 40 years.

Major aphthous ulcers (around 10% to 15% of all RAS cases): [Figure caption and citation for the preceding image starts]: Recurrent aphthous stomatitis (RAS): major aphthaeFrom the personal collection of Crispian Scully, MD, PhD, FDSRCS, FRCPath [Citation ends].com.bmj.content.model.Caption@6779f2a7

  • Often more painful and persistent than minor aphthae

  • Large round or ovoid ulcers greater than 10 mm in diameter

  • Occur in groups of 1 to 6 at a time

  • Involve any oral site, including the keratinised mucosa (palate and dorsum of tongue)

  • Heal slowly over 10-40 days, or occasionally longer

  • Recur frequently and may heal with scarring

  • Occur mainly in people aged 10-40 years.

Herpetiform aphthous ulcers: [Figure caption and citation for the preceding image starts]: Recurrent aphthous stomatitis (RAS): herpetiform ulcerationFrom: Scully C, Flint S, Porter SR, et al. Oral and Maxillofacial diseases. London UK; 2004. Used with permission [Citation ends].com.bmj.content.model.Caption@13aacc93

  • Rarer than major and minor aphthous ulcers

  • Multiple (5-100) pinhead-sized discrete ulcers that can increase in size and coalesce to leave large areas of ulceration

  • Mimics herpes simplex stomatitis, but are not preceded by vesicles or blistering, and are not communicable

  • Often extremely painful

  • Involve any oral site, including the keratinised mucosa (palate and dorsum of tongue)

  • Heal in 10 days or longer

  • Recur so frequently that ulceration may seem continuous

  • Occur in a slightly older age group than the other forms of RAS and mainly in women.

Use of this content is subject to our disclaimer