The viruses causing SAHF are clade B New World arenaviruses (family Arenaviridae; genus Mammarenavirus) found in specific geographical locations within the countries after which they are named. This geographical restriction of the virus is due to the presence of different rodent vectors in specified locations within each country. The viruses are spread mainly through aerosolisation of infected rodent secretions and excreta, and there is a direct correlation between rodent numbers and annual case incidence.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[3]Gómez RM, Jaquenod de Giusti C, Sanchez Vallduvi MM, et al. Junín virus. A XXI century update. Microbes Infect. 2011;13:303-311.
http://www.ncbi.nlm.nih.gov/pubmed/21238601?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
[11]Grant A, Seregin A, Huang C, et al. Junín virus pathogenesis and virus replication. Viruses. 2012;4:2317-2339.
http://www.mdpi.com/1999-4915/4/10/2317
http://www.ncbi.nlm.nih.gov/pubmed/23202466?tool=bestpractice.com
There are 5 SAHFs, each caused by a different New World arenavirus:
Argentine haemorrhagic fever is caused by infection with Junin virus, and is found in the Pampas region in the eastern part of Argentina.[3]Gómez RM, Jaquenod de Giusti C, Sanchez Vallduvi MM, et al. Junín virus. A XXI century update. Microbes Infect. 2011;13:303-311.
http://www.ncbi.nlm.nih.gov/pubmed/21238601?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114. Junin virus was first discovered in 1958.[12]PARODI AS, GREENWAY DJ, RUGIERO HR, et al. [Concerning the epidemic outbreak in Junin]. [in spa]. Dia Med. 1958 Sep 4;30(62):2300-1.
Venezuelan haemorrhagic fever is caused by infection with Guanarito virus, and is found in Portuguesa state and Barinas state in northern Venezuela.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
Guanarito virus was first discovered in 1989.[13]Salas R, de Manzione N, Tesh RB, et al. Venezuelan haemorrhagic fever. Lancet. 1991 Oct 26;338(8774):1033-6.
http://www.ncbi.nlm.nih.gov/pubmed/1681354?tool=bestpractice.com
Bolivian haemorrhagic fever is caused by infection with Machupo virus, and is found in Beni district in northeastern Bolivia.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
Machupo virus was first discovered in 1963.[14]Johnson KM. Epidemiology of Machupo virus infection. 3. Significance of virological observations in man and animals. Am J Trop Med Hyg. 1965 Sep;14(5):816-8.
Chapare virus infection is caused by infection with Chapare virus, and is found in Cochabamba district in central Bolivia.[8]Delgado S, Erickson BR, Agudo R, et al. Chapare virus, a newly discovered arenavirus isolated from a fatal hemorrhagic fever case in Bolivia. PLoS Pathog. 2008;4:e1000047.
http://journals.plos.org/plospathogens/article?id=10.1371/journal.ppat.1000047
http://www.ncbi.nlm.nih.gov/pubmed/18421377?tool=bestpractice.com
Chapare virus was first discovered in 2004.[8]Delgado S, Erickson BR, Agudo R, et al. Chapare virus, a newly discovered arenavirus isolated from a fatal hemorrhagic fever case in Bolivia. PLoS Pathog. 2008;4:e1000047.
http://journals.plos.org/plospathogens/article?id=10.1371/journal.ppat.1000047
http://www.ncbi.nlm.nih.gov/pubmed/18421377?tool=bestpractice.com
Brazilian haemorrhagic fever is caused by infection with Sabia virus, and is found near Sao Paolo, Brazil.[9]Barry M, Russi M, Armstrong L, et al. Brief report: treatment of a laboratory-acquired Sabiá virus infection. N Engl J Med. 1995;333:294-296.
http://www.nejm.org/doi/full/10.1056/NEJM199508033330505
http://www.ncbi.nlm.nih.gov/pubmed/7596373?tool=bestpractice.com
Sabia virus was first discovered in 1993.[15]Lisieux T, Coimbra M, Nassar ES, et al. New arenavirus isolated in Brazil. Lancet. 1994 Feb 12;343(8894):391-2.
https://pmc.ncbi.nlm.nih.gov/articles/PMC3313646
http://www.ncbi.nlm.nih.gov/pubmed/7905555?tool=bestpractice.com
SAHF tends to occur in epidemics in rural areas with seasonal fluctuation, with a predominance of cases during harvest season.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[3]Gómez RM, Jaquenod de Giusti C, Sanchez Vallduvi MM, et al. Junín virus. A XXI century update. Microbes Infect. 2011;13:303-311.
http://www.ncbi.nlm.nih.gov/pubmed/21238601?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
Agricultural workers are at highest risk as the rodent vectors often live in the long grasses at the edge of fields. However, in the 1950s and '60s there were clusters of cases of Bolivian haemorrhagic fever in small towns when infection by the rodent vector Calomys callosus occurred.[16]Mackenzie RB. Epidemiology of Machupo virus infection. I. Pattern of human infection, San Joaquín, Bolivia, 1962-1964. Am J Trop Med Hyg. 1965;14:808-813.
http://www.ncbi.nlm.nih.gov/pubmed/5829142?tool=bestpractice.com
The diseases are most commonly found in adult males (approximately 60% to 70% of cases).[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[3]Gómez RM, Jaquenod de Giusti C, Sanchez Vallduvi MM, et al. Junín virus. A XXI century update. Microbes Infect. 2011;13:303-311.
http://www.ncbi.nlm.nih.gov/pubmed/21238601?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
[11]Grant A, Seregin A, Huang C, et al. Junín virus pathogenesis and virus replication. Viruses. 2012;4:2317-2339.
http://www.mdpi.com/1999-4915/4/10/2317
http://www.ncbi.nlm.nih.gov/pubmed/23202466?tool=bestpractice.com
This is likely due to the demographic of more men working as agricultural labourers when compared with women, who culturally are more likely to be homemakers. The disease has, however, been described in women, particularly those working in fields (e.g., cotton pickers). Children are relatively spared and few cases have been described in children under 5 years of age.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[3]Gómez RM, Jaquenod de Giusti C, Sanchez Vallduvi MM, et al. Junín virus. A XXI century update. Microbes Infect. 2011;13:303-311.
http://www.ncbi.nlm.nih.gov/pubmed/21238601?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
Imported cases of disease outside of the relevant South American countries are unlikely; however, with increasing international travel and changing patterns of adventure and working holidays, these diseases should still be considered in the differential of a returning febrile traveller from an endemic location.
While rare, nosocomial, laboratory, and person-to-person transmission from symptomatic individuals have been described, and appear most common in Bolivian haemorrhagic fever.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[3]Gómez RM, Jaquenod de Giusti C, Sanchez Vallduvi MM, et al. Junín virus. A XXI century update. Microbes Infect. 2011;13:303-311.
http://www.ncbi.nlm.nih.gov/pubmed/21238601?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
Laboratory exposure has been described for several of these viruses.[9]Barry M, Russi M, Armstrong L, et al. Brief report: treatment of a laboratory-acquired Sabiá virus infection. N Engl J Med. 1995;333:294-296.
http://www.nejm.org/doi/full/10.1056/NEJM199508033330505
http://www.ncbi.nlm.nih.gov/pubmed/7596373?tool=bestpractice.com
[10]Sarute N, Ross SR. New world arenavirus biology. Annu Rev Virol. 2017 Sep 29;4(1):141-58.
https://pmc.ncbi.nlm.nih.gov/articles/PMC7478856
http://www.ncbi.nlm.nih.gov/pubmed/28645238?tool=bestpractice.com
Few cases have been described of Chapare virus infection and Brazilian haemorrhagic fever, so little is known about the specific epidemiology of these two diseases. Brazilian haemorrhagic fever has only been identified in 3 cases, two of which were as a result of laboratory exposure.[9]Barry M, Russi M, Armstrong L, et al. Brief report: treatment of a laboratory-acquired Sabiá virus infection. N Engl J Med. 1995;333:294-296.
http://www.nejm.org/doi/full/10.1056/NEJM199508033330505
http://www.ncbi.nlm.nih.gov/pubmed/7596373?tool=bestpractice.com
One confirmed case of Chapare virus infection was identified in 2004; a cluster of 5 cases (with 3 confirmed) occurred in Bolivia in mid-2019.[8]Delgado S, Erickson BR, Agudo R, et al. Chapare virus, a newly discovered arenavirus isolated from a fatal hemorrhagic fever case in Bolivia. PLoS Pathog. 2008;4:e1000047.
http://journals.plos.org/plospathogens/article?id=10.1371/journal.ppat.1000047
http://www.ncbi.nlm.nih.gov/pubmed/18421377?tool=bestpractice.com
[17]Escalera-Antezana JP, Rodriguez-Villena OJ, Arancibia-Alba AW, et al. Clinical features of fatal cases of Chapare virus hemorrhagic fever originating from rural La Paz, Bolivia, 2019: A cluster analysis. Travel Med Infect Dis. 2020 Jul - Aug;36:101589.
http://www.ncbi.nlm.nih.gov/pubmed/32061859?tool=bestpractice.com
Large epidemics have been described for Argentine, Venezuelan, and Bolivian haemorrhagic fever.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
The geographical region where Venezuelan haemorrhagic fever and Bolivian haemorrhagic fever have been found is relatively static; however, the geographical region where Argentine haemorrhagic fever is found has been steadily expanding and it is now estimated that approximately 5 million people are at risk of the disease.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[3]Gómez RM, Jaquenod de Giusti C, Sanchez Vallduvi MM, et al. Junín virus. A XXI century update. Microbes Infect. 2011;13:303-311.
http://www.ncbi.nlm.nih.gov/pubmed/21238601?tool=bestpractice.com
[4]Enria DA, Briggiler AM, Sánchez Z. Treatment of Argentine hemorrhagic fever. Antiviral Res. 2008;78:132-9.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10245337
http://www.ncbi.nlm.nih.gov/pubmed/18054395?tool=bestpractice.com
[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114.[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
The incidence of Argentine haemorrhagic fever is estimated at 140 to 355 per 100,000 adult males in affected rural areas.[5]Enria DA, Briggiler AM, Feuillade MR. An overview of the epidemiological, ecological and preventive hallmarks of Argentine haemorrhagic fever (Junin virus). Bulletin Institut Pasteur. 1998;96:103-114. Incidence figures have not been estimated for Venezuelan and Bolivian haemorrhagic fever, but there has been significant fluctuation in annual case numbers with prolonged periods of very few cases followed by a resurgence of disease for a number of years.[2]Patterson M, Grant A, Paessler S. Epidemiology and pathogenesis of Bolivian hemorrhagic fever. Curr Opin Virol. 2014;5:82-90.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4028408
http://www.ncbi.nlm.nih.gov/pubmed/24636947?tool=bestpractice.com
[6]de Manzione N, Salas RA, Paredes H, et al. Venezuelan hemorrhagic fever: clinical and epidemiological studies of 165 cases. Clin Infect Dis. 1998;26:308-13.
http://cid.oxfordjournals.org/content/26/2/308.long
http://www.ncbi.nlm.nih.gov/pubmed/9502447?tool=bestpractice.com
[Figure caption and citation for the preceding image starts]: Regions of the world at risk of South American haemorrhagic feverCreated by BMJ Evidence Centre [Citation ends].