RT Journal Article
SR Electronic
T1 Benign but fatal: management of endotracheal Rosai-Dorfman disease with acute onset
JF Thorax
JO Thorax
FD BMJ Publishing Group Ltd and British Thoracic Society
SP 211
OP 213
DO 10.1136/thorax-2022-219092
VO 78
IS 2
A1 Wang, Bin
A1 Song, Zhi-min
A1 Li, Jin-dong
A1 Zhao, Yin-long
A1 Sun, Ping-li
A1 Tian, Jia-kun
A1 Yin, Jin-zhi
A1 Zhang, Yan
YR 2023
UL http://thorax.bmj.com/content/78/2/211.abstract
AB Rosai-Dorfman disease (RDD) is a non-malignant condition mainly manifesting as a proliferation of histiocytes in lymph nodes. Endotracheal RDD (ERDD) with an acute onset presentation is extremely rare. There are few case reports of ERDD mainly concerning its pathology, diagnostics and bronchoscopic treatment, without providing sufficient clinical information from a comprehensive perspective. As a novel and challenging technique, tracheal resection and reconstruction (TRR) with spontaneous-ventilation video-assisted thoracoscopic surgery (SV-VATS) has been reported as feasible and safe in highly selected patients, but few centres have shared their experience with this approach. This case-based discussion includes not only practical issues in the management of a life-threatening ERDD patient, but also specialists’ views on the management of acute obstructive airway, and the surgeons’ reflection on TRR with SV-VATS.