Investigations

1st investigations to order

blood glucose

Test
Result
Test

Buerger's disease can be excluded in patients with diabetes.

Result

normal

urea

Test
Result
Test

Biochemical evidence of renal failure may suggest the presence of an autoimmune disease.

Result

normal

serum creatinine

Test
Result
Test

Biochemical evidence of renal failure may suggest the presence of an autoimmune disease.

Result

normal

full blood count (FBC) with differential

Test
Result
Test

Excludes a myeloproliferative disease. WBC count may be elevated if infection present.

Result

normal

coagulation screen

Test
Result
Test

Excludes a hypercoagulable state.

Result

normal

thrombophilia screen

Test
Result
Test

Excludes protein C, protein S, and anti-thrombin III deficiencies.

Result

normal

C-reactive protein (CRP)

Test
Result
Test

May be elevated if wet gangrene present.

Result

normal

erythrocyte sedimentation rate (ESR)

Test
Result
Test

May be elevated if wet gangrene present.

Result

normal

arterial Doppler

Test
Result
Test

An arterial Doppler confirms absence of arterial flow.

Result

confirms the absence of infrapopliteal, brachial, or distal pulses

Investigations to consider

anti-nuclear antibody

Test
Result
Test

To rule out other causes of vascular disease, including Raynaud’s phenomenon and systemic lupus erythematosus. ESR, CRP, anti-nuclear antibody, rheumatoid factor, anti-neutrophilic cytoplasmic antibody (ANCA), and complement measurements should all be normal in people with Buerger’s disease.[28]

Result

normal

rheumatoid factor

Test
Result
Test

To rule out other causes of vascular disease, including rheumatoid vasculitis. ESR, CRP, anti-nuclear antibody, rheumatoid factor, anti-neutrophilic cytoplasmic antibody (ANCA), and complement measurements should all be normal in people with Buerger’s disease.[28]

Result

normal

anti-neutrophilic cytoplasmic antibody (ANCA)

Test
Result
Test

To rule out other causes of vascular disease, including granulomatosis with polyangiitis (Wegener’s granulomatosis). ESR, CRP, anti-nuclear antibody, rheumatoid factor, anti-neutrophilic cytoplasmic antibody (ANCA), and complement measurements should all be normal in people with Buerger’s disease.[28]

Result

normal

complement levels

Test
Result
Test

To rule out other causes of vascular disease. ESR, CRP, anti-nuclear antibody, rheumatoid factor, anti-neutrophilic cytoplasmic antibody (ANCA), and complement measurements should all be normal in people with Buerger’s disease.[28]

Result

normal

anti-centromere antibody

Test
Result
Test

To exclude calcinosis, Raynaud's phenomenon, oesophageal dysmotility, sclerodactyly, and telangiectasia (CREST) syndrome.

Result

normal

topoisomerase I antibodies (Scl-70)

Test
Result
Test

To exclude scleroderma.

Result

normal

echocardiogram

Test
Result
Test

An echocardiogram looks for evidence of an embolic source. It is used to exclude embolic causes and is normal in Buerger's disease.

Result

normal

arterial duplex

Test
Result
Test

'Corkscrew' collaterals are dilated vasa vasorum of the occluded main artery.

Result

identifies non-atherosclerotic occluded vessels; shows medium and small vessel occlusion, often with 'corkscrew'-shaped collateral vessels (Martorell's sign)

digital subtraction angiography

Test
Result
Test

Demonstrates normal non-atherosclerotic proximal arteries and shows occluded distal small and medium-sized vessels.

'Corkscrew' collaterals are dilated vasa vasorum of the occluded main artery.

Arterial lesions are usually confined to the popliteal, crural, and below-knee vessels in the lower limb, and the forearm vessels in the upper limb.

Result

identifies diseased vessels; classical tortuous 'corkscrew'-shaped collaterals (Martorell's sign) connect unaffected segments of distal vessels

anti-cardiolipin antibodies

Test
Result
Test

Associated with periodontal infections and destruction seen in Buerger's disease.[22]

Result

elevated

Emerging tests

CT angiography

Test
Result
Test

'Corkscrew' collaterals are dilated vasa vasorum of the occluded main artery.

Arterial lesions are usually confined to the popliteal, crural, and below-knee vessels in the lower limb, and the forearm vessels in the upper limb.

Result

identifies diseased vessels; shows medium and small vessel occlusion, often with 'corkscrew'-shaped collateral vessels (Martorell's sign)

magnetic resonance angiography

Test
Result
Test

'Corkscrew' collaterals are dilated vasa vasorum of the occluded main artery.

Arterial lesions are usually confined to the popliteal, crural, and below-knee vessels in the lower limb, and the forearm vessels in the upper limb.

Result

identifies diseased vessels; shows medium and small vessel occlusion, often with 'corkscrew'-shaped collateral vessels (Martorell's sign)

tissue biopsy

Test
Result
Test

Tissue biopsy shows evidence pathognomonic of Buerger's disease. Whilst arterial biopsy may aid diagnosis it should be avoided in ischaemic tissue.

Result

highly cellular arterial thrombus; non-disrupted internal elastic lamina; evidence of segmental lesions of collateral vessels

genetic testing

Test
Result
Test

Myeloid differentiation primary-response protein 88 (MyD88) is a gene for which identification may suggest resistance to Buerger's disease, especially in Japanese people.[15]

Result

positive or negative for MyD88 gene resistance polymorphism

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