Patients with autoimmune hepatitis (AIH) require lifelong monitoring, as disease flares and relapses are frequent even after complete remission.[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
Progress is usually monitored by levels of serum aminotransferases, bilirubin, prothrombin time, albumin, and globulins (total or gamma globulin). Once remission is achieved and treatment withdrawn, patients should be closely monitored for relapse with regular laboratory assessments during the first 12 months and 6-12 monthly thereafter.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
Follow-up liver biopsy should be undertaken if alanine aminotransferase and/or IgG levels increase or fluctuate. Follow-up biopsy is not always required to demonstrate histological remission prior to withdrawal of treatment, as the chances of significant inflammatory activity requiring increased immunosuppression are very low once transaminases and IgG levels have normalised. It is recommended, however, if a change of management is likely to result from the procedure; this is particularly the case in patients with sub-optimal response to immunosuppression, and in patients with treatment side effects. Biopsy is also advisable prior to withdrawal of treatment for patients who had a severe initial presentation and low tolerance of induction treatment, as histological findings are predictive of fibrosis progression and relapse.[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
Pre-withdrawal liver biopsy also is still strongly advised in children to ensure resolution of inflammation.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
Patients on immunosuppressants must be monitored for potential complications of corticosteroid and azathioprine therapy. Full blood count for monitoring of leukopenia and thrombocytopenia, glucose levels, and renal function tests should be performed at regular intervals. Patients initiated on prednisolone/azathioprine combination therapy should have baseline clinical and laboratory parameters monitored during the first four weeks. As the steroid dose is tapered, monitoring intervals can be extended to 1-3 months. During maintenance treatment, patients should be seen at 3-6 month intervals.[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
Eye examinations for cataracts and glaucoma are usually recommended in patients on high-dose and/or long-term corticosteroid therapy.
European guidelines advise that bone mineral density assessment (DEXA) should ideally be performed in all patients with AIH at presentation, along with follow-up assessment between 1 and 5 years, depending on outcome and general osteoporosis risk.[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
The US guidelines recommend that DEXA should be performed at baseline in those adult patients with AIH who have risk factors for osteoporosis, and repeated every 2-3 years of continuous glucocorticoid treatment.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
They also advise that serum levels of 25-hydroxyvitamin D should be determined at diagnosis and annually thereafter, with insufficiency treated as required. Both guidelines recommend that patients should take vitamin D supplements and ensure adequate calcium intake while on glucocorticoid therapy. Bisphosphonate therapy is indicated for patients with AIH and documented osteoporosis.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
AIH patients with cirrhosis should undergo screening for hepatocellular carcinoma with 6 monthly ultrasound examination, with or without alpha-fetoprotein measurement.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
Changes in a patient’s mental health status should be monitored throughout management of AIH and their psychosocial needs addressed. Structured, validated questionnaires can be helpful.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
Depression and anxiety are more common in patients with AIH than in the general population, mainly because of concerns about disease progression.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
[26]European Association for the Study of the Liver. EASL clinical practice guidelines: autoimmune hepatitis. J Hepatol. 2015 Oct;63(4):971-1004.
http://www.ncbi.nlm.nih.gov/pubmed/26341719?tool=bestpractice.com
Depression is moderate in 19% of patients and moderately severe in 10%, and correlates strongly with physical fatigue.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com
Low scores on health-related quality of life assessments have been strongly associated with glucocorticoid use. Pre-treatment mental health problems, especially depression, may be intensified during glucocorticoid treatment.[80]Schramm C, Wahl I, Weiler-Normann C, et al. Health-related quality of life, depression, and anxiety in patients with autoimmune hepatitis. J Hepatol. 2014 Mar;60(3):618-24.
http://www.ncbi.nlm.nih.gov/pubmed/24240053?tool=bestpractice.com
The development or worsening of mental health problems may justify targeted counselling, individualised adjustments in the doses of glucocorticoids, or adjunctive antidepressant or anti-anxiety interventions.[1]Mack CL, Adams D, Assis DN, et al. Diagnosis and management of autoimmune hepatitis in adults and children: 2019 practice guidance and guidelines from the American Association for the Study of Liver Diseases. Hepatology. 2020 Aug;72(2):671-722.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31065
http://www.ncbi.nlm.nih.gov/pubmed/31863477?tool=bestpractice.com