Clinical characteristics, functional respiratory decline and follow-up in adult patients with primary ciliary dyskinesia
Justine Frija-Masson, Laurence Bassinet, Isabelle Honoré, Nadine Dufeu, Bruno Housset, André Coste, Jean Francois Papon, Estelle Escudier, Pierre-Régis Burgel, Bernard Maître
Thorax Feb 2017, 72 (2) 154-160; DOI: 10.1136/thoraxjnl-2015-207891