Acute liver failure (ALF) is a rare event with fewer than 10 cases per million people per year in the developed world.[7]Lee WM, Squires RH Jr, Nyberg SL, et al. Acute liver failure: summary of a workshop. Hepatology. 2008 Apr;47(4):1401-15.
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3381946
http://www.ncbi.nlm.nih.gov/pubmed/18318440?tool=bestpractice.com
[9]Bernal W, Wendon J. Acute liver failure. N Engl J Med. 2013 Dec 26;369(26):2525-34.
http://www.nejm.org/doi/full/10.1056/NEJMra1208937
http://www.ncbi.nlm.nih.gov/pubmed/24369077?tool=bestpractice.com
ALF was responsible for 1.9% of US liver transplants in 2021.[10]Kwong AJ, Ebel NH, Kim WR, et al. OPTN/SRTR 2021 Annual data report: liver. Am J Transplant. 2023 Feb;23(2 suppl 1):S178-263.
https://www.amjtransplant.org/article/S1600-6135(23)00253-8/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/37132348?tool=bestpractice.com
Due to its rarity and acute presentation, ALF had not been well studied prospectively until the establishment of the US Acute Liver Failure Study Group (ALFSG). Over nearly 20 years, more than 2000 adult patients in over 30 US centres have been enrolled in the ALFSG database.[7]Lee WM, Squires RH Jr, Nyberg SL, et al. Acute liver failure: summary of a workshop. Hepatology. 2008 Apr;47(4):1401-15.
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3381946
http://www.ncbi.nlm.nih.gov/pubmed/18318440?tool=bestpractice.com
[11]Chung RT, Stravitz RT, Fontana RJ, et al. Pathogenesis of liver injury in acute liver failure. Gastroenterology. 2012 Sep;143(3):e1-7.
http://www.gastrojournal.org/article/S0016-5085%2812%2900959-6/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/22796239?tool=bestpractice.com
[12]Reuben A, Tillman H, Fontana RJ, et al. Outcomes in adults with acute liver failure between 1998 and 2013: an observational cohort study. Ann Intern Med. 2016 Jun 7;164(11):724-32.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5526039
http://www.ncbi.nlm.nih.gov/pubmed/27043883?tool=bestpractice.com
A separate database has also been established for paediatric ALF cases arising from 19 US, 1 Canadian, and 2 UK centres.
Analysis of the adult dataset has revealed that the majority of cases were women (67%) and the mean age was 38 years (range 17-79 years). The overall rate of spontaneous recovery without liver transplantation was 45%; 25% of cases received a liver transplant; and the overall mortality rate was 30%.[7]Lee WM, Squires RH Jr, Nyberg SL, et al. Acute liver failure: summary of a workshop. Hepatology. 2008 Apr;47(4):1401-15.
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3381946
http://www.ncbi.nlm.nih.gov/pubmed/18318440?tool=bestpractice.com
These reported outcomes are an improvement over those described in past decades, partly due to changing trends in aetiologies of ALF. Additional data have revealed improvements in overall short-term survival, transplant-free survival, and post-transplant survival over the last decade in particular, possibly as a result of early recognition and changes in intensive care management.[12]Reuben A, Tillman H, Fontana RJ, et al. Outcomes in adults with acute liver failure between 1998 and 2013: an observational cohort study. Ann Intern Med. 2016 Jun 7;164(11):724-32.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5526039
http://www.ncbi.nlm.nih.gov/pubmed/27043883?tool=bestpractice.com