EEEV is the most deadly encephalitic arbovirus in North America. Case fatality is typically 30% to 50%.[2]Silverman MA, Misasi J, Smole S, et al. Eastern equine encephalitis in children, Massachusetts and New Hampshire, USA, 1970-2010. Emerg Infect Dis. 2013 Feb;19(2):194-201.
http://wwwnc.cdc.gov/eid/article/19/2/12-0039_article
http://www.ncbi.nlm.nih.gov/pubmed/23343480?tool=bestpractice.com
[11]Gaensbauer JT, Lindsey NP, Messacar K, et al. Neuroinvasive arboviral disease in the United States: 2003 to 2012. Pediatrics. 2014 Sep;134(3):e642-50.
http://pediatrics.aappublications.org/content/134/3/e642.long
http://www.ncbi.nlm.nih.gov/pubmed/25113294?tool=bestpractice.com
Death mainly occurs 2 to 10 days after symptom onset, but can occur later.[15]Centers for Disease Control and Prevention. Eastern equine encephalitis. Nov 2019 [internet publication].
https://www.cdc.gov/easternequineencephalitis/index.html
Although some patients with EEEV infection may be asymptomatic, it is common for patients to experience symptoms resembling influenza or dengue fever (i.e., a prodrome), which may have an abrupt onset. Neurological (encephalitic) symptoms may also develop in some patients. Neurological/central nervous system involvement is most commonly seen in those aged over 50 years or under 15 years. However, neurological involvement due to Madariaga virus (MADV) infection is more prevalent in children.[16]Carrera JP, Forrester N, Wang E, et al. Eastern equine encephalitis in Latin America. N Engl J Med. 2013 Aug 22;369(8):732-44.
http://www.nejm.org/doi/full/10.1056/NEJMoa1212628#t=article
http://www.ncbi.nlm.nih.gov/pubmed/23964935?tool=bestpractice.com
In the absence of neurological symptoms, febrile illness usually resolves in 1 to 2 weeks.[5]Calisher CH. Medically important arboviruses of the United States and Canada. Clin Microbiol Rev. 1994 Jan;7(1):89-116.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC358307/?page=15
http://www.ncbi.nlm.nih.gov/pubmed/8118792?tool=bestpractice.com
If neurological symptoms are present, they tend to appear several days into the course of illness, and include irritability, drowsiness, altered mental status, seizures, cranial nerve palsies, focal weakness, photophobia, and meningismus. Severe cases result in coma and death, which usually occurs 2 to 10 days after symptom onset. Of those who recover from EEEV infection, approximately 50% have neurological sequelae.[2]Silverman MA, Misasi J, Smole S, et al. Eastern equine encephalitis in children, Massachusetts and New Hampshire, USA, 1970-2010. Emerg Infect Dis. 2013 Feb;19(2):194-201.
http://wwwnc.cdc.gov/eid/article/19/2/12-0039_article
http://www.ncbi.nlm.nih.gov/pubmed/23343480?tool=bestpractice.com
Prognosis may be better in patients over 40 years of age, and in patients who experience a longer prodrome (e.g., >3 days).[2]Silverman MA, Misasi J, Smole S, et al. Eastern equine encephalitis in children, Massachusetts and New Hampshire, USA, 1970-2010. Emerg Infect Dis. 2013 Feb;19(2):194-201.
http://wwwnc.cdc.gov/eid/article/19/2/12-0039_article
http://www.ncbi.nlm.nih.gov/pubmed/23343480?tool=bestpractice.com
[44]Przelomski MM, O’Rourke E, Grady GF, et al. Eastern equine encephalitis in Massachusetts: a report of 16 cases, 1970-1984. Neurology. 1988 May;38(5):736-9.
http://www.ncbi.nlm.nih.gov/pubmed/3362371?tool=bestpractice.com
The size of radiographic lesions in the brain does not appear to be associated with outcome in patients with EEEV infection; however, pleocytosis in cerebrospinal fluid and severe hyponatraemia have been correlated with poor outcomes.[36]Deresiewicz RL, Thaler SJ, Hsu L, et al. Clinical and neuroradiographic manifestations of eastern equine encephalitis. N Engl J Med. 1997 Jun 26;336(26):1867-74.
http://www.nejm.org/doi/full/10.1056/NEJM199706263362604#t=article
http://www.ncbi.nlm.nih.gov/pubmed/9197215?tool=bestpractice.com
Long-term sequelae
Neurological sequelae may be long-term, consisting of gross and fine motor impairment, memory impairment, behavioural changes, weakness, seizures, or tremors.[16]Carrera JP, Forrester N, Wang E, et al. Eastern equine encephalitis in Latin America. N Engl J Med. 2013 Aug 22;369(8):732-44.
http://www.nejm.org/doi/full/10.1056/NEJMoa1212628#t=article
http://www.ncbi.nlm.nih.gov/pubmed/23964935?tool=bestpractice.com
[45]Villari P, Spielman A, Komar N, et al. The economic burden imposed by a residual case of eastern encephalitis. Am J Trop Med Hyg. 1995 Jan;52(1):8-13.
http://www.ncbi.nlm.nih.gov/pubmed/7856830?tool=bestpractice.com
EEEV infection appears to confer life-long immunity.[15]Centers for Disease Control and Prevention. Eastern equine encephalitis. Nov 2019 [internet publication].
https://www.cdc.gov/easternequineencephalitis/index.html